Medullary Sponge Kidney: Current Perspectives
Talha H Imam,1 Haris Patail,2 Hassan Patail3 1Division of Nephrology, Kaiser Permanente, Fontana, CA, USA; 2St. George’s University School of Medicine, West Indies, Grenada; 3Department of Medicine, Division of Pulmonary Critical Care and Sleep Medicine, Stony Brook University Hospital, St...
Ausführliche Beschreibung
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Imam TH [verfasserIn] Patail H [verfasserIn] |
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E-Artikel |
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Englisch |
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2019 |
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Medullary Sponge Kidney. Nephron. Nephrocalcinosis. Renal Stones. |
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Übergeordnetes Werk: |
In: International Journal of Nephrology and Renovascular Disease - Dove Medical Press, 2009, (2019), Seite 213-218 |
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Übergeordnetes Werk: |
year:2019 ; pages:213-218 |
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(DE-627)DOAJ002589486 (DE-599)DOAJ057016a8e21f4fdeac98d57aae847f68 DE-627 ger DE-627 rakwb eng RC870-923 Imam TH verfasserin aut Medullary Sponge Kidney: Current Perspectives 2019 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Talha H Imam,1 Haris Patail,2 Hassan Patail3 1Division of Nephrology, Kaiser Permanente, Fontana, CA, USA; 2St. George’s University School of Medicine, West Indies, Grenada; 3Department of Medicine, Division of Pulmonary Critical Care and Sleep Medicine, Stony Brook University Hospital, Stony Brook, NY, USACorrespondence: Talha H ImamDivision of Nephrology, Kaiser Permanente, 9985 Sierra Ave, Fontana, CA 92335, USATel +1 909-427-7521Email thimamhotmail.comAbstract: Medullary Sponge Kidney (MSK) disease is a rare congenital malformation of the distal nephron where cystic dilatation is appreciable in the collecting ducts and renal papillae. Most cases of the malformation are thought to arise from a malfunction within neurotrophic factor and tyrosine kinase interactions. Presentation and prognosis are usually indolent; however, they include urinary tract infections (UTI), nephrolithiasis and nephrocalcinosis, distal renal tubular acidosis (dRTA) and hypocitraturia. With an insidious and asymptomatic onset, MSK is a difficult renal manifestation to both diagnose and treat. Difficulty diagnosing MSK today arises from clinical settings deviating from the usage of contrast methods when assessing the urogenital tract. Many healthcare standards for kidney disorders center diagnosis around imaging techniques rather than contrast methods. This ultimately leads to a decrease in the total number of confirmed cases of MSK. Though intra-venous urogram (IVU) remains as the current gold standard to diagnose MSK, other methods such as endoscopy and Multi-detector computed tomography (MDCT) are being put into place. Endoscopic examination and renal biopsy may allow definitive diagnosis; however, such invasive methods may be considered excessive. Moving forward, differential diagnoses for MSK can be made more precisely when patients present with other renal manifestations, especially in groups at risk. These groups include patients between the age of 20 and 30, patients with other renal malformations, high sodium diet patients, hyperparathyroid patients, and patients with family history of MSK. Basic treatment is aimed at controlling stone formation by stabilizing urinary pH. Treatment for patients, especially those prone to forming stones, includes the application of potassium citrate compounds, prophylactic water and diet control, surgical intervention or lithotripsy for removal of symptomatic kidney stones.Keywords: medullary sponge kidney, nephron, nephrocalcinosis, renal stones Medullary Sponge Kidney. Nephron. Nephrocalcinosis. Renal Stones. Diseases of the genitourinary system. Urology Patail H verfasserin aut Patail H verfasserin aut In International Journal of Nephrology and Renovascular Disease Dove Medical Press, 2009 (2019), Seite 213-218 (DE-627)606031928 (DE-600)2508160-3 11787058 nnns year:2019 pages:213-218 https://doaj.org/article/057016a8e21f4fdeac98d57aae847f68 kostenfrei https://www.dovepress.com/medullary-sponge-kidney-current-perspectives-peer-reviewed-article-IJNRD kostenfrei https://doaj.org/toc/1178-7058 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_11 GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2003 GBV_ILN_2014 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 2019 213-218 |
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(DE-627)DOAJ002589486 (DE-599)DOAJ057016a8e21f4fdeac98d57aae847f68 DE-627 ger DE-627 rakwb eng RC870-923 Imam TH verfasserin aut Medullary Sponge Kidney: Current Perspectives 2019 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Talha H Imam,1 Haris Patail,2 Hassan Patail3 1Division of Nephrology, Kaiser Permanente, Fontana, CA, USA; 2St. George’s University School of Medicine, West Indies, Grenada; 3Department of Medicine, Division of Pulmonary Critical Care and Sleep Medicine, Stony Brook University Hospital, Stony Brook, NY, USACorrespondence: Talha H ImamDivision of Nephrology, Kaiser Permanente, 9985 Sierra Ave, Fontana, CA 92335, USATel +1 909-427-7521Email thimamhotmail.comAbstract: Medullary Sponge Kidney (MSK) disease is a rare congenital malformation of the distal nephron where cystic dilatation is appreciable in the collecting ducts and renal papillae. Most cases of the malformation are thought to arise from a malfunction within neurotrophic factor and tyrosine kinase interactions. Presentation and prognosis are usually indolent; however, they include urinary tract infections (UTI), nephrolithiasis and nephrocalcinosis, distal renal tubular acidosis (dRTA) and hypocitraturia. With an insidious and asymptomatic onset, MSK is a difficult renal manifestation to both diagnose and treat. Difficulty diagnosing MSK today arises from clinical settings deviating from the usage of contrast methods when assessing the urogenital tract. Many healthcare standards for kidney disorders center diagnosis around imaging techniques rather than contrast methods. This ultimately leads to a decrease in the total number of confirmed cases of MSK. Though intra-venous urogram (IVU) remains as the current gold standard to diagnose MSK, other methods such as endoscopy and Multi-detector computed tomography (MDCT) are being put into place. Endoscopic examination and renal biopsy may allow definitive diagnosis; however, such invasive methods may be considered excessive. Moving forward, differential diagnoses for MSK can be made more precisely when patients present with other renal manifestations, especially in groups at risk. These groups include patients between the age of 20 and 30, patients with other renal malformations, high sodium diet patients, hyperparathyroid patients, and patients with family history of MSK. Basic treatment is aimed at controlling stone formation by stabilizing urinary pH. Treatment for patients, especially those prone to forming stones, includes the application of potassium citrate compounds, prophylactic water and diet control, surgical intervention or lithotripsy for removal of symptomatic kidney stones.Keywords: medullary sponge kidney, nephron, nephrocalcinosis, renal stones Medullary Sponge Kidney. Nephron. Nephrocalcinosis. Renal Stones. Diseases of the genitourinary system. Urology Patail H verfasserin aut Patail H verfasserin aut In International Journal of Nephrology and Renovascular Disease Dove Medical Press, 2009 (2019), Seite 213-218 (DE-627)606031928 (DE-600)2508160-3 11787058 nnns year:2019 pages:213-218 https://doaj.org/article/057016a8e21f4fdeac98d57aae847f68 kostenfrei https://www.dovepress.com/medullary-sponge-kidney-current-perspectives-peer-reviewed-article-IJNRD kostenfrei https://doaj.org/toc/1178-7058 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_11 GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2003 GBV_ILN_2014 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 2019 213-218 |
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(DE-627)DOAJ002589486 (DE-599)DOAJ057016a8e21f4fdeac98d57aae847f68 DE-627 ger DE-627 rakwb eng RC870-923 Imam TH verfasserin aut Medullary Sponge Kidney: Current Perspectives 2019 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Talha H Imam,1 Haris Patail,2 Hassan Patail3 1Division of Nephrology, Kaiser Permanente, Fontana, CA, USA; 2St. George’s University School of Medicine, West Indies, Grenada; 3Department of Medicine, Division of Pulmonary Critical Care and Sleep Medicine, Stony Brook University Hospital, Stony Brook, NY, USACorrespondence: Talha H ImamDivision of Nephrology, Kaiser Permanente, 9985 Sierra Ave, Fontana, CA 92335, USATel +1 909-427-7521Email thimamhotmail.comAbstract: Medullary Sponge Kidney (MSK) disease is a rare congenital malformation of the distal nephron where cystic dilatation is appreciable in the collecting ducts and renal papillae. Most cases of the malformation are thought to arise from a malfunction within neurotrophic factor and tyrosine kinase interactions. Presentation and prognosis are usually indolent; however, they include urinary tract infections (UTI), nephrolithiasis and nephrocalcinosis, distal renal tubular acidosis (dRTA) and hypocitraturia. With an insidious and asymptomatic onset, MSK is a difficult renal manifestation to both diagnose and treat. Difficulty diagnosing MSK today arises from clinical settings deviating from the usage of contrast methods when assessing the urogenital tract. Many healthcare standards for kidney disorders center diagnosis around imaging techniques rather than contrast methods. This ultimately leads to a decrease in the total number of confirmed cases of MSK. Though intra-venous urogram (IVU) remains as the current gold standard to diagnose MSK, other methods such as endoscopy and Multi-detector computed tomography (MDCT) are being put into place. Endoscopic examination and renal biopsy may allow definitive diagnosis; however, such invasive methods may be considered excessive. Moving forward, differential diagnoses for MSK can be made more precisely when patients present with other renal manifestations, especially in groups at risk. These groups include patients between the age of 20 and 30, patients with other renal malformations, high sodium diet patients, hyperparathyroid patients, and patients with family history of MSK. Basic treatment is aimed at controlling stone formation by stabilizing urinary pH. Treatment for patients, especially those prone to forming stones, includes the application of potassium citrate compounds, prophylactic water and diet control, surgical intervention or lithotripsy for removal of symptomatic kidney stones.Keywords: medullary sponge kidney, nephron, nephrocalcinosis, renal stones Medullary Sponge Kidney. Nephron. Nephrocalcinosis. Renal Stones. Diseases of the genitourinary system. Urology Patail H verfasserin aut Patail H verfasserin aut In International Journal of Nephrology and Renovascular Disease Dove Medical Press, 2009 (2019), Seite 213-218 (DE-627)606031928 (DE-600)2508160-3 11787058 nnns year:2019 pages:213-218 https://doaj.org/article/057016a8e21f4fdeac98d57aae847f68 kostenfrei https://www.dovepress.com/medullary-sponge-kidney-current-perspectives-peer-reviewed-article-IJNRD kostenfrei https://doaj.org/toc/1178-7058 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_11 GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2003 GBV_ILN_2014 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 2019 213-218 |
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(DE-627)DOAJ002589486 (DE-599)DOAJ057016a8e21f4fdeac98d57aae847f68 DE-627 ger DE-627 rakwb eng RC870-923 Imam TH verfasserin aut Medullary Sponge Kidney: Current Perspectives 2019 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Talha H Imam,1 Haris Patail,2 Hassan Patail3 1Division of Nephrology, Kaiser Permanente, Fontana, CA, USA; 2St. George’s University School of Medicine, West Indies, Grenada; 3Department of Medicine, Division of Pulmonary Critical Care and Sleep Medicine, Stony Brook University Hospital, Stony Brook, NY, USACorrespondence: Talha H ImamDivision of Nephrology, Kaiser Permanente, 9985 Sierra Ave, Fontana, CA 92335, USATel +1 909-427-7521Email thimamhotmail.comAbstract: Medullary Sponge Kidney (MSK) disease is a rare congenital malformation of the distal nephron where cystic dilatation is appreciable in the collecting ducts and renal papillae. Most cases of the malformation are thought to arise from a malfunction within neurotrophic factor and tyrosine kinase interactions. Presentation and prognosis are usually indolent; however, they include urinary tract infections (UTI), nephrolithiasis and nephrocalcinosis, distal renal tubular acidosis (dRTA) and hypocitraturia. With an insidious and asymptomatic onset, MSK is a difficult renal manifestation to both diagnose and treat. Difficulty diagnosing MSK today arises from clinical settings deviating from the usage of contrast methods when assessing the urogenital tract. Many healthcare standards for kidney disorders center diagnosis around imaging techniques rather than contrast methods. This ultimately leads to a decrease in the total number of confirmed cases of MSK. Though intra-venous urogram (IVU) remains as the current gold standard to diagnose MSK, other methods such as endoscopy and Multi-detector computed tomography (MDCT) are being put into place. Endoscopic examination and renal biopsy may allow definitive diagnosis; however, such invasive methods may be considered excessive. Moving forward, differential diagnoses for MSK can be made more precisely when patients present with other renal manifestations, especially in groups at risk. These groups include patients between the age of 20 and 30, patients with other renal malformations, high sodium diet patients, hyperparathyroid patients, and patients with family history of MSK. Basic treatment is aimed at controlling stone formation by stabilizing urinary pH. Treatment for patients, especially those prone to forming stones, includes the application of potassium citrate compounds, prophylactic water and diet control, surgical intervention or lithotripsy for removal of symptomatic kidney stones.Keywords: medullary sponge kidney, nephron, nephrocalcinosis, renal stones Medullary Sponge Kidney. Nephron. Nephrocalcinosis. Renal Stones. Diseases of the genitourinary system. Urology Patail H verfasserin aut Patail H verfasserin aut In International Journal of Nephrology and Renovascular Disease Dove Medical Press, 2009 (2019), Seite 213-218 (DE-627)606031928 (DE-600)2508160-3 11787058 nnns year:2019 pages:213-218 https://doaj.org/article/057016a8e21f4fdeac98d57aae847f68 kostenfrei https://www.dovepress.com/medullary-sponge-kidney-current-perspectives-peer-reviewed-article-IJNRD kostenfrei https://doaj.org/toc/1178-7058 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_11 GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2003 GBV_ILN_2014 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 2019 213-218 |
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(DE-627)DOAJ002589486 (DE-599)DOAJ057016a8e21f4fdeac98d57aae847f68 DE-627 ger DE-627 rakwb eng RC870-923 Imam TH verfasserin aut Medullary Sponge Kidney: Current Perspectives 2019 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Talha H Imam,1 Haris Patail,2 Hassan Patail3 1Division of Nephrology, Kaiser Permanente, Fontana, CA, USA; 2St. George’s University School of Medicine, West Indies, Grenada; 3Department of Medicine, Division of Pulmonary Critical Care and Sleep Medicine, Stony Brook University Hospital, Stony Brook, NY, USACorrespondence: Talha H ImamDivision of Nephrology, Kaiser Permanente, 9985 Sierra Ave, Fontana, CA 92335, USATel +1 909-427-7521Email thimamhotmail.comAbstract: Medullary Sponge Kidney (MSK) disease is a rare congenital malformation of the distal nephron where cystic dilatation is appreciable in the collecting ducts and renal papillae. Most cases of the malformation are thought to arise from a malfunction within neurotrophic factor and tyrosine kinase interactions. Presentation and prognosis are usually indolent; however, they include urinary tract infections (UTI), nephrolithiasis and nephrocalcinosis, distal renal tubular acidosis (dRTA) and hypocitraturia. With an insidious and asymptomatic onset, MSK is a difficult renal manifestation to both diagnose and treat. Difficulty diagnosing MSK today arises from clinical settings deviating from the usage of contrast methods when assessing the urogenital tract. Many healthcare standards for kidney disorders center diagnosis around imaging techniques rather than contrast methods. This ultimately leads to a decrease in the total number of confirmed cases of MSK. Though intra-venous urogram (IVU) remains as the current gold standard to diagnose MSK, other methods such as endoscopy and Multi-detector computed tomography (MDCT) are being put into place. Endoscopic examination and renal biopsy may allow definitive diagnosis; however, such invasive methods may be considered excessive. Moving forward, differential diagnoses for MSK can be made more precisely when patients present with other renal manifestations, especially in groups at risk. These groups include patients between the age of 20 and 30, patients with other renal malformations, high sodium diet patients, hyperparathyroid patients, and patients with family history of MSK. Basic treatment is aimed at controlling stone formation by stabilizing urinary pH. Treatment for patients, especially those prone to forming stones, includes the application of potassium citrate compounds, prophylactic water and diet control, surgical intervention or lithotripsy for removal of symptomatic kidney stones.Keywords: medullary sponge kidney, nephron, nephrocalcinosis, renal stones Medullary Sponge Kidney. Nephron. Nephrocalcinosis. Renal Stones. Diseases of the genitourinary system. Urology Patail H verfasserin aut Patail H verfasserin aut In International Journal of Nephrology and Renovascular Disease Dove Medical Press, 2009 (2019), Seite 213-218 (DE-627)606031928 (DE-600)2508160-3 11787058 nnns year:2019 pages:213-218 https://doaj.org/article/057016a8e21f4fdeac98d57aae847f68 kostenfrei https://www.dovepress.com/medullary-sponge-kidney-current-perspectives-peer-reviewed-article-IJNRD kostenfrei https://doaj.org/toc/1178-7058 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_11 GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2003 GBV_ILN_2014 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 2019 213-218 |
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Talha H Imam,1 Haris Patail,2 Hassan Patail3 1Division of Nephrology, Kaiser Permanente, Fontana, CA, USA; 2St. George’s University School of Medicine, West Indies, Grenada; 3Department of Medicine, Division of Pulmonary Critical Care and Sleep Medicine, Stony Brook University Hospital, Stony Brook, NY, USACorrespondence: Talha H ImamDivision of Nephrology, Kaiser Permanente, 9985 Sierra Ave, Fontana, CA 92335, USATel +1 909-427-7521Email thimamhotmail.comAbstract: Medullary Sponge Kidney (MSK) disease is a rare congenital malformation of the distal nephron where cystic dilatation is appreciable in the collecting ducts and renal papillae. Most cases of the malformation are thought to arise from a malfunction within neurotrophic factor and tyrosine kinase interactions. Presentation and prognosis are usually indolent; however, they include urinary tract infections (UTI), nephrolithiasis and nephrocalcinosis, distal renal tubular acidosis (dRTA) and hypocitraturia. With an insidious and asymptomatic onset, MSK is a difficult renal manifestation to both diagnose and treat. Difficulty diagnosing MSK today arises from clinical settings deviating from the usage of contrast methods when assessing the urogenital tract. Many healthcare standards for kidney disorders center diagnosis around imaging techniques rather than contrast methods. This ultimately leads to a decrease in the total number of confirmed cases of MSK. Though intra-venous urogram (IVU) remains as the current gold standard to diagnose MSK, other methods such as endoscopy and Multi-detector computed tomography (MDCT) are being put into place. Endoscopic examination and renal biopsy may allow definitive diagnosis; however, such invasive methods may be considered excessive. Moving forward, differential diagnoses for MSK can be made more precisely when patients present with other renal manifestations, especially in groups at risk. These groups include patients between the age of 20 and 30, patients with other renal malformations, high sodium diet patients, hyperparathyroid patients, and patients with family history of MSK. Basic treatment is aimed at controlling stone formation by stabilizing urinary pH. Treatment for patients, especially those prone to forming stones, includes the application of potassium citrate compounds, prophylactic water and diet control, surgical intervention or lithotripsy for removal of symptomatic kidney stones.Keywords: medullary sponge kidney, nephron, nephrocalcinosis, renal stones |
abstractGer |
Talha H Imam,1 Haris Patail,2 Hassan Patail3 1Division of Nephrology, Kaiser Permanente, Fontana, CA, USA; 2St. George’s University School of Medicine, West Indies, Grenada; 3Department of Medicine, Division of Pulmonary Critical Care and Sleep Medicine, Stony Brook University Hospital, Stony Brook, NY, USACorrespondence: Talha H ImamDivision of Nephrology, Kaiser Permanente, 9985 Sierra Ave, Fontana, CA 92335, USATel +1 909-427-7521Email thimamhotmail.comAbstract: Medullary Sponge Kidney (MSK) disease is a rare congenital malformation of the distal nephron where cystic dilatation is appreciable in the collecting ducts and renal papillae. Most cases of the malformation are thought to arise from a malfunction within neurotrophic factor and tyrosine kinase interactions. Presentation and prognosis are usually indolent; however, they include urinary tract infections (UTI), nephrolithiasis and nephrocalcinosis, distal renal tubular acidosis (dRTA) and hypocitraturia. With an insidious and asymptomatic onset, MSK is a difficult renal manifestation to both diagnose and treat. Difficulty diagnosing MSK today arises from clinical settings deviating from the usage of contrast methods when assessing the urogenital tract. Many healthcare standards for kidney disorders center diagnosis around imaging techniques rather than contrast methods. This ultimately leads to a decrease in the total number of confirmed cases of MSK. Though intra-venous urogram (IVU) remains as the current gold standard to diagnose MSK, other methods such as endoscopy and Multi-detector computed tomography (MDCT) are being put into place. Endoscopic examination and renal biopsy may allow definitive diagnosis; however, such invasive methods may be considered excessive. Moving forward, differential diagnoses for MSK can be made more precisely when patients present with other renal manifestations, especially in groups at risk. These groups include patients between the age of 20 and 30, patients with other renal malformations, high sodium diet patients, hyperparathyroid patients, and patients with family history of MSK. Basic treatment is aimed at controlling stone formation by stabilizing urinary pH. Treatment for patients, especially those prone to forming stones, includes the application of potassium citrate compounds, prophylactic water and diet control, surgical intervention or lithotripsy for removal of symptomatic kidney stones.Keywords: medullary sponge kidney, nephron, nephrocalcinosis, renal stones |
abstract_unstemmed |
Talha H Imam,1 Haris Patail,2 Hassan Patail3 1Division of Nephrology, Kaiser Permanente, Fontana, CA, USA; 2St. George’s University School of Medicine, West Indies, Grenada; 3Department of Medicine, Division of Pulmonary Critical Care and Sleep Medicine, Stony Brook University Hospital, Stony Brook, NY, USACorrespondence: Talha H ImamDivision of Nephrology, Kaiser Permanente, 9985 Sierra Ave, Fontana, CA 92335, USATel +1 909-427-7521Email thimamhotmail.comAbstract: Medullary Sponge Kidney (MSK) disease is a rare congenital malformation of the distal nephron where cystic dilatation is appreciable in the collecting ducts and renal papillae. Most cases of the malformation are thought to arise from a malfunction within neurotrophic factor and tyrosine kinase interactions. Presentation and prognosis are usually indolent; however, they include urinary tract infections (UTI), nephrolithiasis and nephrocalcinosis, distal renal tubular acidosis (dRTA) and hypocitraturia. With an insidious and asymptomatic onset, MSK is a difficult renal manifestation to both diagnose and treat. Difficulty diagnosing MSK today arises from clinical settings deviating from the usage of contrast methods when assessing the urogenital tract. Many healthcare standards for kidney disorders center diagnosis around imaging techniques rather than contrast methods. This ultimately leads to a decrease in the total number of confirmed cases of MSK. Though intra-venous urogram (IVU) remains as the current gold standard to diagnose MSK, other methods such as endoscopy and Multi-detector computed tomography (MDCT) are being put into place. Endoscopic examination and renal biopsy may allow definitive diagnosis; however, such invasive methods may be considered excessive. Moving forward, differential diagnoses for MSK can be made more precisely when patients present with other renal manifestations, especially in groups at risk. These groups include patients between the age of 20 and 30, patients with other renal malformations, high sodium diet patients, hyperparathyroid patients, and patients with family history of MSK. Basic treatment is aimed at controlling stone formation by stabilizing urinary pH. Treatment for patients, especially those prone to forming stones, includes the application of potassium citrate compounds, prophylactic water and diet control, surgical intervention or lithotripsy for removal of symptomatic kidney stones.Keywords: medullary sponge kidney, nephron, nephrocalcinosis, renal stones |
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