Profile of Syndromic Kraniosinostosis for 5 Years in RSUD dr.Soetomo Surabaya
Craniosynostosis is a premature cover of one or more sutures, which may occur as part of syndrome (syndromic) or as a separate defect / isolated defect (nonsyndromic). Cohen and Kreirborg state the incidence of Apert and Crouzon syndromes of 15.5: 1,000,000 and 16.5: 1,000,000 per birth. The inciden...
Ausführliche Beschreibung
Autor*in: |
Adinda Widita [verfasserIn] Magda Hutagalung [verfasserIn] Indri Lakhsmi Putri [verfasserIn] |
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E-Artikel |
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Indonesisch |
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2017 |
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Schlagwörter: |
syndromic craniosinostosis, apert syndrome, Crouzon syndrome, Pfeiffer Syndrome |
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Übergeordnetes Werk: |
In: Qanun Medika: Jurnal Kedokteran Fakultas Kedokteran Universitas Muhammadiyah Surabaya - Universitas Muhammadiyah Surabaya, 2017, 1(2017), 02 |
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Übergeordnetes Werk: |
volume:1 ; year:2017 ; number:02 |
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Katalog-ID: |
DOAJ005271614 |
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520 | |a Craniosynostosis is a premature cover of one or more sutures, which may occur as part of syndrome (syndromic) or as a separate defect / isolated defect (nonsyndromic). Cohen and Kreirborg state the incidence of Apert and Crouzon syndromes of 15.5: 1,000,000 and 16.5: 1,000,000 per birth. The incidence of craniosynostosis in Indonesia still not handled properly, as well as low recognition in this disorder. RSUD Dr. Soetomo as an eastern referral hospital, which has one of the centers of plastic surgery education in Indonesia, where craniosynostosis syndromic often occurs, so we have the most total cases handled in Indonesia. This is a retrospective descriptive study discusses more about the profile of patients syndromic craniosinostosis for 5 years in dr. Soetomo Surabaya, performed on twenty-four first syndromic craniosinostosis patients at Dr. Soetomo Surabaya period 1 January 2008 - 31 December 2013. Out of 24 total patients, 12 cases of apert (29%), 6 crouzon cases (54%) and 3 cases of pfeiffer (17%) were obtained. Based on sex, more commonly found in women (54%). With the most common age the patient comes first is aged 5-10 years (37%). Each patient has an average of 2 surgeries, with a type of surgical action on cranial vault remodeling patients. Abnormalities of syndromic craniosinostosis found the most common in women and apert syndrome in RSUD dr.Sutomo. Where the most common age when the arrival of 5-10 years, caused by the late diagnosis of the disorder | ||
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(DE-627)DOAJ005271614 (DE-599)DOAJ713ebc8316a34549b7f4b76e5d1293aa DE-627 ger DE-627 rakwb ind R5-920 Adinda Widita verfasserin aut Profile of Syndromic Kraniosinostosis for 5 Years in RSUD dr.Soetomo Surabaya 2017 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Craniosynostosis is a premature cover of one or more sutures, which may occur as part of syndrome (syndromic) or as a separate defect / isolated defect (nonsyndromic). Cohen and Kreirborg state the incidence of Apert and Crouzon syndromes of 15.5: 1,000,000 and 16.5: 1,000,000 per birth. The incidence of craniosynostosis in Indonesia still not handled properly, as well as low recognition in this disorder. RSUD Dr. Soetomo as an eastern referral hospital, which has one of the centers of plastic surgery education in Indonesia, where craniosynostosis syndromic often occurs, so we have the most total cases handled in Indonesia. This is a retrospective descriptive study discusses more about the profile of patients syndromic craniosinostosis for 5 years in dr. Soetomo Surabaya, performed on twenty-four first syndromic craniosinostosis patients at Dr. Soetomo Surabaya period 1 January 2008 - 31 December 2013. Out of 24 total patients, 12 cases of apert (29%), 6 crouzon cases (54%) and 3 cases of pfeiffer (17%) were obtained. Based on sex, more commonly found in women (54%). With the most common age the patient comes first is aged 5-10 years (37%). Each patient has an average of 2 surgeries, with a type of surgical action on cranial vault remodeling patients. Abnormalities of syndromic craniosinostosis found the most common in women and apert syndrome in RSUD dr.Sutomo. Where the most common age when the arrival of 5-10 years, caused by the late diagnosis of the disorder syndromic craniosinostosis, apert syndrome, Crouzon syndrome, Pfeiffer Syndrome Medicine (General) Magda Hutagalung verfasserin aut Indri Lakhsmi Putri verfasserin aut In Qanun Medika: Jurnal Kedokteran Fakultas Kedokteran Universitas Muhammadiyah Surabaya Universitas Muhammadiyah Surabaya, 2017 1(2017), 02 (DE-627)1760605484 25489526 nnns volume:1 year:2017 number:02 https://doaj.org/article/713ebc8316a34549b7f4b76e5d1293aa kostenfrei http://journal.um-surabaya.ac.id/index.php/qanunmedika/article/view/555 kostenfrei https://doaj.org/toc/2541-2272 Journal toc kostenfrei https://doaj.org/toc/2548-9526 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ AR 1 2017 02 |
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(DE-627)DOAJ005271614 (DE-599)DOAJ713ebc8316a34549b7f4b76e5d1293aa DE-627 ger DE-627 rakwb ind R5-920 Adinda Widita verfasserin aut Profile of Syndromic Kraniosinostosis for 5 Years in RSUD dr.Soetomo Surabaya 2017 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Craniosynostosis is a premature cover of one or more sutures, which may occur as part of syndrome (syndromic) or as a separate defect / isolated defect (nonsyndromic). Cohen and Kreirborg state the incidence of Apert and Crouzon syndromes of 15.5: 1,000,000 and 16.5: 1,000,000 per birth. The incidence of craniosynostosis in Indonesia still not handled properly, as well as low recognition in this disorder. RSUD Dr. Soetomo as an eastern referral hospital, which has one of the centers of plastic surgery education in Indonesia, where craniosynostosis syndromic often occurs, so we have the most total cases handled in Indonesia. This is a retrospective descriptive study discusses more about the profile of patients syndromic craniosinostosis for 5 years in dr. Soetomo Surabaya, performed on twenty-four first syndromic craniosinostosis patients at Dr. Soetomo Surabaya period 1 January 2008 - 31 December 2013. Out of 24 total patients, 12 cases of apert (29%), 6 crouzon cases (54%) and 3 cases of pfeiffer (17%) were obtained. Based on sex, more commonly found in women (54%). With the most common age the patient comes first is aged 5-10 years (37%). Each patient has an average of 2 surgeries, with a type of surgical action on cranial vault remodeling patients. Abnormalities of syndromic craniosinostosis found the most common in women and apert syndrome in RSUD dr.Sutomo. Where the most common age when the arrival of 5-10 years, caused by the late diagnosis of the disorder syndromic craniosinostosis, apert syndrome, Crouzon syndrome, Pfeiffer Syndrome Medicine (General) Magda Hutagalung verfasserin aut Indri Lakhsmi Putri verfasserin aut In Qanun Medika: Jurnal Kedokteran Fakultas Kedokteran Universitas Muhammadiyah Surabaya Universitas Muhammadiyah Surabaya, 2017 1(2017), 02 (DE-627)1760605484 25489526 nnns volume:1 year:2017 number:02 https://doaj.org/article/713ebc8316a34549b7f4b76e5d1293aa kostenfrei http://journal.um-surabaya.ac.id/index.php/qanunmedika/article/view/555 kostenfrei https://doaj.org/toc/2541-2272 Journal toc kostenfrei https://doaj.org/toc/2548-9526 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ AR 1 2017 02 |
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(DE-627)DOAJ005271614 (DE-599)DOAJ713ebc8316a34549b7f4b76e5d1293aa DE-627 ger DE-627 rakwb ind R5-920 Adinda Widita verfasserin aut Profile of Syndromic Kraniosinostosis for 5 Years in RSUD dr.Soetomo Surabaya 2017 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Craniosynostosis is a premature cover of one or more sutures, which may occur as part of syndrome (syndromic) or as a separate defect / isolated defect (nonsyndromic). Cohen and Kreirborg state the incidence of Apert and Crouzon syndromes of 15.5: 1,000,000 and 16.5: 1,000,000 per birth. The incidence of craniosynostosis in Indonesia still not handled properly, as well as low recognition in this disorder. RSUD Dr. Soetomo as an eastern referral hospital, which has one of the centers of plastic surgery education in Indonesia, where craniosynostosis syndromic often occurs, so we have the most total cases handled in Indonesia. This is a retrospective descriptive study discusses more about the profile of patients syndromic craniosinostosis for 5 years in dr. Soetomo Surabaya, performed on twenty-four first syndromic craniosinostosis patients at Dr. Soetomo Surabaya period 1 January 2008 - 31 December 2013. Out of 24 total patients, 12 cases of apert (29%), 6 crouzon cases (54%) and 3 cases of pfeiffer (17%) were obtained. Based on sex, more commonly found in women (54%). With the most common age the patient comes first is aged 5-10 years (37%). Each patient has an average of 2 surgeries, with a type of surgical action on cranial vault remodeling patients. Abnormalities of syndromic craniosinostosis found the most common in women and apert syndrome in RSUD dr.Sutomo. Where the most common age when the arrival of 5-10 years, caused by the late diagnosis of the disorder syndromic craniosinostosis, apert syndrome, Crouzon syndrome, Pfeiffer Syndrome Medicine (General) Magda Hutagalung verfasserin aut Indri Lakhsmi Putri verfasserin aut In Qanun Medika: Jurnal Kedokteran Fakultas Kedokteran Universitas Muhammadiyah Surabaya Universitas Muhammadiyah Surabaya, 2017 1(2017), 02 (DE-627)1760605484 25489526 nnns volume:1 year:2017 number:02 https://doaj.org/article/713ebc8316a34549b7f4b76e5d1293aa kostenfrei http://journal.um-surabaya.ac.id/index.php/qanunmedika/article/view/555 kostenfrei https://doaj.org/toc/2541-2272 Journal toc kostenfrei https://doaj.org/toc/2548-9526 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ AR 1 2017 02 |
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(DE-627)DOAJ005271614 (DE-599)DOAJ713ebc8316a34549b7f4b76e5d1293aa DE-627 ger DE-627 rakwb ind R5-920 Adinda Widita verfasserin aut Profile of Syndromic Kraniosinostosis for 5 Years in RSUD dr.Soetomo Surabaya 2017 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Craniosynostosis is a premature cover of one or more sutures, which may occur as part of syndrome (syndromic) or as a separate defect / isolated defect (nonsyndromic). Cohen and Kreirborg state the incidence of Apert and Crouzon syndromes of 15.5: 1,000,000 and 16.5: 1,000,000 per birth. The incidence of craniosynostosis in Indonesia still not handled properly, as well as low recognition in this disorder. RSUD Dr. Soetomo as an eastern referral hospital, which has one of the centers of plastic surgery education in Indonesia, where craniosynostosis syndromic often occurs, so we have the most total cases handled in Indonesia. This is a retrospective descriptive study discusses more about the profile of patients syndromic craniosinostosis for 5 years in dr. Soetomo Surabaya, performed on twenty-four first syndromic craniosinostosis patients at Dr. Soetomo Surabaya period 1 January 2008 - 31 December 2013. Out of 24 total patients, 12 cases of apert (29%), 6 crouzon cases (54%) and 3 cases of pfeiffer (17%) were obtained. Based on sex, more commonly found in women (54%). With the most common age the patient comes first is aged 5-10 years (37%). Each patient has an average of 2 surgeries, with a type of surgical action on cranial vault remodeling patients. Abnormalities of syndromic craniosinostosis found the most common in women and apert syndrome in RSUD dr.Sutomo. Where the most common age when the arrival of 5-10 years, caused by the late diagnosis of the disorder syndromic craniosinostosis, apert syndrome, Crouzon syndrome, Pfeiffer Syndrome Medicine (General) Magda Hutagalung verfasserin aut Indri Lakhsmi Putri verfasserin aut In Qanun Medika: Jurnal Kedokteran Fakultas Kedokteran Universitas Muhammadiyah Surabaya Universitas Muhammadiyah Surabaya, 2017 1(2017), 02 (DE-627)1760605484 25489526 nnns volume:1 year:2017 number:02 https://doaj.org/article/713ebc8316a34549b7f4b76e5d1293aa kostenfrei http://journal.um-surabaya.ac.id/index.php/qanunmedika/article/view/555 kostenfrei https://doaj.org/toc/2541-2272 Journal toc kostenfrei https://doaj.org/toc/2548-9526 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ AR 1 2017 02 |
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Profile of Syndromic Kraniosinostosis for 5 Years in RSUD dr.Soetomo Surabaya |
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Profile of Syndromic Kraniosinostosis for 5 Years in RSUD dr.Soetomo Surabaya |
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Adinda Widita |
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Qanun Medika: Jurnal Kedokteran Fakultas Kedokteran Universitas Muhammadiyah Surabaya |
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Profile of Syndromic Kraniosinostosis for 5 Years in RSUD dr.Soetomo Surabaya |
abstract |
Craniosynostosis is a premature cover of one or more sutures, which may occur as part of syndrome (syndromic) or as a separate defect / isolated defect (nonsyndromic). Cohen and Kreirborg state the incidence of Apert and Crouzon syndromes of 15.5: 1,000,000 and 16.5: 1,000,000 per birth. The incidence of craniosynostosis in Indonesia still not handled properly, as well as low recognition in this disorder. RSUD Dr. Soetomo as an eastern referral hospital, which has one of the centers of plastic surgery education in Indonesia, where craniosynostosis syndromic often occurs, so we have the most total cases handled in Indonesia. This is a retrospective descriptive study discusses more about the profile of patients syndromic craniosinostosis for 5 years in dr. Soetomo Surabaya, performed on twenty-four first syndromic craniosinostosis patients at Dr. Soetomo Surabaya period 1 January 2008 - 31 December 2013. Out of 24 total patients, 12 cases of apert (29%), 6 crouzon cases (54%) and 3 cases of pfeiffer (17%) were obtained. Based on sex, more commonly found in women (54%). With the most common age the patient comes first is aged 5-10 years (37%). Each patient has an average of 2 surgeries, with a type of surgical action on cranial vault remodeling patients. Abnormalities of syndromic craniosinostosis found the most common in women and apert syndrome in RSUD dr.Sutomo. Where the most common age when the arrival of 5-10 years, caused by the late diagnosis of the disorder |
abstractGer |
Craniosynostosis is a premature cover of one or more sutures, which may occur as part of syndrome (syndromic) or as a separate defect / isolated defect (nonsyndromic). Cohen and Kreirborg state the incidence of Apert and Crouzon syndromes of 15.5: 1,000,000 and 16.5: 1,000,000 per birth. The incidence of craniosynostosis in Indonesia still not handled properly, as well as low recognition in this disorder. RSUD Dr. Soetomo as an eastern referral hospital, which has one of the centers of plastic surgery education in Indonesia, where craniosynostosis syndromic often occurs, so we have the most total cases handled in Indonesia. This is a retrospective descriptive study discusses more about the profile of patients syndromic craniosinostosis for 5 years in dr. Soetomo Surabaya, performed on twenty-four first syndromic craniosinostosis patients at Dr. Soetomo Surabaya period 1 January 2008 - 31 December 2013. Out of 24 total patients, 12 cases of apert (29%), 6 crouzon cases (54%) and 3 cases of pfeiffer (17%) were obtained. Based on sex, more commonly found in women (54%). With the most common age the patient comes first is aged 5-10 years (37%). Each patient has an average of 2 surgeries, with a type of surgical action on cranial vault remodeling patients. Abnormalities of syndromic craniosinostosis found the most common in women and apert syndrome in RSUD dr.Sutomo. Where the most common age when the arrival of 5-10 years, caused by the late diagnosis of the disorder |
abstract_unstemmed |
Craniosynostosis is a premature cover of one or more sutures, which may occur as part of syndrome (syndromic) or as a separate defect / isolated defect (nonsyndromic). Cohen and Kreirborg state the incidence of Apert and Crouzon syndromes of 15.5: 1,000,000 and 16.5: 1,000,000 per birth. The incidence of craniosynostosis in Indonesia still not handled properly, as well as low recognition in this disorder. RSUD Dr. Soetomo as an eastern referral hospital, which has one of the centers of plastic surgery education in Indonesia, where craniosynostosis syndromic often occurs, so we have the most total cases handled in Indonesia. This is a retrospective descriptive study discusses more about the profile of patients syndromic craniosinostosis for 5 years in dr. Soetomo Surabaya, performed on twenty-four first syndromic craniosinostosis patients at Dr. Soetomo Surabaya period 1 January 2008 - 31 December 2013. Out of 24 total patients, 12 cases of apert (29%), 6 crouzon cases (54%) and 3 cases of pfeiffer (17%) were obtained. Based on sex, more commonly found in women (54%). With the most common age the patient comes first is aged 5-10 years (37%). Each patient has an average of 2 surgeries, with a type of surgical action on cranial vault remodeling patients. Abnormalities of syndromic craniosinostosis found the most common in women and apert syndrome in RSUD dr.Sutomo. Where the most common age when the arrival of 5-10 years, caused by the late diagnosis of the disorder |
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Profile of Syndromic Kraniosinostosis for 5 Years in RSUD dr.Soetomo Surabaya |
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https://doaj.org/article/713ebc8316a34549b7f4b76e5d1293aa http://journal.um-surabaya.ac.id/index.php/qanunmedika/article/view/555 https://doaj.org/toc/2541-2272 https://doaj.org/toc/2548-9526 |
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