Plexiform neurofibroma in the hepatic hilum associated with neurofibromatosis type 1: case report
We present an extremely rare case of plexiform neurofibroma involving the hepatic hilum. A 24-year old woman who had been diagnosed with neurofibromatosis type 1 was referred to our hospital for evaluation of an abdominal mass found on computed tomography and progressive aggravation of intermittent...
Ausführliche Beschreibung
Autor*in: |
Sojun Hoshimoto [verfasserIn] Zenichi Morise [verfasserIn] Chinatsu Takeura [verfasserIn] Atsushi Sugioka [verfasserIn] Yasuhiro Okabe [verfasserIn] Tadashi Kagawa [verfasserIn] Yoshinao Tanahashi [verfasserIn] Masahiro Ikeda [verfasserIn] Yoshikazu Mizoguchi [verfasserIn] |
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E-Artikel |
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Sprache: |
Englisch |
Erschienen: |
2009 |
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Übergeordnetes Werk: |
In: Rare Tumors ; 1(2009), 1, Seite e23-e23 volume:1 ; year:2009 ; number:1 ; pages:e23-e23 |
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Links: |
Link aufrufen |
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DOI / URN: |
10.4081/rt.2009.e23 |
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Katalog-ID: |
DOAJ015435326 |
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10.4081/rt.2009.e23 doi (DE-627)DOAJ015435326 (DE-599)DOAJ1cb8f60b3ba14d3dacd99961ff524ade DE-627 ger DE-627 rakwb eng RC254-282 Sojun Hoshimoto verfasserin aut Plexiform neurofibroma in the hepatic hilum associated with neurofibromatosis type 1: case report 2009 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier We present an extremely rare case of plexiform neurofibroma involving the hepatic hilum. A 24-year old woman who had been diagnosed with neurofibromatosis type 1 was referred to our hospital for evaluation of an abdominal mass found on computed tomography and progressive aggravation of intermittent abdominal pain. Abdominal computed tomography revealed a multilobulated non-enhancing mass involving the celiac trunk and hepatic artery, that extended to the hepatic hilum through the hepatoduodenal ligament. Magnetic resonance imaging showed the lesion extending along the intrahepatic Glisson’s sheath. Based on the imaging findings, the patient was diagnosed to have a neurofibroma, although sarcomatous differentiation could not be excluded. The tumor was resected, leaving behind the intrahepatic extension, with the aim of alleviating the abdominal pain and preventing obstructive jaundice. Histopathological examination revealed the diagnosis of plexiform neurofibroma. At present, three years after the surgery, the patient remains symptom-free, without any evidence of recurrence. plexiform neurofibroma neurofibromatosis hepatic hilum Neoplasms. Tumors. Oncology. Including cancer and carcinogens Zenichi Morise verfasserin aut Chinatsu Takeura verfasserin aut Atsushi Sugioka verfasserin aut Yasuhiro Okabe verfasserin aut Tadashi Kagawa verfasserin aut Yoshinao Tanahashi verfasserin aut Masahiro Ikeda verfasserin aut Yoshikazu Mizoguchi verfasserin aut In Rare Tumors 1(2009), 1, Seite e23-e23 volume:1 year:2009 number:1 pages:e23-e23 https://doi.org/10.4081/rt.2009.e23 kostenfrei https://doaj.org/article/1cb8f60b3ba14d3dacd99961ff524ade kostenfrei http://www.pagepress.org/journals/index.php/rt/article/view/1086 kostenfrei https://doaj.org/toc/2036-3603 Journal toc kostenfrei https://doaj.org/toc/2036-3613 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ SSG-OLC-PHA AR 1 2009 1 e23-e23 |
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10.4081/rt.2009.e23 doi (DE-627)DOAJ015435326 (DE-599)DOAJ1cb8f60b3ba14d3dacd99961ff524ade DE-627 ger DE-627 rakwb eng RC254-282 Sojun Hoshimoto verfasserin aut Plexiform neurofibroma in the hepatic hilum associated with neurofibromatosis type 1: case report 2009 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier We present an extremely rare case of plexiform neurofibroma involving the hepatic hilum. A 24-year old woman who had been diagnosed with neurofibromatosis type 1 was referred to our hospital for evaluation of an abdominal mass found on computed tomography and progressive aggravation of intermittent abdominal pain. Abdominal computed tomography revealed a multilobulated non-enhancing mass involving the celiac trunk and hepatic artery, that extended to the hepatic hilum through the hepatoduodenal ligament. Magnetic resonance imaging showed the lesion extending along the intrahepatic Glisson’s sheath. Based on the imaging findings, the patient was diagnosed to have a neurofibroma, although sarcomatous differentiation could not be excluded. The tumor was resected, leaving behind the intrahepatic extension, with the aim of alleviating the abdominal pain and preventing obstructive jaundice. Histopathological examination revealed the diagnosis of plexiform neurofibroma. At present, three years after the surgery, the patient remains symptom-free, without any evidence of recurrence. plexiform neurofibroma neurofibromatosis hepatic hilum Neoplasms. Tumors. Oncology. Including cancer and carcinogens Zenichi Morise verfasserin aut Chinatsu Takeura verfasserin aut Atsushi Sugioka verfasserin aut Yasuhiro Okabe verfasserin aut Tadashi Kagawa verfasserin aut Yoshinao Tanahashi verfasserin aut Masahiro Ikeda verfasserin aut Yoshikazu Mizoguchi verfasserin aut In Rare Tumors 1(2009), 1, Seite e23-e23 volume:1 year:2009 number:1 pages:e23-e23 https://doi.org/10.4081/rt.2009.e23 kostenfrei https://doaj.org/article/1cb8f60b3ba14d3dacd99961ff524ade kostenfrei http://www.pagepress.org/journals/index.php/rt/article/view/1086 kostenfrei https://doaj.org/toc/2036-3603 Journal toc kostenfrei https://doaj.org/toc/2036-3613 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ SSG-OLC-PHA AR 1 2009 1 e23-e23 |
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10.4081/rt.2009.e23 doi (DE-627)DOAJ015435326 (DE-599)DOAJ1cb8f60b3ba14d3dacd99961ff524ade DE-627 ger DE-627 rakwb eng RC254-282 Sojun Hoshimoto verfasserin aut Plexiform neurofibroma in the hepatic hilum associated with neurofibromatosis type 1: case report 2009 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier We present an extremely rare case of plexiform neurofibroma involving the hepatic hilum. A 24-year old woman who had been diagnosed with neurofibromatosis type 1 was referred to our hospital for evaluation of an abdominal mass found on computed tomography and progressive aggravation of intermittent abdominal pain. Abdominal computed tomography revealed a multilobulated non-enhancing mass involving the celiac trunk and hepatic artery, that extended to the hepatic hilum through the hepatoduodenal ligament. Magnetic resonance imaging showed the lesion extending along the intrahepatic Glisson’s sheath. Based on the imaging findings, the patient was diagnosed to have a neurofibroma, although sarcomatous differentiation could not be excluded. The tumor was resected, leaving behind the intrahepatic extension, with the aim of alleviating the abdominal pain and preventing obstructive jaundice. Histopathological examination revealed the diagnosis of plexiform neurofibroma. At present, three years after the surgery, the patient remains symptom-free, without any evidence of recurrence. plexiform neurofibroma neurofibromatosis hepatic hilum Neoplasms. Tumors. Oncology. Including cancer and carcinogens Zenichi Morise verfasserin aut Chinatsu Takeura verfasserin aut Atsushi Sugioka verfasserin aut Yasuhiro Okabe verfasserin aut Tadashi Kagawa verfasserin aut Yoshinao Tanahashi verfasserin aut Masahiro Ikeda verfasserin aut Yoshikazu Mizoguchi verfasserin aut In Rare Tumors 1(2009), 1, Seite e23-e23 volume:1 year:2009 number:1 pages:e23-e23 https://doi.org/10.4081/rt.2009.e23 kostenfrei https://doaj.org/article/1cb8f60b3ba14d3dacd99961ff524ade kostenfrei http://www.pagepress.org/journals/index.php/rt/article/view/1086 kostenfrei https://doaj.org/toc/2036-3603 Journal toc kostenfrei https://doaj.org/toc/2036-3613 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ SSG-OLC-PHA AR 1 2009 1 e23-e23 |
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10.4081/rt.2009.e23 doi (DE-627)DOAJ015435326 (DE-599)DOAJ1cb8f60b3ba14d3dacd99961ff524ade DE-627 ger DE-627 rakwb eng RC254-282 Sojun Hoshimoto verfasserin aut Plexiform neurofibroma in the hepatic hilum associated with neurofibromatosis type 1: case report 2009 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier We present an extremely rare case of plexiform neurofibroma involving the hepatic hilum. A 24-year old woman who had been diagnosed with neurofibromatosis type 1 was referred to our hospital for evaluation of an abdominal mass found on computed tomography and progressive aggravation of intermittent abdominal pain. Abdominal computed tomography revealed a multilobulated non-enhancing mass involving the celiac trunk and hepatic artery, that extended to the hepatic hilum through the hepatoduodenal ligament. Magnetic resonance imaging showed the lesion extending along the intrahepatic Glisson’s sheath. Based on the imaging findings, the patient was diagnosed to have a neurofibroma, although sarcomatous differentiation could not be excluded. The tumor was resected, leaving behind the intrahepatic extension, with the aim of alleviating the abdominal pain and preventing obstructive jaundice. Histopathological examination revealed the diagnosis of plexiform neurofibroma. At present, three years after the surgery, the patient remains symptom-free, without any evidence of recurrence. plexiform neurofibroma neurofibromatosis hepatic hilum Neoplasms. Tumors. Oncology. Including cancer and carcinogens Zenichi Morise verfasserin aut Chinatsu Takeura verfasserin aut Atsushi Sugioka verfasserin aut Yasuhiro Okabe verfasserin aut Tadashi Kagawa verfasserin aut Yoshinao Tanahashi verfasserin aut Masahiro Ikeda verfasserin aut Yoshikazu Mizoguchi verfasserin aut In Rare Tumors 1(2009), 1, Seite e23-e23 volume:1 year:2009 number:1 pages:e23-e23 https://doi.org/10.4081/rt.2009.e23 kostenfrei https://doaj.org/article/1cb8f60b3ba14d3dacd99961ff524ade kostenfrei http://www.pagepress.org/journals/index.php/rt/article/view/1086 kostenfrei https://doaj.org/toc/2036-3603 Journal toc kostenfrei https://doaj.org/toc/2036-3613 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ SSG-OLC-PHA AR 1 2009 1 e23-e23 |
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Sojun Hoshimoto Zenichi Morise Chinatsu Takeura Atsushi Sugioka Yasuhiro Okabe Tadashi Kagawa Yoshinao Tanahashi Masahiro Ikeda Yoshikazu Mizoguchi |
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plexiform neurofibroma in the hepatic hilum associated with neurofibromatosis type 1: case report |
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Plexiform neurofibroma in the hepatic hilum associated with neurofibromatosis type 1: case report |
abstract |
We present an extremely rare case of plexiform neurofibroma involving the hepatic hilum. A 24-year old woman who had been diagnosed with neurofibromatosis type 1 was referred to our hospital for evaluation of an abdominal mass found on computed tomography and progressive aggravation of intermittent abdominal pain. Abdominal computed tomography revealed a multilobulated non-enhancing mass involving the celiac trunk and hepatic artery, that extended to the hepatic hilum through the hepatoduodenal ligament. Magnetic resonance imaging showed the lesion extending along the intrahepatic Glisson’s sheath. Based on the imaging findings, the patient was diagnosed to have a neurofibroma, although sarcomatous differentiation could not be excluded. The tumor was resected, leaving behind the intrahepatic extension, with the aim of alleviating the abdominal pain and preventing obstructive jaundice. Histopathological examination revealed the diagnosis of plexiform neurofibroma. At present, three years after the surgery, the patient remains symptom-free, without any evidence of recurrence. |
abstractGer |
We present an extremely rare case of plexiform neurofibroma involving the hepatic hilum. A 24-year old woman who had been diagnosed with neurofibromatosis type 1 was referred to our hospital for evaluation of an abdominal mass found on computed tomography and progressive aggravation of intermittent abdominal pain. Abdominal computed tomography revealed a multilobulated non-enhancing mass involving the celiac trunk and hepatic artery, that extended to the hepatic hilum through the hepatoduodenal ligament. Magnetic resonance imaging showed the lesion extending along the intrahepatic Glisson’s sheath. Based on the imaging findings, the patient was diagnosed to have a neurofibroma, although sarcomatous differentiation could not be excluded. The tumor was resected, leaving behind the intrahepatic extension, with the aim of alleviating the abdominal pain and preventing obstructive jaundice. Histopathological examination revealed the diagnosis of plexiform neurofibroma. At present, three years after the surgery, the patient remains symptom-free, without any evidence of recurrence. |
abstract_unstemmed |
We present an extremely rare case of plexiform neurofibroma involving the hepatic hilum. A 24-year old woman who had been diagnosed with neurofibromatosis type 1 was referred to our hospital for evaluation of an abdominal mass found on computed tomography and progressive aggravation of intermittent abdominal pain. Abdominal computed tomography revealed a multilobulated non-enhancing mass involving the celiac trunk and hepatic artery, that extended to the hepatic hilum through the hepatoduodenal ligament. Magnetic resonance imaging showed the lesion extending along the intrahepatic Glisson’s sheath. Based on the imaging findings, the patient was diagnosed to have a neurofibroma, although sarcomatous differentiation could not be excluded. The tumor was resected, leaving behind the intrahepatic extension, with the aim of alleviating the abdominal pain and preventing obstructive jaundice. Histopathological examination revealed the diagnosis of plexiform neurofibroma. At present, three years after the surgery, the patient remains symptom-free, without any evidence of recurrence. |
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Plexiform neurofibroma in the hepatic hilum associated with neurofibromatosis type 1: case report |
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Zenichi Morise Chinatsu Takeura Atsushi Sugioka Yasuhiro Okabe Tadashi Kagawa Yoshinao Tanahashi Masahiro Ikeda Yoshikazu Mizoguchi |
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