Non-Coding RNAs and Hereditary Hemorrhagic Telangiectasia
Non-coding RNAs (ncRNAs) are functional ribonucleic acid (RNA) species that include microRNAs (miRs), a class of short non-coding RNAs (∼21–25 nucleotides), and long non-coding RNAs (lncRNAs) consisting of more than 200 nucleotides. They regulate gene expression post-transcriptionally and are involv...
Ausführliche Beschreibung
Autor*in: |
Anthony Cannavicci [verfasserIn] Qiuwang Zhang [verfasserIn] Michael J. B. Kutryk [verfasserIn] |
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E-Artikel |
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Sprache: |
Englisch |
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2020 |
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Übergeordnetes Werk: |
In: Journal of Clinical Medicine - MDPI AG, 2013, 9(2020), 10, p 3333 |
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Übergeordnetes Werk: |
volume:9 ; year:2020 ; number:10, p 3333 |
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DOI / URN: |
10.3390/jcm9103333 |
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Katalog-ID: |
DOAJ016765745 |
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10.3390/jcm9103333 doi (DE-627)DOAJ016765745 (DE-599)DOAJ26e6c6db9cb540dd916163029680e524 DE-627 ger DE-627 rakwb eng Anthony Cannavicci verfasserin aut Non-Coding RNAs and Hereditary Hemorrhagic Telangiectasia 2020 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Non-coding RNAs (ncRNAs) are functional ribonucleic acid (RNA) species that include microRNAs (miRs), a class of short non-coding RNAs (∼21–25 nucleotides), and long non-coding RNAs (lncRNAs) consisting of more than 200 nucleotides. They regulate gene expression post-transcriptionally and are involved in a wide range of pathophysiological processes. Hereditary hemorrhagic telangiectasia (HHT) is a rare disorder inherited in an autosomal dominant fashion characterized by vascular dysplasia. Patients can develop life-threatening vascular malformations and experience severe hemorrhaging. Effective pharmacological therapies are limited. The study of ncRNAs in HHT is an emerging field with great promise. This review will explore the current literature on the involvement of ncRNAs in HHT as diagnostic and pathogenic factors. non-coding RNAs microRNAs long non-coding RNAs hereditary hemorrhagic telangiectasia biomarkers endothelial cells Medicine R Qiuwang Zhang verfasserin aut Michael J. B. Kutryk verfasserin aut In Journal of Clinical Medicine MDPI AG, 2013 9(2020), 10, p 3333 (DE-627)718632478 (DE-600)2662592-1 20770383 nnns volume:9 year:2020 number:10, p 3333 https://doi.org/10.3390/jcm9103333 kostenfrei https://doaj.org/article/26e6c6db9cb540dd916163029680e524 kostenfrei https://www.mdpi.com/2077-0383/9/10/3333 kostenfrei https://doaj.org/toc/2077-0383 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2005 GBV_ILN_2009 GBV_ILN_2014 GBV_ILN_2055 GBV_ILN_2111 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 9 2020 10, p 3333 |
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10.3390/jcm9103333 doi (DE-627)DOAJ016765745 (DE-599)DOAJ26e6c6db9cb540dd916163029680e524 DE-627 ger DE-627 rakwb eng Anthony Cannavicci verfasserin aut Non-Coding RNAs and Hereditary Hemorrhagic Telangiectasia 2020 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Non-coding RNAs (ncRNAs) are functional ribonucleic acid (RNA) species that include microRNAs (miRs), a class of short non-coding RNAs (∼21–25 nucleotides), and long non-coding RNAs (lncRNAs) consisting of more than 200 nucleotides. They regulate gene expression post-transcriptionally and are involved in a wide range of pathophysiological processes. Hereditary hemorrhagic telangiectasia (HHT) is a rare disorder inherited in an autosomal dominant fashion characterized by vascular dysplasia. Patients can develop life-threatening vascular malformations and experience severe hemorrhaging. Effective pharmacological therapies are limited. The study of ncRNAs in HHT is an emerging field with great promise. This review will explore the current literature on the involvement of ncRNAs in HHT as diagnostic and pathogenic factors. non-coding RNAs microRNAs long non-coding RNAs hereditary hemorrhagic telangiectasia biomarkers endothelial cells Medicine R Qiuwang Zhang verfasserin aut Michael J. B. Kutryk verfasserin aut In Journal of Clinical Medicine MDPI AG, 2013 9(2020), 10, p 3333 (DE-627)718632478 (DE-600)2662592-1 20770383 nnns volume:9 year:2020 number:10, p 3333 https://doi.org/10.3390/jcm9103333 kostenfrei https://doaj.org/article/26e6c6db9cb540dd916163029680e524 kostenfrei https://www.mdpi.com/2077-0383/9/10/3333 kostenfrei https://doaj.org/toc/2077-0383 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2005 GBV_ILN_2009 GBV_ILN_2014 GBV_ILN_2055 GBV_ILN_2111 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 9 2020 10, p 3333 |
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10.3390/jcm9103333 doi (DE-627)DOAJ016765745 (DE-599)DOAJ26e6c6db9cb540dd916163029680e524 DE-627 ger DE-627 rakwb eng Anthony Cannavicci verfasserin aut Non-Coding RNAs and Hereditary Hemorrhagic Telangiectasia 2020 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Non-coding RNAs (ncRNAs) are functional ribonucleic acid (RNA) species that include microRNAs (miRs), a class of short non-coding RNAs (∼21–25 nucleotides), and long non-coding RNAs (lncRNAs) consisting of more than 200 nucleotides. They regulate gene expression post-transcriptionally and are involved in a wide range of pathophysiological processes. Hereditary hemorrhagic telangiectasia (HHT) is a rare disorder inherited in an autosomal dominant fashion characterized by vascular dysplasia. Patients can develop life-threatening vascular malformations and experience severe hemorrhaging. Effective pharmacological therapies are limited. The study of ncRNAs in HHT is an emerging field with great promise. This review will explore the current literature on the involvement of ncRNAs in HHT as diagnostic and pathogenic factors. non-coding RNAs microRNAs long non-coding RNAs hereditary hemorrhagic telangiectasia biomarkers endothelial cells Medicine R Qiuwang Zhang verfasserin aut Michael J. B. Kutryk verfasserin aut In Journal of Clinical Medicine MDPI AG, 2013 9(2020), 10, p 3333 (DE-627)718632478 (DE-600)2662592-1 20770383 nnns volume:9 year:2020 number:10, p 3333 https://doi.org/10.3390/jcm9103333 kostenfrei https://doaj.org/article/26e6c6db9cb540dd916163029680e524 kostenfrei https://www.mdpi.com/2077-0383/9/10/3333 kostenfrei https://doaj.org/toc/2077-0383 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2005 GBV_ILN_2009 GBV_ILN_2014 GBV_ILN_2055 GBV_ILN_2111 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 9 2020 10, p 3333 |
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10.3390/jcm9103333 doi (DE-627)DOAJ016765745 (DE-599)DOAJ26e6c6db9cb540dd916163029680e524 DE-627 ger DE-627 rakwb eng Anthony Cannavicci verfasserin aut Non-Coding RNAs and Hereditary Hemorrhagic Telangiectasia 2020 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Non-coding RNAs (ncRNAs) are functional ribonucleic acid (RNA) species that include microRNAs (miRs), a class of short non-coding RNAs (∼21–25 nucleotides), and long non-coding RNAs (lncRNAs) consisting of more than 200 nucleotides. They regulate gene expression post-transcriptionally and are involved in a wide range of pathophysiological processes. Hereditary hemorrhagic telangiectasia (HHT) is a rare disorder inherited in an autosomal dominant fashion characterized by vascular dysplasia. Patients can develop life-threatening vascular malformations and experience severe hemorrhaging. Effective pharmacological therapies are limited. The study of ncRNAs in HHT is an emerging field with great promise. This review will explore the current literature on the involvement of ncRNAs in HHT as diagnostic and pathogenic factors. non-coding RNAs microRNAs long non-coding RNAs hereditary hemorrhagic telangiectasia biomarkers endothelial cells Medicine R Qiuwang Zhang verfasserin aut Michael J. B. Kutryk verfasserin aut In Journal of Clinical Medicine MDPI AG, 2013 9(2020), 10, p 3333 (DE-627)718632478 (DE-600)2662592-1 20770383 nnns volume:9 year:2020 number:10, p 3333 https://doi.org/10.3390/jcm9103333 kostenfrei https://doaj.org/article/26e6c6db9cb540dd916163029680e524 kostenfrei https://www.mdpi.com/2077-0383/9/10/3333 kostenfrei https://doaj.org/toc/2077-0383 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2005 GBV_ILN_2009 GBV_ILN_2014 GBV_ILN_2055 GBV_ILN_2111 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 9 2020 10, p 3333 |
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Non-Coding RNAs and Hereditary Hemorrhagic Telangiectasia non-coding RNAs microRNAs long non-coding RNAs hereditary hemorrhagic telangiectasia biomarkers endothelial cells |
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misc non-coding RNAs misc microRNAs misc long non-coding RNAs misc hereditary hemorrhagic telangiectasia misc biomarkers misc endothelial cells misc Medicine misc R |
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misc non-coding RNAs misc microRNAs misc long non-coding RNAs misc hereditary hemorrhagic telangiectasia misc biomarkers misc endothelial cells misc Medicine misc R |
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Non-Coding RNAs and Hereditary Hemorrhagic Telangiectasia |
abstract |
Non-coding RNAs (ncRNAs) are functional ribonucleic acid (RNA) species that include microRNAs (miRs), a class of short non-coding RNAs (∼21–25 nucleotides), and long non-coding RNAs (lncRNAs) consisting of more than 200 nucleotides. They regulate gene expression post-transcriptionally and are involved in a wide range of pathophysiological processes. Hereditary hemorrhagic telangiectasia (HHT) is a rare disorder inherited in an autosomal dominant fashion characterized by vascular dysplasia. Patients can develop life-threatening vascular malformations and experience severe hemorrhaging. Effective pharmacological therapies are limited. The study of ncRNAs in HHT is an emerging field with great promise. This review will explore the current literature on the involvement of ncRNAs in HHT as diagnostic and pathogenic factors. |
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Non-coding RNAs (ncRNAs) are functional ribonucleic acid (RNA) species that include microRNAs (miRs), a class of short non-coding RNAs (∼21–25 nucleotides), and long non-coding RNAs (lncRNAs) consisting of more than 200 nucleotides. They regulate gene expression post-transcriptionally and are involved in a wide range of pathophysiological processes. Hereditary hemorrhagic telangiectasia (HHT) is a rare disorder inherited in an autosomal dominant fashion characterized by vascular dysplasia. Patients can develop life-threatening vascular malformations and experience severe hemorrhaging. Effective pharmacological therapies are limited. The study of ncRNAs in HHT is an emerging field with great promise. This review will explore the current literature on the involvement of ncRNAs in HHT as diagnostic and pathogenic factors. |
abstract_unstemmed |
Non-coding RNAs (ncRNAs) are functional ribonucleic acid (RNA) species that include microRNAs (miRs), a class of short non-coding RNAs (∼21–25 nucleotides), and long non-coding RNAs (lncRNAs) consisting of more than 200 nucleotides. They regulate gene expression post-transcriptionally and are involved in a wide range of pathophysiological processes. Hereditary hemorrhagic telangiectasia (HHT) is a rare disorder inherited in an autosomal dominant fashion characterized by vascular dysplasia. Patients can develop life-threatening vascular malformations and experience severe hemorrhaging. Effective pharmacological therapies are limited. The study of ncRNAs in HHT is an emerging field with great promise. This review will explore the current literature on the involvement of ncRNAs in HHT as diagnostic and pathogenic factors. |
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|
score |
7.399748 |