Otologic Problems in Turner Syndrome
Background and Aim: Turner syndrome is the most common sex chromosome abnormality in females, affecting an estimated 3% of all conceiving females. Otologic disease is a common problem in Turner syndrome patients that is due to a combination of small dysfunction Eustachian tube, palatal dysfunction a...
Ausführliche Beschreibung
Autor*in: |
Ahmadreza Okhovat [verfasserIn] Dr. Mahin Hashemipour [verfasserIn] Dr. Alireza Majlesi [verfasserIn] Mehdi Salek [verfasserIn] Masoumeh Raufi [verfasserIn] Dr. Saied Hanif Okhovat [verfasserIn] |
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2011 |
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In: Audiology - Tehran University of Medical Sciences, 2011, 19(2011), 1, Seite 57-62 |
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Übergeordnetes Werk: |
volume:19 ; year:2011 ; number:1 ; pages:57-62 |
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DOAJ024460273 |
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(DE-627)DOAJ024460273 (DE-599)DOAJ89baa3b2801745f1bf93ff0b36268f8f DE-627 ger DE-627 rakwb per Ahmadreza Okhovat verfasserin aut Otologic Problems in Turner Syndrome 2011 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Background and Aim: Turner syndrome is the most common sex chromosome abnormality in females, affecting an estimated 3% of all conceiving females. Otologic disease is a common problem in Turner syndrome patients that is due to a combination of small dysfunction Eustachian tube, palatal dysfunction and cochlear malformation.Methods: This study assessed the otologic and audiologic characteristics of a group of Turner syndrome patients. We studied 40 Turner patients aged 10 to 20 years (mean age: 15.84 years, SD=2.67). Pure tone audiometry was carried out for all of them.Results: Forty percent of the patients reported a history of middle ear disease. Analysis of audiometric data in 40 patients tested reveals normal hearing in 47.5%, pure sensorineural hearing loss in 32.5%, pure conductive hearing loss in 17.5% and mixed hearing loss in 2.5% of patients.Conclusion: Careful follow up during early childhood of children with Turner syndrome is necessary to detect middle ear disease and prevent the probable sequel. However, long term periodic follow up is mandatory even after resolution of middle ear disease to detect sensorineural hearing loss Turner Syndrome Sensorineural Hearing Loss Conductive Hearing Loss Mixed Hearing Loss Medicine R Dr. Mahin Hashemipour verfasserin aut Dr. Alireza Majlesi verfasserin aut Mehdi Salek verfasserin aut Masoumeh Raufi verfasserin aut Dr. Saied Hanif Okhovat verfasserin aut In Audiology Tehran University of Medical Sciences, 2011 19(2011), 1, Seite 57-62 (DE-627)545782643 (DE-600)2388035-1 20082657 nnns volume:19 year:2011 number:1 pages:57-62 https://doaj.org/article/89baa3b2801745f1bf93ff0b36268f8f kostenfrei http://journals.tums.ac.ir/upload_files/pdf/15443.pdf kostenfrei https://doaj.org/toc/1735-1936 Journal toc kostenfrei https://doaj.org/toc/2008-2657 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_31 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2005 GBV_ILN_2009 GBV_ILN_2011 GBV_ILN_2014 GBV_ILN_2055 GBV_ILN_2111 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 19 2011 1 57-62 |
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(DE-627)DOAJ024460273 (DE-599)DOAJ89baa3b2801745f1bf93ff0b36268f8f DE-627 ger DE-627 rakwb per Ahmadreza Okhovat verfasserin aut Otologic Problems in Turner Syndrome 2011 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Background and Aim: Turner syndrome is the most common sex chromosome abnormality in females, affecting an estimated 3% of all conceiving females. Otologic disease is a common problem in Turner syndrome patients that is due to a combination of small dysfunction Eustachian tube, palatal dysfunction and cochlear malformation.Methods: This study assessed the otologic and audiologic characteristics of a group of Turner syndrome patients. We studied 40 Turner patients aged 10 to 20 years (mean age: 15.84 years, SD=2.67). Pure tone audiometry was carried out for all of them.Results: Forty percent of the patients reported a history of middle ear disease. Analysis of audiometric data in 40 patients tested reveals normal hearing in 47.5%, pure sensorineural hearing loss in 32.5%, pure conductive hearing loss in 17.5% and mixed hearing loss in 2.5% of patients.Conclusion: Careful follow up during early childhood of children with Turner syndrome is necessary to detect middle ear disease and prevent the probable sequel. However, long term periodic follow up is mandatory even after resolution of middle ear disease to detect sensorineural hearing loss Turner Syndrome Sensorineural Hearing Loss Conductive Hearing Loss Mixed Hearing Loss Medicine R Dr. Mahin Hashemipour verfasserin aut Dr. Alireza Majlesi verfasserin aut Mehdi Salek verfasserin aut Masoumeh Raufi verfasserin aut Dr. Saied Hanif Okhovat verfasserin aut In Audiology Tehran University of Medical Sciences, 2011 19(2011), 1, Seite 57-62 (DE-627)545782643 (DE-600)2388035-1 20082657 nnns volume:19 year:2011 number:1 pages:57-62 https://doaj.org/article/89baa3b2801745f1bf93ff0b36268f8f kostenfrei http://journals.tums.ac.ir/upload_files/pdf/15443.pdf kostenfrei https://doaj.org/toc/1735-1936 Journal toc kostenfrei https://doaj.org/toc/2008-2657 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_31 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2005 GBV_ILN_2009 GBV_ILN_2011 GBV_ILN_2014 GBV_ILN_2055 GBV_ILN_2111 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 19 2011 1 57-62 |
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(DE-627)DOAJ024460273 (DE-599)DOAJ89baa3b2801745f1bf93ff0b36268f8f DE-627 ger DE-627 rakwb per Ahmadreza Okhovat verfasserin aut Otologic Problems in Turner Syndrome 2011 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Background and Aim: Turner syndrome is the most common sex chromosome abnormality in females, affecting an estimated 3% of all conceiving females. Otologic disease is a common problem in Turner syndrome patients that is due to a combination of small dysfunction Eustachian tube, palatal dysfunction and cochlear malformation.Methods: This study assessed the otologic and audiologic characteristics of a group of Turner syndrome patients. We studied 40 Turner patients aged 10 to 20 years (mean age: 15.84 years, SD=2.67). Pure tone audiometry was carried out for all of them.Results: Forty percent of the patients reported a history of middle ear disease. Analysis of audiometric data in 40 patients tested reveals normal hearing in 47.5%, pure sensorineural hearing loss in 32.5%, pure conductive hearing loss in 17.5% and mixed hearing loss in 2.5% of patients.Conclusion: Careful follow up during early childhood of children with Turner syndrome is necessary to detect middle ear disease and prevent the probable sequel. However, long term periodic follow up is mandatory even after resolution of middle ear disease to detect sensorineural hearing loss Turner Syndrome Sensorineural Hearing Loss Conductive Hearing Loss Mixed Hearing Loss Medicine R Dr. Mahin Hashemipour verfasserin aut Dr. Alireza Majlesi verfasserin aut Mehdi Salek verfasserin aut Masoumeh Raufi verfasserin aut Dr. Saied Hanif Okhovat verfasserin aut In Audiology Tehran University of Medical Sciences, 2011 19(2011), 1, Seite 57-62 (DE-627)545782643 (DE-600)2388035-1 20082657 nnns volume:19 year:2011 number:1 pages:57-62 https://doaj.org/article/89baa3b2801745f1bf93ff0b36268f8f kostenfrei http://journals.tums.ac.ir/upload_files/pdf/15443.pdf kostenfrei https://doaj.org/toc/1735-1936 Journal toc kostenfrei https://doaj.org/toc/2008-2657 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_31 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2005 GBV_ILN_2009 GBV_ILN_2011 GBV_ILN_2014 GBV_ILN_2055 GBV_ILN_2111 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 19 2011 1 57-62 |
allfieldsGer |
(DE-627)DOAJ024460273 (DE-599)DOAJ89baa3b2801745f1bf93ff0b36268f8f DE-627 ger DE-627 rakwb per Ahmadreza Okhovat verfasserin aut Otologic Problems in Turner Syndrome 2011 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Background and Aim: Turner syndrome is the most common sex chromosome abnormality in females, affecting an estimated 3% of all conceiving females. Otologic disease is a common problem in Turner syndrome patients that is due to a combination of small dysfunction Eustachian tube, palatal dysfunction and cochlear malformation.Methods: This study assessed the otologic and audiologic characteristics of a group of Turner syndrome patients. We studied 40 Turner patients aged 10 to 20 years (mean age: 15.84 years, SD=2.67). Pure tone audiometry was carried out for all of them.Results: Forty percent of the patients reported a history of middle ear disease. Analysis of audiometric data in 40 patients tested reveals normal hearing in 47.5%, pure sensorineural hearing loss in 32.5%, pure conductive hearing loss in 17.5% and mixed hearing loss in 2.5% of patients.Conclusion: Careful follow up during early childhood of children with Turner syndrome is necessary to detect middle ear disease and prevent the probable sequel. However, long term periodic follow up is mandatory even after resolution of middle ear disease to detect sensorineural hearing loss Turner Syndrome Sensorineural Hearing Loss Conductive Hearing Loss Mixed Hearing Loss Medicine R Dr. Mahin Hashemipour verfasserin aut Dr. Alireza Majlesi verfasserin aut Mehdi Salek verfasserin aut Masoumeh Raufi verfasserin aut Dr. Saied Hanif Okhovat verfasserin aut In Audiology Tehran University of Medical Sciences, 2011 19(2011), 1, Seite 57-62 (DE-627)545782643 (DE-600)2388035-1 20082657 nnns volume:19 year:2011 number:1 pages:57-62 https://doaj.org/article/89baa3b2801745f1bf93ff0b36268f8f kostenfrei http://journals.tums.ac.ir/upload_files/pdf/15443.pdf kostenfrei https://doaj.org/toc/1735-1936 Journal toc kostenfrei https://doaj.org/toc/2008-2657 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_31 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2005 GBV_ILN_2009 GBV_ILN_2011 GBV_ILN_2014 GBV_ILN_2055 GBV_ILN_2111 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 19 2011 1 57-62 |
allfieldsSound |
(DE-627)DOAJ024460273 (DE-599)DOAJ89baa3b2801745f1bf93ff0b36268f8f DE-627 ger DE-627 rakwb per Ahmadreza Okhovat verfasserin aut Otologic Problems in Turner Syndrome 2011 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Background and Aim: Turner syndrome is the most common sex chromosome abnormality in females, affecting an estimated 3% of all conceiving females. Otologic disease is a common problem in Turner syndrome patients that is due to a combination of small dysfunction Eustachian tube, palatal dysfunction and cochlear malformation.Methods: This study assessed the otologic and audiologic characteristics of a group of Turner syndrome patients. We studied 40 Turner patients aged 10 to 20 years (mean age: 15.84 years, SD=2.67). Pure tone audiometry was carried out for all of them.Results: Forty percent of the patients reported a history of middle ear disease. Analysis of audiometric data in 40 patients tested reveals normal hearing in 47.5%, pure sensorineural hearing loss in 32.5%, pure conductive hearing loss in 17.5% and mixed hearing loss in 2.5% of patients.Conclusion: Careful follow up during early childhood of children with Turner syndrome is necessary to detect middle ear disease and prevent the probable sequel. However, long term periodic follow up is mandatory even after resolution of middle ear disease to detect sensorineural hearing loss Turner Syndrome Sensorineural Hearing Loss Conductive Hearing Loss Mixed Hearing Loss Medicine R Dr. Mahin Hashemipour verfasserin aut Dr. Alireza Majlesi verfasserin aut Mehdi Salek verfasserin aut Masoumeh Raufi verfasserin aut Dr. Saied Hanif Okhovat verfasserin aut In Audiology Tehran University of Medical Sciences, 2011 19(2011), 1, Seite 57-62 (DE-627)545782643 (DE-600)2388035-1 20082657 nnns volume:19 year:2011 number:1 pages:57-62 https://doaj.org/article/89baa3b2801745f1bf93ff0b36268f8f kostenfrei http://journals.tums.ac.ir/upload_files/pdf/15443.pdf kostenfrei https://doaj.org/toc/1735-1936 Journal toc kostenfrei https://doaj.org/toc/2008-2657 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_31 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2005 GBV_ILN_2009 GBV_ILN_2011 GBV_ILN_2014 GBV_ILN_2055 GBV_ILN_2111 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 19 2011 1 57-62 |
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Ahmadreza Okhovat @@aut@@ Dr. Mahin Hashemipour @@aut@@ Dr. Alireza Majlesi @@aut@@ Mehdi Salek @@aut@@ Masoumeh Raufi @@aut@@ Dr. Saied Hanif Okhovat @@aut@@ |
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Background and Aim: Turner syndrome is the most common sex chromosome abnormality in females, affecting an estimated 3% of all conceiving females. Otologic disease is a common problem in Turner syndrome patients that is due to a combination of small dysfunction Eustachian tube, palatal dysfunction and cochlear malformation.Methods: This study assessed the otologic and audiologic characteristics of a group of Turner syndrome patients. We studied 40 Turner patients aged 10 to 20 years (mean age: 15.84 years, SD=2.67). Pure tone audiometry was carried out for all of them.Results: Forty percent of the patients reported a history of middle ear disease. Analysis of audiometric data in 40 patients tested reveals normal hearing in 47.5%, pure sensorineural hearing loss in 32.5%, pure conductive hearing loss in 17.5% and mixed hearing loss in 2.5% of patients.Conclusion: Careful follow up during early childhood of children with Turner syndrome is necessary to detect middle ear disease and prevent the probable sequel. However, long term periodic follow up is mandatory even after resolution of middle ear disease to detect sensorineural hearing loss |
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Background and Aim: Turner syndrome is the most common sex chromosome abnormality in females, affecting an estimated 3% of all conceiving females. Otologic disease is a common problem in Turner syndrome patients that is due to a combination of small dysfunction Eustachian tube, palatal dysfunction and cochlear malformation.Methods: This study assessed the otologic and audiologic characteristics of a group of Turner syndrome patients. We studied 40 Turner patients aged 10 to 20 years (mean age: 15.84 years, SD=2.67). Pure tone audiometry was carried out for all of them.Results: Forty percent of the patients reported a history of middle ear disease. Analysis of audiometric data in 40 patients tested reveals normal hearing in 47.5%, pure sensorineural hearing loss in 32.5%, pure conductive hearing loss in 17.5% and mixed hearing loss in 2.5% of patients.Conclusion: Careful follow up during early childhood of children with Turner syndrome is necessary to detect middle ear disease and prevent the probable sequel. However, long term periodic follow up is mandatory even after resolution of middle ear disease to detect sensorineural hearing loss |
abstract_unstemmed |
Background and Aim: Turner syndrome is the most common sex chromosome abnormality in females, affecting an estimated 3% of all conceiving females. Otologic disease is a common problem in Turner syndrome patients that is due to a combination of small dysfunction Eustachian tube, palatal dysfunction and cochlear malformation.Methods: This study assessed the otologic and audiologic characteristics of a group of Turner syndrome patients. We studied 40 Turner patients aged 10 to 20 years (mean age: 15.84 years, SD=2.67). Pure tone audiometry was carried out for all of them.Results: Forty percent of the patients reported a history of middle ear disease. Analysis of audiometric data in 40 patients tested reveals normal hearing in 47.5%, pure sensorineural hearing loss in 32.5%, pure conductive hearing loss in 17.5% and mixed hearing loss in 2.5% of patients.Conclusion: Careful follow up during early childhood of children with Turner syndrome is necessary to detect middle ear disease and prevent the probable sequel. However, long term periodic follow up is mandatory even after resolution of middle ear disease to detect sensorineural hearing loss |
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