The Epidemiology and Clinical Presentations of Atopic Diseases in Selective IgA Deficiency
Selective IgA deficiency (sIgAD) is the most common primary immunodeficiency disease (PID), with an estimated occurrence from about 1:3000 to even 1:150, depending on population. sIgAD is diagnosed in adults and children after the 4th year of age, with immunoglobulin A level below 0.07 g/L and norma...
Ausführliche Beschreibung
Autor*in: |
Izabela Morawska [verfasserIn] Sara Kurkowska [verfasserIn] Dominika Bębnowska [verfasserIn] Rafał Hrynkiewicz [verfasserIn] Rafał Becht [verfasserIn] Adam Michalski [verfasserIn] Hanna Piwowarska-Bilska [verfasserIn] Bożena Birkenfeld [verfasserIn] Katarzyna Załuska-Ogryzek [verfasserIn] Ewelina Grywalska [verfasserIn] Jacek Roliński [verfasserIn] Paulina Niedźwiedzka-Rystwej [verfasserIn] |
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E-Artikel |
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Sprache: |
Englisch |
Erschienen: |
2021 |
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Übergeordnetes Werk: |
In: Journal of Clinical Medicine - MDPI AG, 2013, 10(2021), 17, p 3809 |
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Übergeordnetes Werk: |
volume:10 ; year:2021 ; number:17, p 3809 |
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DOI / URN: |
10.3390/jcm10173809 |
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Katalog-ID: |
DOAJ059717092 |
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10.3390/jcm10173809 doi (DE-627)DOAJ059717092 (DE-599)DOAJc088177578c04f16931b6d04ac2380fe DE-627 ger DE-627 rakwb eng Izabela Morawska verfasserin aut The Epidemiology and Clinical Presentations of Atopic Diseases in Selective IgA Deficiency 2021 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Selective IgA deficiency (sIgAD) is the most common primary immunodeficiency disease (PID), with an estimated occurrence from about 1:3000 to even 1:150, depending on population. sIgAD is diagnosed in adults and children after the 4th year of age, with immunoglobulin A level below 0.07 g/L and normal levels of IgM and IgG. Usually, the disease remains undiagnosed throughout the patient’s life, due to its frequent asymptomatic course. If symptomatic, sIgAD is connected to more frequent viral and bacterial infections of upper respiratory, urinary, and gastrointestinal tracts, as well as autoimmune and allergic diseases. Interestingly, it may also be associated with other PIDs, such as IgG subclasses deficiency or specific antibodies deficiency. Rarely sIgAD can evolve to common variable immunodeficiency disease (CVID). It should also be remembered that IgA deficiency may occur in the course of other conditions or result from their treatment. It is hypothesized that allergic diseases (e.g., eczema, rhinitis, asthma) are more common in patients diagnosed with this particular PID. Selective IgA deficiency, although usually mildly symptomatic, can be difficult for clinicians. The aim of the study is to summarize the connection between selective IgA deficiency and atopic diseases. atopic diseases atopy allergy selective IgA deficiency primary immunodeficiency Medicine R Sara Kurkowska verfasserin aut Dominika Bębnowska verfasserin aut Rafał Hrynkiewicz verfasserin aut Rafał Becht verfasserin aut Adam Michalski verfasserin aut Hanna Piwowarska-Bilska verfasserin aut Bożena Birkenfeld verfasserin aut Katarzyna Załuska-Ogryzek verfasserin aut Ewelina Grywalska verfasserin aut Jacek Roliński verfasserin aut Paulina Niedźwiedzka-Rystwej verfasserin aut In Journal of Clinical Medicine MDPI AG, 2013 10(2021), 17, p 3809 (DE-627)718632478 (DE-600)2662592-1 20770383 nnns volume:10 year:2021 number:17, p 3809 https://doi.org/10.3390/jcm10173809 kostenfrei https://doaj.org/article/c088177578c04f16931b6d04ac2380fe kostenfrei https://www.mdpi.com/2077-0383/10/17/3809 kostenfrei https://doaj.org/toc/2077-0383 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2005 GBV_ILN_2009 GBV_ILN_2014 GBV_ILN_2055 GBV_ILN_2111 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 10 2021 17, p 3809 |
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10.3390/jcm10173809 doi (DE-627)DOAJ059717092 (DE-599)DOAJc088177578c04f16931b6d04ac2380fe DE-627 ger DE-627 rakwb eng Izabela Morawska verfasserin aut The Epidemiology and Clinical Presentations of Atopic Diseases in Selective IgA Deficiency 2021 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Selective IgA deficiency (sIgAD) is the most common primary immunodeficiency disease (PID), with an estimated occurrence from about 1:3000 to even 1:150, depending on population. sIgAD is diagnosed in adults and children after the 4th year of age, with immunoglobulin A level below 0.07 g/L and normal levels of IgM and IgG. Usually, the disease remains undiagnosed throughout the patient’s life, due to its frequent asymptomatic course. If symptomatic, sIgAD is connected to more frequent viral and bacterial infections of upper respiratory, urinary, and gastrointestinal tracts, as well as autoimmune and allergic diseases. Interestingly, it may also be associated with other PIDs, such as IgG subclasses deficiency or specific antibodies deficiency. Rarely sIgAD can evolve to common variable immunodeficiency disease (CVID). It should also be remembered that IgA deficiency may occur in the course of other conditions or result from their treatment. It is hypothesized that allergic diseases (e.g., eczema, rhinitis, asthma) are more common in patients diagnosed with this particular PID. Selective IgA deficiency, although usually mildly symptomatic, can be difficult for clinicians. The aim of the study is to summarize the connection between selective IgA deficiency and atopic diseases. atopic diseases atopy allergy selective IgA deficiency primary immunodeficiency Medicine R Sara Kurkowska verfasserin aut Dominika Bębnowska verfasserin aut Rafał Hrynkiewicz verfasserin aut Rafał Becht verfasserin aut Adam Michalski verfasserin aut Hanna Piwowarska-Bilska verfasserin aut Bożena Birkenfeld verfasserin aut Katarzyna Załuska-Ogryzek verfasserin aut Ewelina Grywalska verfasserin aut Jacek Roliński verfasserin aut Paulina Niedźwiedzka-Rystwej verfasserin aut In Journal of Clinical Medicine MDPI AG, 2013 10(2021), 17, p 3809 (DE-627)718632478 (DE-600)2662592-1 20770383 nnns volume:10 year:2021 number:17, p 3809 https://doi.org/10.3390/jcm10173809 kostenfrei https://doaj.org/article/c088177578c04f16931b6d04ac2380fe kostenfrei https://www.mdpi.com/2077-0383/10/17/3809 kostenfrei https://doaj.org/toc/2077-0383 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2005 GBV_ILN_2009 GBV_ILN_2014 GBV_ILN_2055 GBV_ILN_2111 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 10 2021 17, p 3809 |
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10.3390/jcm10173809 doi (DE-627)DOAJ059717092 (DE-599)DOAJc088177578c04f16931b6d04ac2380fe DE-627 ger DE-627 rakwb eng Izabela Morawska verfasserin aut The Epidemiology and Clinical Presentations of Atopic Diseases in Selective IgA Deficiency 2021 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Selective IgA deficiency (sIgAD) is the most common primary immunodeficiency disease (PID), with an estimated occurrence from about 1:3000 to even 1:150, depending on population. sIgAD is diagnosed in adults and children after the 4th year of age, with immunoglobulin A level below 0.07 g/L and normal levels of IgM and IgG. Usually, the disease remains undiagnosed throughout the patient’s life, due to its frequent asymptomatic course. If symptomatic, sIgAD is connected to more frequent viral and bacterial infections of upper respiratory, urinary, and gastrointestinal tracts, as well as autoimmune and allergic diseases. Interestingly, it may also be associated with other PIDs, such as IgG subclasses deficiency or specific antibodies deficiency. Rarely sIgAD can evolve to common variable immunodeficiency disease (CVID). It should also be remembered that IgA deficiency may occur in the course of other conditions or result from their treatment. It is hypothesized that allergic diseases (e.g., eczema, rhinitis, asthma) are more common in patients diagnosed with this particular PID. Selective IgA deficiency, although usually mildly symptomatic, can be difficult for clinicians. The aim of the study is to summarize the connection between selective IgA deficiency and atopic diseases. atopic diseases atopy allergy selective IgA deficiency primary immunodeficiency Medicine R Sara Kurkowska verfasserin aut Dominika Bębnowska verfasserin aut Rafał Hrynkiewicz verfasserin aut Rafał Becht verfasserin aut Adam Michalski verfasserin aut Hanna Piwowarska-Bilska verfasserin aut Bożena Birkenfeld verfasserin aut Katarzyna Załuska-Ogryzek verfasserin aut Ewelina Grywalska verfasserin aut Jacek Roliński verfasserin aut Paulina Niedźwiedzka-Rystwej verfasserin aut In Journal of Clinical Medicine MDPI AG, 2013 10(2021), 17, p 3809 (DE-627)718632478 (DE-600)2662592-1 20770383 nnns volume:10 year:2021 number:17, p 3809 https://doi.org/10.3390/jcm10173809 kostenfrei https://doaj.org/article/c088177578c04f16931b6d04ac2380fe kostenfrei https://www.mdpi.com/2077-0383/10/17/3809 kostenfrei https://doaj.org/toc/2077-0383 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2005 GBV_ILN_2009 GBV_ILN_2014 GBV_ILN_2055 GBV_ILN_2111 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 10 2021 17, p 3809 |
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10.3390/jcm10173809 doi (DE-627)DOAJ059717092 (DE-599)DOAJc088177578c04f16931b6d04ac2380fe DE-627 ger DE-627 rakwb eng Izabela Morawska verfasserin aut The Epidemiology and Clinical Presentations of Atopic Diseases in Selective IgA Deficiency 2021 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Selective IgA deficiency (sIgAD) is the most common primary immunodeficiency disease (PID), with an estimated occurrence from about 1:3000 to even 1:150, depending on population. sIgAD is diagnosed in adults and children after the 4th year of age, with immunoglobulin A level below 0.07 g/L and normal levels of IgM and IgG. Usually, the disease remains undiagnosed throughout the patient’s life, due to its frequent asymptomatic course. If symptomatic, sIgAD is connected to more frequent viral and bacterial infections of upper respiratory, urinary, and gastrointestinal tracts, as well as autoimmune and allergic diseases. Interestingly, it may also be associated with other PIDs, such as IgG subclasses deficiency or specific antibodies deficiency. Rarely sIgAD can evolve to common variable immunodeficiency disease (CVID). It should also be remembered that IgA deficiency may occur in the course of other conditions or result from their treatment. It is hypothesized that allergic diseases (e.g., eczema, rhinitis, asthma) are more common in patients diagnosed with this particular PID. Selective IgA deficiency, although usually mildly symptomatic, can be difficult for clinicians. The aim of the study is to summarize the connection between selective IgA deficiency and atopic diseases. atopic diseases atopy allergy selective IgA deficiency primary immunodeficiency Medicine R Sara Kurkowska verfasserin aut Dominika Bębnowska verfasserin aut Rafał Hrynkiewicz verfasserin aut Rafał Becht verfasserin aut Adam Michalski verfasserin aut Hanna Piwowarska-Bilska verfasserin aut Bożena Birkenfeld verfasserin aut Katarzyna Załuska-Ogryzek verfasserin aut Ewelina Grywalska verfasserin aut Jacek Roliński verfasserin aut Paulina Niedźwiedzka-Rystwej verfasserin aut In Journal of Clinical Medicine MDPI AG, 2013 10(2021), 17, p 3809 (DE-627)718632478 (DE-600)2662592-1 20770383 nnns volume:10 year:2021 number:17, p 3809 https://doi.org/10.3390/jcm10173809 kostenfrei https://doaj.org/article/c088177578c04f16931b6d04ac2380fe kostenfrei https://www.mdpi.com/2077-0383/10/17/3809 kostenfrei https://doaj.org/toc/2077-0383 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2005 GBV_ILN_2009 GBV_ILN_2014 GBV_ILN_2055 GBV_ILN_2111 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 10 2021 17, p 3809 |
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10.3390/jcm10173809 doi (DE-627)DOAJ059717092 (DE-599)DOAJc088177578c04f16931b6d04ac2380fe DE-627 ger DE-627 rakwb eng Izabela Morawska verfasserin aut The Epidemiology and Clinical Presentations of Atopic Diseases in Selective IgA Deficiency 2021 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Selective IgA deficiency (sIgAD) is the most common primary immunodeficiency disease (PID), with an estimated occurrence from about 1:3000 to even 1:150, depending on population. sIgAD is diagnosed in adults and children after the 4th year of age, with immunoglobulin A level below 0.07 g/L and normal levels of IgM and IgG. Usually, the disease remains undiagnosed throughout the patient’s life, due to its frequent asymptomatic course. If symptomatic, sIgAD is connected to more frequent viral and bacterial infections of upper respiratory, urinary, and gastrointestinal tracts, as well as autoimmune and allergic diseases. Interestingly, it may also be associated with other PIDs, such as IgG subclasses deficiency or specific antibodies deficiency. Rarely sIgAD can evolve to common variable immunodeficiency disease (CVID). It should also be remembered that IgA deficiency may occur in the course of other conditions or result from their treatment. It is hypothesized that allergic diseases (e.g., eczema, rhinitis, asthma) are more common in patients diagnosed with this particular PID. Selective IgA deficiency, although usually mildly symptomatic, can be difficult for clinicians. The aim of the study is to summarize the connection between selective IgA deficiency and atopic diseases. atopic diseases atopy allergy selective IgA deficiency primary immunodeficiency Medicine R Sara Kurkowska verfasserin aut Dominika Bębnowska verfasserin aut Rafał Hrynkiewicz verfasserin aut Rafał Becht verfasserin aut Adam Michalski verfasserin aut Hanna Piwowarska-Bilska verfasserin aut Bożena Birkenfeld verfasserin aut Katarzyna Załuska-Ogryzek verfasserin aut Ewelina Grywalska verfasserin aut Jacek Roliński verfasserin aut Paulina Niedźwiedzka-Rystwej verfasserin aut In Journal of Clinical Medicine MDPI AG, 2013 10(2021), 17, p 3809 (DE-627)718632478 (DE-600)2662592-1 20770383 nnns volume:10 year:2021 number:17, p 3809 https://doi.org/10.3390/jcm10173809 kostenfrei https://doaj.org/article/c088177578c04f16931b6d04ac2380fe kostenfrei https://www.mdpi.com/2077-0383/10/17/3809 kostenfrei https://doaj.org/toc/2077-0383 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2005 GBV_ILN_2009 GBV_ILN_2014 GBV_ILN_2055 GBV_ILN_2111 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 10 2021 17, p 3809 |
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The Epidemiology and Clinical Presentations of Atopic Diseases in Selective IgA Deficiency |
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Selective IgA deficiency (sIgAD) is the most common primary immunodeficiency disease (PID), with an estimated occurrence from about 1:3000 to even 1:150, depending on population. sIgAD is diagnosed in adults and children after the 4th year of age, with immunoglobulin A level below 0.07 g/L and normal levels of IgM and IgG. Usually, the disease remains undiagnosed throughout the patient’s life, due to its frequent asymptomatic course. If symptomatic, sIgAD is connected to more frequent viral and bacterial infections of upper respiratory, urinary, and gastrointestinal tracts, as well as autoimmune and allergic diseases. Interestingly, it may also be associated with other PIDs, such as IgG subclasses deficiency or specific antibodies deficiency. Rarely sIgAD can evolve to common variable immunodeficiency disease (CVID). It should also be remembered that IgA deficiency may occur in the course of other conditions or result from their treatment. It is hypothesized that allergic diseases (e.g., eczema, rhinitis, asthma) are more common in patients diagnosed with this particular PID. Selective IgA deficiency, although usually mildly symptomatic, can be difficult for clinicians. The aim of the study is to summarize the connection between selective IgA deficiency and atopic diseases. |
abstractGer |
Selective IgA deficiency (sIgAD) is the most common primary immunodeficiency disease (PID), with an estimated occurrence from about 1:3000 to even 1:150, depending on population. sIgAD is diagnosed in adults and children after the 4th year of age, with immunoglobulin A level below 0.07 g/L and normal levels of IgM and IgG. Usually, the disease remains undiagnosed throughout the patient’s life, due to its frequent asymptomatic course. If symptomatic, sIgAD is connected to more frequent viral and bacterial infections of upper respiratory, urinary, and gastrointestinal tracts, as well as autoimmune and allergic diseases. Interestingly, it may also be associated with other PIDs, such as IgG subclasses deficiency or specific antibodies deficiency. Rarely sIgAD can evolve to common variable immunodeficiency disease (CVID). It should also be remembered that IgA deficiency may occur in the course of other conditions or result from their treatment. It is hypothesized that allergic diseases (e.g., eczema, rhinitis, asthma) are more common in patients diagnosed with this particular PID. Selective IgA deficiency, although usually mildly symptomatic, can be difficult for clinicians. The aim of the study is to summarize the connection between selective IgA deficiency and atopic diseases. |
abstract_unstemmed |
Selective IgA deficiency (sIgAD) is the most common primary immunodeficiency disease (PID), with an estimated occurrence from about 1:3000 to even 1:150, depending on population. sIgAD is diagnosed in adults and children after the 4th year of age, with immunoglobulin A level below 0.07 g/L and normal levels of IgM and IgG. Usually, the disease remains undiagnosed throughout the patient’s life, due to its frequent asymptomatic course. If symptomatic, sIgAD is connected to more frequent viral and bacterial infections of upper respiratory, urinary, and gastrointestinal tracts, as well as autoimmune and allergic diseases. Interestingly, it may also be associated with other PIDs, such as IgG subclasses deficiency or specific antibodies deficiency. Rarely sIgAD can evolve to common variable immunodeficiency disease (CVID). It should also be remembered that IgA deficiency may occur in the course of other conditions or result from their treatment. It is hypothesized that allergic diseases (e.g., eczema, rhinitis, asthma) are more common in patients diagnosed with this particular PID. Selective IgA deficiency, although usually mildly symptomatic, can be difficult for clinicians. The aim of the study is to summarize the connection between selective IgA deficiency and atopic diseases. |
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<?xml version="1.0" encoding="UTF-8"?><collection xmlns="http://www.loc.gov/MARC21/slim"><record><leader>01000caa a22002652 4500</leader><controlfield tag="001">DOAJ059717092</controlfield><controlfield tag="003">DE-627</controlfield><controlfield tag="005">20240412161905.0</controlfield><controlfield tag="007">cr uuu---uuuuu</controlfield><controlfield tag="008">230228s2021 xx |||||o 00| ||eng c</controlfield><datafield tag="024" ind1="7" ind2=" "><subfield code="a">10.3390/jcm10173809</subfield><subfield code="2">doi</subfield></datafield><datafield tag="035" ind1=" " ind2=" "><subfield code="a">(DE-627)DOAJ059717092</subfield></datafield><datafield tag="035" ind1=" " ind2=" "><subfield code="a">(DE-599)DOAJc088177578c04f16931b6d04ac2380fe</subfield></datafield><datafield tag="040" ind1=" " ind2=" "><subfield code="a">DE-627</subfield><subfield code="b">ger</subfield><subfield code="c">DE-627</subfield><subfield code="e">rakwb</subfield></datafield><datafield tag="041" ind1=" " ind2=" "><subfield code="a">eng</subfield></datafield><datafield tag="100" ind1="0" ind2=" "><subfield code="a">Izabela Morawska</subfield><subfield code="e">verfasserin</subfield><subfield code="4">aut</subfield></datafield><datafield tag="245" ind1="1" ind2="4"><subfield code="a">The Epidemiology and Clinical Presentations of Atopic Diseases in Selective IgA Deficiency</subfield></datafield><datafield tag="264" ind1=" " ind2="1"><subfield code="c">2021</subfield></datafield><datafield tag="336" ind1=" " ind2=" "><subfield code="a">Text</subfield><subfield code="b">txt</subfield><subfield code="2">rdacontent</subfield></datafield><datafield tag="337" ind1=" " ind2=" "><subfield code="a">Computermedien</subfield><subfield code="b">c</subfield><subfield code="2">rdamedia</subfield></datafield><datafield tag="338" ind1=" " ind2=" "><subfield code="a">Online-Ressource</subfield><subfield code="b">cr</subfield><subfield code="2">rdacarrier</subfield></datafield><datafield tag="520" ind1=" " ind2=" "><subfield code="a">Selective IgA deficiency (sIgAD) is the most common primary immunodeficiency disease (PID), with an estimated occurrence from about 1:3000 to even 1:150, depending on population. sIgAD is diagnosed in adults and children after the 4th year of age, with immunoglobulin A level below 0.07 g/L and normal levels of IgM and IgG. 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