Early manifestations of cystic fibrosis in a premature patient with complex meconium ileus at birth

OBJECTIVE: To report a case of a preterm infant with complex meconium ileus at birth and cystic fibrosis. CASE DESCRIPTION: A male infant was born by vaginal delivery at 33 weeks and 5 days of gestational age with respiratory distress and severe abdominal distension. The exploratory laparotomy in th...
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Autor*in:	Ieda Regina Lopes Del Ciampo [verfasserIn] Tainara Queiroz Oliveira [verfasserIn] Luiz Antonio Del Ciampo [verfasserIn] Regina Sawamura [verfasserIn] Lidia Alice Gomes Monteiro Marin Torres [verfasserIn] Albin Eugenio Augustin [verfasserIn] Maria Inez Machado Fernandes [verfasserIn]

Format:	E-Artikel
Sprache:	Englisch ; Spanisch ; Portugiesisch

Erschienen:	2015

Schlagwörter:	Fibrose cística Íleo meconial Prematuridade

Übergeordnetes Werk:	In: Revista Paulista de Pediatria - Sociedade de Pediatria de São Paulo, 2008, 33(2015), 2, Seite 241-245
Übergeordnetes Werk:	volume:33 ; year:2015 ; number:2 ; pages:241-245

Links:	Link aufrufen Link aufrufen Link aufrufen Journal toc

DOI / URN:	10.1016/j.rpped.2014.12.004

Katalog-ID:	DOAJ06427151X

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allfields	10.1016/j.rpped.2014.12.004 doi (DE-627)DOAJ06427151X (DE-599)DOAJbf1fe8cf8bd64befa5b6fcb0653270b5 DE-627 ger DE-627 rakwb eng spa por RJ1-570 Ieda Regina Lopes Del Ciampo verfasserin aut Early manifestations of cystic fibrosis in a premature patient with complex meconium ileus at birth 2015 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier OBJECTIVE: To report a case of a preterm infant with complex meconium ileus at birth and cystic fibrosis. CASE DESCRIPTION: A male infant was born by vaginal delivery at 33 weeks and 5 days of gestational age with respiratory distress and severe abdominal distension. The exploratory laparotomy in the first day of life identified meconium ileus and secondary peritonitis. Ileal resection and ileostomy were performed, followed by reconstruction of the bowel transit at 20 days of life. At 11 days of life, the first immunoreactive trypsinogen (IRT) was 154 ng/mL (reference value = 70), and oral pancreatic enzymes replacement therapy was started. After 23 days, the second IRT was 172ng/mL (reference value = 70). At 35 days of age he was discharged with referrals to primary care and to a special clinic for CF for the determination of sweat chloride. He was received in the outpatient clinic for neonatal screening for CF at 65 days of life presenting malnutrition and respiratory distress. The sweat chloride test was performed, with a positive result (126mEq/L). COMMENTS: This case illustrates the rapid evolution of CF in a premature patient with complex meconium ileus as the first clinical manifestation. Fibrose cística Íleo meconial Prematuridade Pediatrics Tainara Queiroz Oliveira verfasserin aut Luiz Antonio Del Ciampo verfasserin aut Regina Sawamura verfasserin aut Lidia Alice Gomes Monteiro Marin Torres verfasserin aut Albin Eugenio Augustin verfasserin aut Maria Inez Machado Fernandes verfasserin aut In Revista Paulista de Pediatria Sociedade de Pediatria de São Paulo, 2008 33(2015), 2, Seite 241-245 (DE-627)630360057 (DE-600)2560228-7 19840462 nnns volume:33 year:2015 number:2 pages:241-245 https://doi.org/10.1016/j.rpped.2014.12.004 kostenfrei https://doaj.org/article/bf1fe8cf8bd64befa5b6fcb0653270b5 kostenfrei http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0103-05822015000200241&lng=en&tlng=en kostenfrei https://doaj.org/toc/1984-0462 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_31 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2005 GBV_ILN_2009 GBV_ILN_2014 GBV_ILN_2055 GBV_ILN_2111 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 33 2015 2 241-245
spelling	10.1016/j.rpped.2014.12.004 doi (DE-627)DOAJ06427151X (DE-599)DOAJbf1fe8cf8bd64befa5b6fcb0653270b5 DE-627 ger DE-627 rakwb eng spa por RJ1-570 Ieda Regina Lopes Del Ciampo verfasserin aut Early manifestations of cystic fibrosis in a premature patient with complex meconium ileus at birth 2015 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier OBJECTIVE: To report a case of a preterm infant with complex meconium ileus at birth and cystic fibrosis. CASE DESCRIPTION: A male infant was born by vaginal delivery at 33 weeks and 5 days of gestational age with respiratory distress and severe abdominal distension. The exploratory laparotomy in the first day of life identified meconium ileus and secondary peritonitis. Ileal resection and ileostomy were performed, followed by reconstruction of the bowel transit at 20 days of life. At 11 days of life, the first immunoreactive trypsinogen (IRT) was 154 ng/mL (reference value = 70), and oral pancreatic enzymes replacement therapy was started. After 23 days, the second IRT was 172ng/mL (reference value = 70). At 35 days of age he was discharged with referrals to primary care and to a special clinic for CF for the determination of sweat chloride. He was received in the outpatient clinic for neonatal screening for CF at 65 days of life presenting malnutrition and respiratory distress. The sweat chloride test was performed, with a positive result (126mEq/L). COMMENTS: This case illustrates the rapid evolution of CF in a premature patient with complex meconium ileus as the first clinical manifestation. Fibrose cística Íleo meconial Prematuridade Pediatrics Tainara Queiroz Oliveira verfasserin aut Luiz Antonio Del Ciampo verfasserin aut Regina Sawamura verfasserin aut Lidia Alice Gomes Monteiro Marin Torres verfasserin aut Albin Eugenio Augustin verfasserin aut Maria Inez Machado Fernandes verfasserin aut In Revista Paulista de Pediatria Sociedade de Pediatria de São Paulo, 2008 33(2015), 2, Seite 241-245 (DE-627)630360057 (DE-600)2560228-7 19840462 nnns volume:33 year:2015 number:2 pages:241-245 https://doi.org/10.1016/j.rpped.2014.12.004 kostenfrei https://doaj.org/article/bf1fe8cf8bd64befa5b6fcb0653270b5 kostenfrei http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0103-05822015000200241&lng=en&tlng=en kostenfrei https://doaj.org/toc/1984-0462 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_31 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2005 GBV_ILN_2009 GBV_ILN_2014 GBV_ILN_2055 GBV_ILN_2111 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 33 2015 2 241-245
allfields_unstemmed	10.1016/j.rpped.2014.12.004 doi (DE-627)DOAJ06427151X (DE-599)DOAJbf1fe8cf8bd64befa5b6fcb0653270b5 DE-627 ger DE-627 rakwb eng spa por RJ1-570 Ieda Regina Lopes Del Ciampo verfasserin aut Early manifestations of cystic fibrosis in a premature patient with complex meconium ileus at birth 2015 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier OBJECTIVE: To report a case of a preterm infant with complex meconium ileus at birth and cystic fibrosis. CASE DESCRIPTION: A male infant was born by vaginal delivery at 33 weeks and 5 days of gestational age with respiratory distress and severe abdominal distension. The exploratory laparotomy in the first day of life identified meconium ileus and secondary peritonitis. Ileal resection and ileostomy were performed, followed by reconstruction of the bowel transit at 20 days of life. At 11 days of life, the first immunoreactive trypsinogen (IRT) was 154 ng/mL (reference value = 70), and oral pancreatic enzymes replacement therapy was started. After 23 days, the second IRT was 172ng/mL (reference value = 70). At 35 days of age he was discharged with referrals to primary care and to a special clinic for CF for the determination of sweat chloride. He was received in the outpatient clinic for neonatal screening for CF at 65 days of life presenting malnutrition and respiratory distress. The sweat chloride test was performed, with a positive result (126mEq/L). COMMENTS: This case illustrates the rapid evolution of CF in a premature patient with complex meconium ileus as the first clinical manifestation. Fibrose cística Íleo meconial Prematuridade Pediatrics Tainara Queiroz Oliveira verfasserin aut Luiz Antonio Del Ciampo verfasserin aut Regina Sawamura verfasserin aut Lidia Alice Gomes Monteiro Marin Torres verfasserin aut Albin Eugenio Augustin verfasserin aut Maria Inez Machado Fernandes verfasserin aut In Revista Paulista de Pediatria Sociedade de Pediatria de São Paulo, 2008 33(2015), 2, Seite 241-245 (DE-627)630360057 (DE-600)2560228-7 19840462 nnns volume:33 year:2015 number:2 pages:241-245 https://doi.org/10.1016/j.rpped.2014.12.004 kostenfrei https://doaj.org/article/bf1fe8cf8bd64befa5b6fcb0653270b5 kostenfrei http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0103-05822015000200241&lng=en&tlng=en kostenfrei https://doaj.org/toc/1984-0462 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_31 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2005 GBV_ILN_2009 GBV_ILN_2014 GBV_ILN_2055 GBV_ILN_2111 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 33 2015 2 241-245
allfieldsGer	10.1016/j.rpped.2014.12.004 doi (DE-627)DOAJ06427151X (DE-599)DOAJbf1fe8cf8bd64befa5b6fcb0653270b5 DE-627 ger DE-627 rakwb eng spa por RJ1-570 Ieda Regina Lopes Del Ciampo verfasserin aut Early manifestations of cystic fibrosis in a premature patient with complex meconium ileus at birth 2015 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier OBJECTIVE: To report a case of a preterm infant with complex meconium ileus at birth and cystic fibrosis. CASE DESCRIPTION: A male infant was born by vaginal delivery at 33 weeks and 5 days of gestational age with respiratory distress and severe abdominal distension. The exploratory laparotomy in the first day of life identified meconium ileus and secondary peritonitis. Ileal resection and ileostomy were performed, followed by reconstruction of the bowel transit at 20 days of life. At 11 days of life, the first immunoreactive trypsinogen (IRT) was 154 ng/mL (reference value = 70), and oral pancreatic enzymes replacement therapy was started. After 23 days, the second IRT was 172ng/mL (reference value = 70). At 35 days of age he was discharged with referrals to primary care and to a special clinic for CF for the determination of sweat chloride. He was received in the outpatient clinic for neonatal screening for CF at 65 days of life presenting malnutrition and respiratory distress. The sweat chloride test was performed, with a positive result (126mEq/L). COMMENTS: This case illustrates the rapid evolution of CF in a premature patient with complex meconium ileus as the first clinical manifestation. Fibrose cística Íleo meconial Prematuridade Pediatrics Tainara Queiroz Oliveira verfasserin aut Luiz Antonio Del Ciampo verfasserin aut Regina Sawamura verfasserin aut Lidia Alice Gomes Monteiro Marin Torres verfasserin aut Albin Eugenio Augustin verfasserin aut Maria Inez Machado Fernandes verfasserin aut In Revista Paulista de Pediatria Sociedade de Pediatria de São Paulo, 2008 33(2015), 2, Seite 241-245 (DE-627)630360057 (DE-600)2560228-7 19840462 nnns volume:33 year:2015 number:2 pages:241-245 https://doi.org/10.1016/j.rpped.2014.12.004 kostenfrei https://doaj.org/article/bf1fe8cf8bd64befa5b6fcb0653270b5 kostenfrei http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0103-05822015000200241&lng=en&tlng=en kostenfrei https://doaj.org/toc/1984-0462 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_31 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2005 GBV_ILN_2009 GBV_ILN_2014 GBV_ILN_2055 GBV_ILN_2111 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 33 2015 2 241-245
allfieldsSound	10.1016/j.rpped.2014.12.004 doi (DE-627)DOAJ06427151X (DE-599)DOAJbf1fe8cf8bd64befa5b6fcb0653270b5 DE-627 ger DE-627 rakwb eng spa por RJ1-570 Ieda Regina Lopes Del Ciampo verfasserin aut Early manifestations of cystic fibrosis in a premature patient with complex meconium ileus at birth 2015 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier OBJECTIVE: To report a case of a preterm infant with complex meconium ileus at birth and cystic fibrosis. CASE DESCRIPTION: A male infant was born by vaginal delivery at 33 weeks and 5 days of gestational age with respiratory distress and severe abdominal distension. The exploratory laparotomy in the first day of life identified meconium ileus and secondary peritonitis. Ileal resection and ileostomy were performed, followed by reconstruction of the bowel transit at 20 days of life. At 11 days of life, the first immunoreactive trypsinogen (IRT) was 154 ng/mL (reference value = 70), and oral pancreatic enzymes replacement therapy was started. After 23 days, the second IRT was 172ng/mL (reference value = 70). At 35 days of age he was discharged with referrals to primary care and to a special clinic for CF for the determination of sweat chloride. He was received in the outpatient clinic for neonatal screening for CF at 65 days of life presenting malnutrition and respiratory distress. The sweat chloride test was performed, with a positive result (126mEq/L). COMMENTS: This case illustrates the rapid evolution of CF in a premature patient with complex meconium ileus as the first clinical manifestation. Fibrose cística Íleo meconial Prematuridade Pediatrics Tainara Queiroz Oliveira verfasserin aut Luiz Antonio Del Ciampo verfasserin aut Regina Sawamura verfasserin aut Lidia Alice Gomes Monteiro Marin Torres verfasserin aut Albin Eugenio Augustin verfasserin aut Maria Inez Machado Fernandes verfasserin aut In Revista Paulista de Pediatria Sociedade de Pediatria de São Paulo, 2008 33(2015), 2, Seite 241-245 (DE-627)630360057 (DE-600)2560228-7 19840462 nnns volume:33 year:2015 number:2 pages:241-245 https://doi.org/10.1016/j.rpped.2014.12.004 kostenfrei https://doaj.org/article/bf1fe8cf8bd64befa5b6fcb0653270b5 kostenfrei http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0103-05822015000200241&lng=en&tlng=en kostenfrei https://doaj.org/toc/1984-0462 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_31 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2005 GBV_ILN_2009 GBV_ILN_2014 GBV_ILN_2055 GBV_ILN_2111 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 33 2015 2 241-245
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callnumber-first	R - Medicine
author	Ieda Regina Lopes Del Ciampo
spellingShingle	Ieda Regina Lopes Del Ciampo misc RJ1-570 misc Fibrose cística misc Íleo meconial misc Prematuridade misc Pediatrics Early manifestations of cystic fibrosis in a premature patient with complex meconium ileus at birth
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topic_title	RJ1-570 Early manifestations of cystic fibrosis in a premature patient with complex meconium ileus at birth Fibrose cística Íleo meconial Prematuridade
topic	misc RJ1-570 misc Fibrose cística misc Íleo meconial misc Prematuridade misc Pediatrics
topic_unstemmed	misc RJ1-570 misc Fibrose cística misc Íleo meconial misc Prematuridade misc Pediatrics
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title	Early manifestations of cystic fibrosis in a premature patient with complex meconium ileus at birth
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title_full	Early manifestations of cystic fibrosis in a premature patient with complex meconium ileus at birth
author_sort	Ieda Regina Lopes Del Ciampo
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author_browse	Ieda Regina Lopes Del Ciampo Tainara Queiroz Oliveira Luiz Antonio Del Ciampo Regina Sawamura Lidia Alice Gomes Monteiro Marin Torres Albin Eugenio Augustin Maria Inez Machado Fernandes
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title_sort	early manifestations of cystic fibrosis in a premature patient with complex meconium ileus at birth
callnumber	RJ1-570
title_auth	Early manifestations of cystic fibrosis in a premature patient with complex meconium ileus at birth
abstract	OBJECTIVE: To report a case of a preterm infant with complex meconium ileus at birth and cystic fibrosis. CASE DESCRIPTION: A male infant was born by vaginal delivery at 33 weeks and 5 days of gestational age with respiratory distress and severe abdominal distension. The exploratory laparotomy in the first day of life identified meconium ileus and secondary peritonitis. Ileal resection and ileostomy were performed, followed by reconstruction of the bowel transit at 20 days of life. At 11 days of life, the first immunoreactive trypsinogen (IRT) was 154 ng/mL (reference value = 70), and oral pancreatic enzymes replacement therapy was started. After 23 days, the second IRT was 172ng/mL (reference value = 70). At 35 days of age he was discharged with referrals to primary care and to a special clinic for CF for the determination of sweat chloride. He was received in the outpatient clinic for neonatal screening for CF at 65 days of life presenting malnutrition and respiratory distress. The sweat chloride test was performed, with a positive result (126mEq/L). COMMENTS: This case illustrates the rapid evolution of CF in a premature patient with complex meconium ileus as the first clinical manifestation.
abstractGer	OBJECTIVE: To report a case of a preterm infant with complex meconium ileus at birth and cystic fibrosis. CASE DESCRIPTION: A male infant was born by vaginal delivery at 33 weeks and 5 days of gestational age with respiratory distress and severe abdominal distension. The exploratory laparotomy in the first day of life identified meconium ileus and secondary peritonitis. Ileal resection and ileostomy were performed, followed by reconstruction of the bowel transit at 20 days of life. At 11 days of life, the first immunoreactive trypsinogen (IRT) was 154 ng/mL (reference value = 70), and oral pancreatic enzymes replacement therapy was started. After 23 days, the second IRT was 172ng/mL (reference value = 70). At 35 days of age he was discharged with referrals to primary care and to a special clinic for CF for the determination of sweat chloride. He was received in the outpatient clinic for neonatal screening for CF at 65 days of life presenting malnutrition and respiratory distress. The sweat chloride test was performed, with a positive result (126mEq/L). COMMENTS: This case illustrates the rapid evolution of CF in a premature patient with complex meconium ileus as the first clinical manifestation.
abstract_unstemmed	OBJECTIVE: To report a case of a preterm infant with complex meconium ileus at birth and cystic fibrosis. CASE DESCRIPTION: A male infant was born by vaginal delivery at 33 weeks and 5 days of gestational age with respiratory distress and severe abdominal distension. The exploratory laparotomy in the first day of life identified meconium ileus and secondary peritonitis. Ileal resection and ileostomy were performed, followed by reconstruction of the bowel transit at 20 days of life. At 11 days of life, the first immunoreactive trypsinogen (IRT) was 154 ng/mL (reference value = 70), and oral pancreatic enzymes replacement therapy was started. After 23 days, the second IRT was 172ng/mL (reference value = 70). At 35 days of age he was discharged with referrals to primary care and to a special clinic for CF for the determination of sweat chloride. He was received in the outpatient clinic for neonatal screening for CF at 65 days of life presenting malnutrition and respiratory distress. The sweat chloride test was performed, with a positive result (126mEq/L). COMMENTS: This case illustrates the rapid evolution of CF in a premature patient with complex meconium ileus as the first clinical manifestation.
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title_short	Early manifestations of cystic fibrosis in a premature patient with complex meconium ileus at birth
url	https://doi.org/10.1016/j.rpped.2014.12.004 https://doaj.org/article/bf1fe8cf8bd64befa5b6fcb0653270b5 http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0103-05822015000200241&lng=en&tlng=en https://doaj.org/toc/1984-0462
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author2	Tainara Queiroz Oliveira Luiz Antonio Del Ciampo Regina Sawamura Lidia Alice Gomes Monteiro Marin Torres Albin Eugenio Augustin Maria Inez Machado Fernandes
author2Str	Tainara Queiroz Oliveira Luiz Antonio Del Ciampo Regina Sawamura Lidia Alice Gomes Monteiro Marin Torres Albin Eugenio Augustin Maria Inez Machado Fernandes
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up_date	2024-07-03T22:03:37.267Z
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Early manifestations of cystic fibrosis in a premature patient with complex meconium ileus at birth

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