Hemophagocytic lymphohistiocytosis/macrophage activation syndrome: a case series
Hemophagocytic lymphohistiocytosis (HLH) is a rare, life-threatening hematologic disorder occurring more commonly in children, but there are reported cases in adults as well. It is classified as a primary HLH or secondary HLH, which can occur due to autoimmune diseases, infections, and malignancies....
Ausführliche Beschreibung
Autor*in: |
Musa Azhar [verfasserIn] Syed Abdul Mannan Hamdani [verfasserIn] Shafquat Ali Khan [verfasserIn] Abdul Wahab [verfasserIn] Jhanzeb Iftikhar [verfasserIn] Usman Ahmad [verfasserIn] Bushra Ahsan [verfasserIn] |
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Format: |
E-Artikel |
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Sprache: |
Englisch ; Portugiesisch |
Erschienen: |
2022 |
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Schlagwörter: |
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Übergeordnetes Werk: |
In: International Journal of Medical Reviews and Case Reports - International Sci Ink Press Ltd, 2018, 6(2022), 16, Seite 8-13 |
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Übergeordnetes Werk: |
volume:6 ; year:2022 ; number:16 ; pages:8-13 |
Links: |
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DOAJ088220281 |
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(DE-627)DOAJ088220281 (DE-599)DOAJ04555633b2a64831b918c0327e81b102 DE-627 ger DE-627 rakwb eng por Musa Azhar verfasserin aut Hemophagocytic lymphohistiocytosis/macrophage activation syndrome: a case series 2022 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Hemophagocytic lymphohistiocytosis (HLH) is a rare, life-threatening hematologic disorder occurring more commonly in children, but there are reported cases in adults as well. It is classified as a primary HLH or secondary HLH, which can occur due to autoimmune diseases, infections, and malignancies. Secondary HLH is a challenge for physicians concerning diagnosis and management. In this case series, we report two patients of HLH diagnosed between August 2018 and August 2019 at Shaukat Khanum Memorial Cancer Hospital & Research Centre Lahore Pakistan, which were triggered by different underlying conditions like autoimmune diseases and malignancies or a combination of both. familial hlh (fhl) hemophagocytic lymphohistiocytosis (hlh) Medicine R Syed Abdul Mannan Hamdani verfasserin aut Shafquat Ali Khan verfasserin aut Abdul Wahab verfasserin aut Jhanzeb Iftikhar verfasserin aut Usman Ahmad verfasserin aut Bushra Ahsan verfasserin aut In International Journal of Medical Reviews and Case Reports International Sci Ink Press Ltd, 2018 6(2022), 16, Seite 8-13 (DE-627)1760646792 25349821 nnns volume:6 year:2022 number:16 pages:8-13 http://dx.doi.org/10.5455/IJMRCR.172-1617681669 kostenfrei https://doaj.org/article/04555633b2a64831b918c0327e81b102 kostenfrei https://mdpub.net/index.php?fulltxt=70732&fulltxtj=172&fulltxtp=172-1617681669.pdf kostenfrei https://doaj.org/toc/2534-9821 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ SSG-OLC-PHA AR 6 2022 16 8-13 |
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(DE-627)DOAJ088220281 (DE-599)DOAJ04555633b2a64831b918c0327e81b102 DE-627 ger DE-627 rakwb eng por Musa Azhar verfasserin aut Hemophagocytic lymphohistiocytosis/macrophage activation syndrome: a case series 2022 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Hemophagocytic lymphohistiocytosis (HLH) is a rare, life-threatening hematologic disorder occurring more commonly in children, but there are reported cases in adults as well. It is classified as a primary HLH or secondary HLH, which can occur due to autoimmune diseases, infections, and malignancies. Secondary HLH is a challenge for physicians concerning diagnosis and management. In this case series, we report two patients of HLH diagnosed between August 2018 and August 2019 at Shaukat Khanum Memorial Cancer Hospital & Research Centre Lahore Pakistan, which were triggered by different underlying conditions like autoimmune diseases and malignancies or a combination of both. familial hlh (fhl) hemophagocytic lymphohistiocytosis (hlh) Medicine R Syed Abdul Mannan Hamdani verfasserin aut Shafquat Ali Khan verfasserin aut Abdul Wahab verfasserin aut Jhanzeb Iftikhar verfasserin aut Usman Ahmad verfasserin aut Bushra Ahsan verfasserin aut In International Journal of Medical Reviews and Case Reports International Sci Ink Press Ltd, 2018 6(2022), 16, Seite 8-13 (DE-627)1760646792 25349821 nnns volume:6 year:2022 number:16 pages:8-13 http://dx.doi.org/10.5455/IJMRCR.172-1617681669 kostenfrei https://doaj.org/article/04555633b2a64831b918c0327e81b102 kostenfrei https://mdpub.net/index.php?fulltxt=70732&fulltxtj=172&fulltxtp=172-1617681669.pdf kostenfrei https://doaj.org/toc/2534-9821 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ SSG-OLC-PHA AR 6 2022 16 8-13 |
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(DE-627)DOAJ088220281 (DE-599)DOAJ04555633b2a64831b918c0327e81b102 DE-627 ger DE-627 rakwb eng por Musa Azhar verfasserin aut Hemophagocytic lymphohistiocytosis/macrophage activation syndrome: a case series 2022 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Hemophagocytic lymphohistiocytosis (HLH) is a rare, life-threatening hematologic disorder occurring more commonly in children, but there are reported cases in adults as well. It is classified as a primary HLH or secondary HLH, which can occur due to autoimmune diseases, infections, and malignancies. Secondary HLH is a challenge for physicians concerning diagnosis and management. In this case series, we report two patients of HLH diagnosed between August 2018 and August 2019 at Shaukat Khanum Memorial Cancer Hospital & Research Centre Lahore Pakistan, which were triggered by different underlying conditions like autoimmune diseases and malignancies or a combination of both. familial hlh (fhl) hemophagocytic lymphohistiocytosis (hlh) Medicine R Syed Abdul Mannan Hamdani verfasserin aut Shafquat Ali Khan verfasserin aut Abdul Wahab verfasserin aut Jhanzeb Iftikhar verfasserin aut Usman Ahmad verfasserin aut Bushra Ahsan verfasserin aut In International Journal of Medical Reviews and Case Reports International Sci Ink Press Ltd, 2018 6(2022), 16, Seite 8-13 (DE-627)1760646792 25349821 nnns volume:6 year:2022 number:16 pages:8-13 http://dx.doi.org/10.5455/IJMRCR.172-1617681669 kostenfrei https://doaj.org/article/04555633b2a64831b918c0327e81b102 kostenfrei https://mdpub.net/index.php?fulltxt=70732&fulltxtj=172&fulltxtp=172-1617681669.pdf kostenfrei https://doaj.org/toc/2534-9821 Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ SSG-OLC-PHA AR 6 2022 16 8-13 |
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Hemophagocytic lymphohistiocytosis (HLH) is a rare, life-threatening hematologic disorder occurring more commonly in children, but there are reported cases in adults as well. It is classified as a primary HLH or secondary HLH, which can occur due to autoimmune diseases, infections, and malignancies. Secondary HLH is a challenge for physicians concerning diagnosis and management. In this case series, we report two patients of HLH diagnosed between August 2018 and August 2019 at Shaukat Khanum Memorial Cancer Hospital & Research Centre Lahore Pakistan, which were triggered by different underlying conditions like autoimmune diseases and malignancies or a combination of both. |
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Hemophagocytic lymphohistiocytosis (HLH) is a rare, life-threatening hematologic disorder occurring more commonly in children, but there are reported cases in adults as well. It is classified as a primary HLH or secondary HLH, which can occur due to autoimmune diseases, infections, and malignancies. Secondary HLH is a challenge for physicians concerning diagnosis and management. In this case series, we report two patients of HLH diagnosed between August 2018 and August 2019 at Shaukat Khanum Memorial Cancer Hospital & Research Centre Lahore Pakistan, which were triggered by different underlying conditions like autoimmune diseases and malignancies or a combination of both. |
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Hemophagocytic lymphohistiocytosis (HLH) is a rare, life-threatening hematologic disorder occurring more commonly in children, but there are reported cases in adults as well. It is classified as a primary HLH or secondary HLH, which can occur due to autoimmune diseases, infections, and malignancies. Secondary HLH is a challenge for physicians concerning diagnosis and management. In this case series, we report two patients of HLH diagnosed between August 2018 and August 2019 at Shaukat Khanum Memorial Cancer Hospital & Research Centre Lahore Pakistan, which were triggered by different underlying conditions like autoimmune diseases and malignancies or a combination of both. |
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<?xml version="1.0" encoding="UTF-8"?><collection xmlns="http://www.loc.gov/MARC21/slim"><record><leader>01000caa a22002652 4500</leader><controlfield tag="001">DOAJ088220281</controlfield><controlfield tag="003">DE-627</controlfield><controlfield tag="005">20230503064833.0</controlfield><controlfield tag="007">cr uuu---uuuuu</controlfield><controlfield tag="008">230410s2022 xx |||||o 00| ||eng c</controlfield><datafield tag="035" ind1=" " ind2=" "><subfield code="a">(DE-627)DOAJ088220281</subfield></datafield><datafield tag="035" ind1=" " ind2=" "><subfield code="a">(DE-599)DOAJ04555633b2a64831b918c0327e81b102</subfield></datafield><datafield tag="040" ind1=" " ind2=" "><subfield code="a">DE-627</subfield><subfield code="b">ger</subfield><subfield code="c">DE-627</subfield><subfield code="e">rakwb</subfield></datafield><datafield tag="041" ind1=" " ind2=" "><subfield code="a">eng</subfield><subfield code="a">por</subfield></datafield><datafield tag="100" ind1="0" ind2=" "><subfield code="a">Musa Azhar</subfield><subfield code="e">verfasserin</subfield><subfield code="4">aut</subfield></datafield><datafield tag="245" ind1="1" ind2="0"><subfield code="a">Hemophagocytic lymphohistiocytosis/macrophage activation syndrome: a case series</subfield></datafield><datafield tag="264" ind1=" " ind2="1"><subfield code="c">2022</subfield></datafield><datafield tag="336" ind1=" " ind2=" "><subfield code="a">Text</subfield><subfield code="b">txt</subfield><subfield code="2">rdacontent</subfield></datafield><datafield tag="337" ind1=" " ind2=" "><subfield code="a">Computermedien</subfield><subfield code="b">c</subfield><subfield code="2">rdamedia</subfield></datafield><datafield tag="338" ind1=" " ind2=" "><subfield code="a">Online-Ressource</subfield><subfield code="b">cr</subfield><subfield code="2">rdacarrier</subfield></datafield><datafield tag="520" ind1=" " ind2=" "><subfield code="a">Hemophagocytic lymphohistiocytosis (HLH) is a rare, life-threatening hematologic disorder occurring more commonly in children, but there are reported cases in adults as well. It is classified as a primary HLH or secondary HLH, which can occur due to autoimmune diseases, infections, and malignancies. Secondary HLH is a challenge for physicians concerning diagnosis and management. 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