Bulbar Onset Amyotrophic Lateral Sclerosis: A Case Report
Amyotrophic lateral sclerosis is a rare, progressive, incurable neurodegenerative disorder that affects motor neurons leading to progressive muscle weakness, disability, and eventually death. A 45-year-old male, initially presented with hoarseness, flickering of tongue, and intermittent aspirations....
Ausführliche Beschreibung
Autor*in: |
Kabindra Rai [verfasserIn] Nilshan Rai [verfasserIn] Milan Kumar Chhantel Thapa [verfasserIn] Rajan Shrestha [verfasserIn] Sampurna Singh [verfasserIn] Monika Thapa [verfasserIn] |
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Format: |
E-Artikel |
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Sprache: |
Englisch |
Erschienen: |
2023 |
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Schlagwörter: |
amyotrophic lateral sclerosis; aspiration pneumonia; case reports; edaravone. |
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Übergeordnetes Werk: |
In: Journal of Nepal Medical Association - Nepal Medical Association, 2017, 61(2023), 259 |
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Übergeordnetes Werk: |
volume:61 ; year:2023 ; number:259 |
Links: |
Link aufrufen |
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DOI / URN: |
10.31729/jnma.8098 |
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Katalog-ID: |
DOAJ088294129 |
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10.31729/jnma.8098 doi (DE-627)DOAJ088294129 (DE-599)DOAJ93ee8b1ba3e241b08d1549a0066557ef DE-627 ger DE-627 rakwb eng R5-920 Kabindra Rai verfasserin aut Bulbar Onset Amyotrophic Lateral Sclerosis: A Case Report 2023 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Amyotrophic lateral sclerosis is a rare, progressive, incurable neurodegenerative disorder that affects motor neurons leading to progressive muscle weakness, disability, and eventually death. A 45-year-old male, initially presented with hoarseness, flickering of tongue, and intermittent aspirations. In course of three years, patient developed motor aphasia, frequent aspirations and an inability to hold his neck. Patient was diagnosed with a bulbar onset type of amyotrophic lateral sclerosis on the basis of neurodegenerative features with normal radiographic imaging. For the prevention of recurrent aspiration pneumonia, he was managed with a percutaneous endoscopic gastrostomy tube. As he started developing respiratory failure tracheostomy was performed and kept on a continuous bi-level positive airway pressure ventilator, in the meantime, two courses of injection Edaravone were given. Early evaluation, diagnosis and management of the condition is a cornerstone for better prognosis of disease and survival. amyotrophic lateral sclerosis; aspiration pneumonia; case reports; edaravone. Medicine (General) Nilshan Rai verfasserin aut Milan Kumar Chhantel Thapa verfasserin aut Rajan Shrestha verfasserin aut Sampurna Singh verfasserin aut Monika Thapa verfasserin aut In Journal of Nepal Medical Association Nepal Medical Association, 2017 61(2023), 259 (DE-627)502926767 (DE-600)2209910-4 1815672X nnns volume:61 year:2023 number:259 https://doi.org/10.31729/jnma.8098 kostenfrei https://doaj.org/article/93ee8b1ba3e241b08d1549a0066557ef kostenfrei https://www.jnma.com.np/jnma/index.php/jnma/article/view/8098 kostenfrei https://doaj.org/toc/0028-2715 Journal toc kostenfrei https://doaj.org/toc/1815-672X Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2014 GBV_ILN_2153 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 61 2023 259 |
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10.31729/jnma.8098 doi (DE-627)DOAJ088294129 (DE-599)DOAJ93ee8b1ba3e241b08d1549a0066557ef DE-627 ger DE-627 rakwb eng R5-920 Kabindra Rai verfasserin aut Bulbar Onset Amyotrophic Lateral Sclerosis: A Case Report 2023 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Amyotrophic lateral sclerosis is a rare, progressive, incurable neurodegenerative disorder that affects motor neurons leading to progressive muscle weakness, disability, and eventually death. A 45-year-old male, initially presented with hoarseness, flickering of tongue, and intermittent aspirations. In course of three years, patient developed motor aphasia, frequent aspirations and an inability to hold his neck. Patient was diagnosed with a bulbar onset type of amyotrophic lateral sclerosis on the basis of neurodegenerative features with normal radiographic imaging. For the prevention of recurrent aspiration pneumonia, he was managed with a percutaneous endoscopic gastrostomy tube. As he started developing respiratory failure tracheostomy was performed and kept on a continuous bi-level positive airway pressure ventilator, in the meantime, two courses of injection Edaravone were given. Early evaluation, diagnosis and management of the condition is a cornerstone for better prognosis of disease and survival. amyotrophic lateral sclerosis; aspiration pneumonia; case reports; edaravone. Medicine (General) Nilshan Rai verfasserin aut Milan Kumar Chhantel Thapa verfasserin aut Rajan Shrestha verfasserin aut Sampurna Singh verfasserin aut Monika Thapa verfasserin aut In Journal of Nepal Medical Association Nepal Medical Association, 2017 61(2023), 259 (DE-627)502926767 (DE-600)2209910-4 1815672X nnns volume:61 year:2023 number:259 https://doi.org/10.31729/jnma.8098 kostenfrei https://doaj.org/article/93ee8b1ba3e241b08d1549a0066557ef kostenfrei https://www.jnma.com.np/jnma/index.php/jnma/article/view/8098 kostenfrei https://doaj.org/toc/0028-2715 Journal toc kostenfrei https://doaj.org/toc/1815-672X Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2014 GBV_ILN_2153 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 61 2023 259 |
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10.31729/jnma.8098 doi (DE-627)DOAJ088294129 (DE-599)DOAJ93ee8b1ba3e241b08d1549a0066557ef DE-627 ger DE-627 rakwb eng R5-920 Kabindra Rai verfasserin aut Bulbar Onset Amyotrophic Lateral Sclerosis: A Case Report 2023 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Amyotrophic lateral sclerosis is a rare, progressive, incurable neurodegenerative disorder that affects motor neurons leading to progressive muscle weakness, disability, and eventually death. A 45-year-old male, initially presented with hoarseness, flickering of tongue, and intermittent aspirations. In course of three years, patient developed motor aphasia, frequent aspirations and an inability to hold his neck. Patient was diagnosed with a bulbar onset type of amyotrophic lateral sclerosis on the basis of neurodegenerative features with normal radiographic imaging. For the prevention of recurrent aspiration pneumonia, he was managed with a percutaneous endoscopic gastrostomy tube. As he started developing respiratory failure tracheostomy was performed and kept on a continuous bi-level positive airway pressure ventilator, in the meantime, two courses of injection Edaravone were given. Early evaluation, diagnosis and management of the condition is a cornerstone for better prognosis of disease and survival. amyotrophic lateral sclerosis; aspiration pneumonia; case reports; edaravone. Medicine (General) Nilshan Rai verfasserin aut Milan Kumar Chhantel Thapa verfasserin aut Rajan Shrestha verfasserin aut Sampurna Singh verfasserin aut Monika Thapa verfasserin aut In Journal of Nepal Medical Association Nepal Medical Association, 2017 61(2023), 259 (DE-627)502926767 (DE-600)2209910-4 1815672X nnns volume:61 year:2023 number:259 https://doi.org/10.31729/jnma.8098 kostenfrei https://doaj.org/article/93ee8b1ba3e241b08d1549a0066557ef kostenfrei https://www.jnma.com.np/jnma/index.php/jnma/article/view/8098 kostenfrei https://doaj.org/toc/0028-2715 Journal toc kostenfrei https://doaj.org/toc/1815-672X Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2014 GBV_ILN_2153 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 61 2023 259 |
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10.31729/jnma.8098 doi (DE-627)DOAJ088294129 (DE-599)DOAJ93ee8b1ba3e241b08d1549a0066557ef DE-627 ger DE-627 rakwb eng R5-920 Kabindra Rai verfasserin aut Bulbar Onset Amyotrophic Lateral Sclerosis: A Case Report 2023 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier Amyotrophic lateral sclerosis is a rare, progressive, incurable neurodegenerative disorder that affects motor neurons leading to progressive muscle weakness, disability, and eventually death. A 45-year-old male, initially presented with hoarseness, flickering of tongue, and intermittent aspirations. In course of three years, patient developed motor aphasia, frequent aspirations and an inability to hold his neck. Patient was diagnosed with a bulbar onset type of amyotrophic lateral sclerosis on the basis of neurodegenerative features with normal radiographic imaging. For the prevention of recurrent aspiration pneumonia, he was managed with a percutaneous endoscopic gastrostomy tube. As he started developing respiratory failure tracheostomy was performed and kept on a continuous bi-level positive airway pressure ventilator, in the meantime, two courses of injection Edaravone were given. Early evaluation, diagnosis and management of the condition is a cornerstone for better prognosis of disease and survival. amyotrophic lateral sclerosis; aspiration pneumonia; case reports; edaravone. Medicine (General) Nilshan Rai verfasserin aut Milan Kumar Chhantel Thapa verfasserin aut Rajan Shrestha verfasserin aut Sampurna Singh verfasserin aut Monika Thapa verfasserin aut In Journal of Nepal Medical Association Nepal Medical Association, 2017 61(2023), 259 (DE-627)502926767 (DE-600)2209910-4 1815672X nnns volume:61 year:2023 number:259 https://doi.org/10.31729/jnma.8098 kostenfrei https://doaj.org/article/93ee8b1ba3e241b08d1549a0066557ef kostenfrei https://www.jnma.com.np/jnma/index.php/jnma/article/view/8098 kostenfrei https://doaj.org/toc/0028-2715 Journal toc kostenfrei https://doaj.org/toc/1815-672X Journal toc kostenfrei GBV_USEFLAG_A SYSFLAG_A GBV_DOAJ GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2014 GBV_ILN_2153 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 61 2023 259 |
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Amyotrophic lateral sclerosis is a rare, progressive, incurable neurodegenerative disorder that affects motor neurons leading to progressive muscle weakness, disability, and eventually death. A 45-year-old male, initially presented with hoarseness, flickering of tongue, and intermittent aspirations. In course of three years, patient developed motor aphasia, frequent aspirations and an inability to hold his neck. Patient was diagnosed with a bulbar onset type of amyotrophic lateral sclerosis on the basis of neurodegenerative features with normal radiographic imaging. For the prevention of recurrent aspiration pneumonia, he was managed with a percutaneous endoscopic gastrostomy tube. As he started developing respiratory failure tracheostomy was performed and kept on a continuous bi-level positive airway pressure ventilator, in the meantime, two courses of injection Edaravone were given. Early evaluation, diagnosis and management of the condition is a cornerstone for better prognosis of disease and survival. |
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Amyotrophic lateral sclerosis is a rare, progressive, incurable neurodegenerative disorder that affects motor neurons leading to progressive muscle weakness, disability, and eventually death. A 45-year-old male, initially presented with hoarseness, flickering of tongue, and intermittent aspirations. In course of three years, patient developed motor aphasia, frequent aspirations and an inability to hold his neck. Patient was diagnosed with a bulbar onset type of amyotrophic lateral sclerosis on the basis of neurodegenerative features with normal radiographic imaging. For the prevention of recurrent aspiration pneumonia, he was managed with a percutaneous endoscopic gastrostomy tube. As he started developing respiratory failure tracheostomy was performed and kept on a continuous bi-level positive airway pressure ventilator, in the meantime, two courses of injection Edaravone were given. Early evaluation, diagnosis and management of the condition is a cornerstone for better prognosis of disease and survival. |
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Amyotrophic lateral sclerosis is a rare, progressive, incurable neurodegenerative disorder that affects motor neurons leading to progressive muscle weakness, disability, and eventually death. A 45-year-old male, initially presented with hoarseness, flickering of tongue, and intermittent aspirations. In course of three years, patient developed motor aphasia, frequent aspirations and an inability to hold his neck. Patient was diagnosed with a bulbar onset type of amyotrophic lateral sclerosis on the basis of neurodegenerative features with normal radiographic imaging. For the prevention of recurrent aspiration pneumonia, he was managed with a percutaneous endoscopic gastrostomy tube. As he started developing respiratory failure tracheostomy was performed and kept on a continuous bi-level positive airway pressure ventilator, in the meantime, two courses of injection Edaravone were given. Early evaluation, diagnosis and management of the condition is a cornerstone for better prognosis of disease and survival. |
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|
score |
7.399806 |