Phenotype, genotype, treatment, and survival outcomes in patients with X-linked inhibitor of apoptosis deficiency
X-linked inhibitor of apoptosis (XIAP) deficiency is a rare primary immunodeficiency disease caused by XIAP gene mutations. A broad range of phenotype, severity, and age at onset present challenges for patient management.
Autor*in: |
Yang, Linlin [verfasserIn] |
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E-Artikel |
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Sprache: |
Englisch |
Erschienen: |
2022 |
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Schlagwörter: |
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Umfang: |
11 |
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Übergeordnetes Werk: |
Enthalten in: Antidiabetic treatment in elderly patients with low performance status admitted to internal medicine ward - Papakitsou, I. ELSEVIER, 2022, official publication of the American Academy of Allergy, Asthma and Immunology, Amsterdam [u.a.] |
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Übergeordnetes Werk: |
volume:150 ; year:2022 ; number:2 ; pages:456-466 ; extent:11 |
Links: |
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DOI / URN: |
10.1016/j.jaci.2021.10.037 |
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Katalog-ID: |
ELV058520775 |
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10.1016/j.jaci.2021.10.037 doi /cbs_pica/cbs_olc/import_discovery/elsevier/einzuspielen/GBV00000000001856.pica (DE-627)ELV058520775 (ELSEVIER)S0091-6749(21)02597-5 DE-627 ger DE-627 rakwb eng 610 VZ 44.85 bkl Yang, Linlin verfasserin aut Phenotype, genotype, treatment, and survival outcomes in patients with X-linked inhibitor of apoptosis deficiency 2022 11 nicht spezifiziert zzz rdacontent nicht spezifiziert z rdamedia nicht spezifiziert zu rdacarrier X-linked inhibitor of apoptosis (XIAP) deficiency is a rare primary immunodeficiency disease caused by XIAP gene mutations. A broad range of phenotype, severity, and age at onset present challenges for patient management. phenotype Elsevier conservative treatment Elsevier HLH Elsevier therapy Elsevier primary immunodeficiency Elsevier IBD Elsevier adult Elsevier survival outcomes Elsevier HSCT Elsevier X-linked inhibitor of apoptosis Elsevier XIAP deficiency Elsevier Booth, Claire oth Speckmann, Carsten oth Seidel, Markus G. oth Worth, Austen J.J. oth Kindle, Gerhard oth Lankester, Arjan C. oth Grimbacher, Bodo oth Sediva, Anna oth Neven, Benedicte oth Hauck, Fabian oth Warnatz, Klaus oth Pac, Malgorzata oth Carrabba, Maria oth Palacin, Pere oth Jandus, Peter oth Gardulf, Ann oth Mahlaoui, Nizar oth Pergent, Martine oth Schutz, Catharina oth Sharapova, Svetlana oth Vassilios, Lougaris oth Candotti, Fabio oth Volpi, Stephano oth Enthalten in Elsevier Papakitsou, I. ELSEVIER Antidiabetic treatment in elderly patients with low performance status admitted to internal medicine ward 2022 official publication of the American Academy of Allergy, Asthma and Immunology Amsterdam [u.a.] (DE-627)ELV000021164 volume:150 year:2022 number:2 pages:456-466 extent:11 https://doi.org/10.1016/j.jaci.2021.10.037 Volltext GBV_USEFLAG_U GBV_ELV SYSFLAG_U SSG-OLC-PHA 44.85 Kardiologie Angiologie VZ AR 150 2022 2 456-466 11 |
spelling |
10.1016/j.jaci.2021.10.037 doi /cbs_pica/cbs_olc/import_discovery/elsevier/einzuspielen/GBV00000000001856.pica (DE-627)ELV058520775 (ELSEVIER)S0091-6749(21)02597-5 DE-627 ger DE-627 rakwb eng 610 VZ 44.85 bkl Yang, Linlin verfasserin aut Phenotype, genotype, treatment, and survival outcomes in patients with X-linked inhibitor of apoptosis deficiency 2022 11 nicht spezifiziert zzz rdacontent nicht spezifiziert z rdamedia nicht spezifiziert zu rdacarrier X-linked inhibitor of apoptosis (XIAP) deficiency is a rare primary immunodeficiency disease caused by XIAP gene mutations. A broad range of phenotype, severity, and age at onset present challenges for patient management. phenotype Elsevier conservative treatment Elsevier HLH Elsevier therapy Elsevier primary immunodeficiency Elsevier IBD Elsevier adult Elsevier survival outcomes Elsevier HSCT Elsevier X-linked inhibitor of apoptosis Elsevier XIAP deficiency Elsevier Booth, Claire oth Speckmann, Carsten oth Seidel, Markus G. oth Worth, Austen J.J. oth Kindle, Gerhard oth Lankester, Arjan C. oth Grimbacher, Bodo oth Sediva, Anna oth Neven, Benedicte oth Hauck, Fabian oth Warnatz, Klaus oth Pac, Malgorzata oth Carrabba, Maria oth Palacin, Pere oth Jandus, Peter oth Gardulf, Ann oth Mahlaoui, Nizar oth Pergent, Martine oth Schutz, Catharina oth Sharapova, Svetlana oth Vassilios, Lougaris oth Candotti, Fabio oth Volpi, Stephano oth Enthalten in Elsevier Papakitsou, I. ELSEVIER Antidiabetic treatment in elderly patients with low performance status admitted to internal medicine ward 2022 official publication of the American Academy of Allergy, Asthma and Immunology Amsterdam [u.a.] (DE-627)ELV000021164 volume:150 year:2022 number:2 pages:456-466 extent:11 https://doi.org/10.1016/j.jaci.2021.10.037 Volltext GBV_USEFLAG_U GBV_ELV SYSFLAG_U SSG-OLC-PHA 44.85 Kardiologie Angiologie VZ AR 150 2022 2 456-466 11 |
allfields_unstemmed |
10.1016/j.jaci.2021.10.037 doi /cbs_pica/cbs_olc/import_discovery/elsevier/einzuspielen/GBV00000000001856.pica (DE-627)ELV058520775 (ELSEVIER)S0091-6749(21)02597-5 DE-627 ger DE-627 rakwb eng 610 VZ 44.85 bkl Yang, Linlin verfasserin aut Phenotype, genotype, treatment, and survival outcomes in patients with X-linked inhibitor of apoptosis deficiency 2022 11 nicht spezifiziert zzz rdacontent nicht spezifiziert z rdamedia nicht spezifiziert zu rdacarrier X-linked inhibitor of apoptosis (XIAP) deficiency is a rare primary immunodeficiency disease caused by XIAP gene mutations. A broad range of phenotype, severity, and age at onset present challenges for patient management. phenotype Elsevier conservative treatment Elsevier HLH Elsevier therapy Elsevier primary immunodeficiency Elsevier IBD Elsevier adult Elsevier survival outcomes Elsevier HSCT Elsevier X-linked inhibitor of apoptosis Elsevier XIAP deficiency Elsevier Booth, Claire oth Speckmann, Carsten oth Seidel, Markus G. oth Worth, Austen J.J. oth Kindle, Gerhard oth Lankester, Arjan C. oth Grimbacher, Bodo oth Sediva, Anna oth Neven, Benedicte oth Hauck, Fabian oth Warnatz, Klaus oth Pac, Malgorzata oth Carrabba, Maria oth Palacin, Pere oth Jandus, Peter oth Gardulf, Ann oth Mahlaoui, Nizar oth Pergent, Martine oth Schutz, Catharina oth Sharapova, Svetlana oth Vassilios, Lougaris oth Candotti, Fabio oth Volpi, Stephano oth Enthalten in Elsevier Papakitsou, I. ELSEVIER Antidiabetic treatment in elderly patients with low performance status admitted to internal medicine ward 2022 official publication of the American Academy of Allergy, Asthma and Immunology Amsterdam [u.a.] (DE-627)ELV000021164 volume:150 year:2022 number:2 pages:456-466 extent:11 https://doi.org/10.1016/j.jaci.2021.10.037 Volltext GBV_USEFLAG_U GBV_ELV SYSFLAG_U SSG-OLC-PHA 44.85 Kardiologie Angiologie VZ AR 150 2022 2 456-466 11 |
allfieldsGer |
10.1016/j.jaci.2021.10.037 doi /cbs_pica/cbs_olc/import_discovery/elsevier/einzuspielen/GBV00000000001856.pica (DE-627)ELV058520775 (ELSEVIER)S0091-6749(21)02597-5 DE-627 ger DE-627 rakwb eng 610 VZ 44.85 bkl Yang, Linlin verfasserin aut Phenotype, genotype, treatment, and survival outcomes in patients with X-linked inhibitor of apoptosis deficiency 2022 11 nicht spezifiziert zzz rdacontent nicht spezifiziert z rdamedia nicht spezifiziert zu rdacarrier X-linked inhibitor of apoptosis (XIAP) deficiency is a rare primary immunodeficiency disease caused by XIAP gene mutations. A broad range of phenotype, severity, and age at onset present challenges for patient management. phenotype Elsevier conservative treatment Elsevier HLH Elsevier therapy Elsevier primary immunodeficiency Elsevier IBD Elsevier adult Elsevier survival outcomes Elsevier HSCT Elsevier X-linked inhibitor of apoptosis Elsevier XIAP deficiency Elsevier Booth, Claire oth Speckmann, Carsten oth Seidel, Markus G. oth Worth, Austen J.J. oth Kindle, Gerhard oth Lankester, Arjan C. oth Grimbacher, Bodo oth Sediva, Anna oth Neven, Benedicte oth Hauck, Fabian oth Warnatz, Klaus oth Pac, Malgorzata oth Carrabba, Maria oth Palacin, Pere oth Jandus, Peter oth Gardulf, Ann oth Mahlaoui, Nizar oth Pergent, Martine oth Schutz, Catharina oth Sharapova, Svetlana oth Vassilios, Lougaris oth Candotti, Fabio oth Volpi, Stephano oth Enthalten in Elsevier Papakitsou, I. ELSEVIER Antidiabetic treatment in elderly patients with low performance status admitted to internal medicine ward 2022 official publication of the American Academy of Allergy, Asthma and Immunology Amsterdam [u.a.] (DE-627)ELV000021164 volume:150 year:2022 number:2 pages:456-466 extent:11 https://doi.org/10.1016/j.jaci.2021.10.037 Volltext GBV_USEFLAG_U GBV_ELV SYSFLAG_U SSG-OLC-PHA 44.85 Kardiologie Angiologie VZ AR 150 2022 2 456-466 11 |
allfieldsSound |
10.1016/j.jaci.2021.10.037 doi /cbs_pica/cbs_olc/import_discovery/elsevier/einzuspielen/GBV00000000001856.pica (DE-627)ELV058520775 (ELSEVIER)S0091-6749(21)02597-5 DE-627 ger DE-627 rakwb eng 610 VZ 44.85 bkl Yang, Linlin verfasserin aut Phenotype, genotype, treatment, and survival outcomes in patients with X-linked inhibitor of apoptosis deficiency 2022 11 nicht spezifiziert zzz rdacontent nicht spezifiziert z rdamedia nicht spezifiziert zu rdacarrier X-linked inhibitor of apoptosis (XIAP) deficiency is a rare primary immunodeficiency disease caused by XIAP gene mutations. A broad range of phenotype, severity, and age at onset present challenges for patient management. phenotype Elsevier conservative treatment Elsevier HLH Elsevier therapy Elsevier primary immunodeficiency Elsevier IBD Elsevier adult Elsevier survival outcomes Elsevier HSCT Elsevier X-linked inhibitor of apoptosis Elsevier XIAP deficiency Elsevier Booth, Claire oth Speckmann, Carsten oth Seidel, Markus G. oth Worth, Austen J.J. oth Kindle, Gerhard oth Lankester, Arjan C. oth Grimbacher, Bodo oth Sediva, Anna oth Neven, Benedicte oth Hauck, Fabian oth Warnatz, Klaus oth Pac, Malgorzata oth Carrabba, Maria oth Palacin, Pere oth Jandus, Peter oth Gardulf, Ann oth Mahlaoui, Nizar oth Pergent, Martine oth Schutz, Catharina oth Sharapova, Svetlana oth Vassilios, Lougaris oth Candotti, Fabio oth Volpi, Stephano oth Enthalten in Elsevier Papakitsou, I. ELSEVIER Antidiabetic treatment in elderly patients with low performance status admitted to internal medicine ward 2022 official publication of the American Academy of Allergy, Asthma and Immunology Amsterdam [u.a.] (DE-627)ELV000021164 volume:150 year:2022 number:2 pages:456-466 extent:11 https://doi.org/10.1016/j.jaci.2021.10.037 Volltext GBV_USEFLAG_U GBV_ELV SYSFLAG_U SSG-OLC-PHA 44.85 Kardiologie Angiologie VZ AR 150 2022 2 456-466 11 |
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Antidiabetic treatment in elderly patients with low performance status admitted to internal medicine ward |
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Yang, Linlin @@aut@@ Booth, Claire @@oth@@ Speckmann, Carsten @@oth@@ Seidel, Markus G. @@oth@@ Worth, Austen J.J. @@oth@@ Kindle, Gerhard @@oth@@ Lankester, Arjan C. @@oth@@ Grimbacher, Bodo @@oth@@ Sediva, Anna @@oth@@ Neven, Benedicte @@oth@@ Hauck, Fabian @@oth@@ Warnatz, Klaus @@oth@@ Pac, Malgorzata @@oth@@ Carrabba, Maria @@oth@@ Palacin, Pere @@oth@@ Jandus, Peter @@oth@@ Gardulf, Ann @@oth@@ Mahlaoui, Nizar @@oth@@ Pergent, Martine @@oth@@ Schutz, Catharina @@oth@@ Sharapova, Svetlana @@oth@@ Vassilios, Lougaris @@oth@@ Candotti, Fabio @@oth@@ Volpi, Stephano @@oth@@ |
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Phenotype, genotype, treatment, and survival outcomes in patients with X-linked inhibitor of apoptosis deficiency |
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X-linked inhibitor of apoptosis (XIAP) deficiency is a rare primary immunodeficiency disease caused by XIAP gene mutations. A broad range of phenotype, severity, and age at onset present challenges for patient management. |
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X-linked inhibitor of apoptosis (XIAP) deficiency is a rare primary immunodeficiency disease caused by XIAP gene mutations. A broad range of phenotype, severity, and age at onset present challenges for patient management. |
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X-linked inhibitor of apoptosis (XIAP) deficiency is a rare primary immunodeficiency disease caused by XIAP gene mutations. A broad range of phenotype, severity, and age at onset present challenges for patient management. |
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