Biliary atresia and its mimics
Biliary atresia (BA) is an idiopathic, progressive, fibroinflammatory, and obliterative disease of the biliary tract that manifests in the neonatal period with scleral icterus, acholic stools, conjugated hyperbilirubinemia, and elevated serum-gamma glutamyl transferase. Definitive diagnosis is estab...
Ausführliche Beschreibung
Gespeichert in:
| Autor*in: |
Patel, Kalyani R. [verfasserIn] |
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| Format: |
E-Artikel |
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| Sprache: |
Englisch |
| Erschienen: |
2023transfer abstract |
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| Umfang: |
15 |
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| Übergeordnetes Werk: |
Enthalten in: Levonorgestrel intra-uterine system as a treatment option for complex endometrial hyperplasia - Haoula, Zeina J. ELSEVIER, 2011, the continuously updated review of diagnostic histopathology, Amsterdam [u.a.] |
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| Übergeordnetes Werk: |
volume:29 ; year:2023 ; number:1 ; pages:52-66 ; extent:15 |
| Links: |
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| DOI / URN: |
10.1016/j.mpdhp.2022.11.001 |
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| 520 | |a Biliary atresia (BA) is an idiopathic, progressive, fibroinflammatory, and obliterative disease of the biliary tract that manifests in the neonatal period with scleral icterus, acholic stools, conjugated hyperbilirubinemia, and elevated serum-gamma glutamyl transferase. Definitive diagnosis is established by a multi-disciplinary team comprising of pediatricians, hepatologists, radiologists, surgeons, and pathologists. It is currently the most common cause of pediatric liver transplantation in the USA and worldwide. More than 100 diseases can present with neonatal cholestasis mimicking BA. Early diagnosis (<60 days of age) with a timely Kasai portoenterostomy (KP) is crucial to relieve biliary obstruction and achieve longer native liver survival. Histopathologic features of BA can differ based on age and specific surgical interventions. This review describes histopathologic features of BA at various stages and focuses on a variety of common and uncommon diseases mimicking BA. With the increasing use of molecular testing and comprehensive genetic cholestasis panels, several patients who would have otherwise been diagnosed as BA, are now classified with specific genetic conditions leading to cholestasis. | ||
| 520 | |a Biliary atresia (BA) is an idiopathic, progressive, fibroinflammatory, and obliterative disease of the biliary tract that manifests in the neonatal period with scleral icterus, acholic stools, conjugated hyperbilirubinemia, and elevated serum-gamma glutamyl transferase. Definitive diagnosis is established by a multi-disciplinary team comprising of pediatricians, hepatologists, radiologists, surgeons, and pathologists. It is currently the most common cause of pediatric liver transplantation in the USA and worldwide. More than 100 diseases can present with neonatal cholestasis mimicking BA. Early diagnosis (<60 days of age) with a timely Kasai portoenterostomy (KP) is crucial to relieve biliary obstruction and achieve longer native liver survival. Histopathologic features of BA can differ based on age and specific surgical interventions. This review describes histopathologic features of BA at various stages and focuses on a variety of common and uncommon diseases mimicking BA. With the increasing use of molecular testing and comprehensive genetic cholestasis panels, several patients who would have otherwise been diagnosed as BA, are now classified with specific genetic conditions leading to cholestasis. | ||
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10.1016/j.mpdhp.2022.11.001 doi /cbs_pica/cbs_olc/import_discovery/elsevier/einzuspielen/GBV00000000001997.pica (DE-627)ELV059879564 (ELSEVIER)S1756-2317(22)00163-3 DE-627 ger DE-627 rakwb eng 610 VZ 44.92 bkl Patel, Kalyani R. verfasserin aut Biliary atresia and its mimics 2023transfer abstract 15 nicht spezifiziert zzz rdacontent nicht spezifiziert z rdamedia nicht spezifiziert zu rdacarrier Biliary atresia (BA) is an idiopathic, progressive, fibroinflammatory, and obliterative disease of the biliary tract that manifests in the neonatal period with scleral icterus, acholic stools, conjugated hyperbilirubinemia, and elevated serum-gamma glutamyl transferase. Definitive diagnosis is established by a multi-disciplinary team comprising of pediatricians, hepatologists, radiologists, surgeons, and pathologists. It is currently the most common cause of pediatric liver transplantation in the USA and worldwide. More than 100 diseases can present with neonatal cholestasis mimicking BA. Early diagnosis (<60 days of age) with a timely Kasai portoenterostomy (KP) is crucial to relieve biliary obstruction and achieve longer native liver survival. Histopathologic features of BA can differ based on age and specific surgical interventions. This review describes histopathologic features of BA at various stages and focuses on a variety of common and uncommon diseases mimicking BA. With the increasing use of molecular testing and comprehensive genetic cholestasis panels, several patients who would have otherwise been diagnosed as BA, are now classified with specific genetic conditions leading to cholestasis. Biliary atresia (BA) is an idiopathic, progressive, fibroinflammatory, and obliterative disease of the biliary tract that manifests in the neonatal period with scleral icterus, acholic stools, conjugated hyperbilirubinemia, and elevated serum-gamma glutamyl transferase. Definitive diagnosis is established by a multi-disciplinary team comprising of pediatricians, hepatologists, radiologists, surgeons, and pathologists. It is currently the most common cause of pediatric liver transplantation in the USA and worldwide. More than 100 diseases can present with neonatal cholestasis mimicking BA. Early diagnosis (<60 days of age) with a timely Kasai portoenterostomy (KP) is crucial to relieve biliary obstruction and achieve longer native liver survival. Histopathologic features of BA can differ based on age and specific surgical interventions. This review describes histopathologic features of BA at various stages and focuses on a variety of common and uncommon diseases mimicking BA. With the increasing use of molecular testing and comprehensive genetic cholestasis panels, several patients who would have otherwise been diagnosed as BA, are now classified with specific genetic conditions leading to cholestasis. atresia Elsevier hypoplasia Elsevier venopathy Elsevier biliary Elsevier extrahepatic Elsevier obliterative Elsevier non-cholestatic Elsevier Enthalten in Elsevier Haoula, Zeina J. ELSEVIER Levonorgestrel intra-uterine system as a treatment option for complex endometrial hyperplasia 2011 the continuously updated review of diagnostic histopathology Amsterdam [u.a.] (DE-627)ELV007989881 volume:29 year:2023 number:1 pages:52-66 extent:15 https://doi.org/10.1016/j.mpdhp.2022.11.001 Volltext GBV_USEFLAG_U GBV_ELV SYSFLAG_U SSG-OLC-PHA 44.92 Gynäkologie VZ AR 29 2023 1 52-66 15 |
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10.1016/j.mpdhp.2022.11.001 doi /cbs_pica/cbs_olc/import_discovery/elsevier/einzuspielen/GBV00000000001997.pica (DE-627)ELV059879564 (ELSEVIER)S1756-2317(22)00163-3 DE-627 ger DE-627 rakwb eng 610 VZ 44.92 bkl Patel, Kalyani R. verfasserin aut Biliary atresia and its mimics 2023transfer abstract 15 nicht spezifiziert zzz rdacontent nicht spezifiziert z rdamedia nicht spezifiziert zu rdacarrier Biliary atresia (BA) is an idiopathic, progressive, fibroinflammatory, and obliterative disease of the biliary tract that manifests in the neonatal period with scleral icterus, acholic stools, conjugated hyperbilirubinemia, and elevated serum-gamma glutamyl transferase. Definitive diagnosis is established by a multi-disciplinary team comprising of pediatricians, hepatologists, radiologists, surgeons, and pathologists. It is currently the most common cause of pediatric liver transplantation in the USA and worldwide. More than 100 diseases can present with neonatal cholestasis mimicking BA. Early diagnosis (<60 days of age) with a timely Kasai portoenterostomy (KP) is crucial to relieve biliary obstruction and achieve longer native liver survival. Histopathologic features of BA can differ based on age and specific surgical interventions. This review describes histopathologic features of BA at various stages and focuses on a variety of common and uncommon diseases mimicking BA. With the increasing use of molecular testing and comprehensive genetic cholestasis panels, several patients who would have otherwise been diagnosed as BA, are now classified with specific genetic conditions leading to cholestasis. Biliary atresia (BA) is an idiopathic, progressive, fibroinflammatory, and obliterative disease of the biliary tract that manifests in the neonatal period with scleral icterus, acholic stools, conjugated hyperbilirubinemia, and elevated serum-gamma glutamyl transferase. Definitive diagnosis is established by a multi-disciplinary team comprising of pediatricians, hepatologists, radiologists, surgeons, and pathologists. It is currently the most common cause of pediatric liver transplantation in the USA and worldwide. More than 100 diseases can present with neonatal cholestasis mimicking BA. Early diagnosis (<60 days of age) with a timely Kasai portoenterostomy (KP) is crucial to relieve biliary obstruction and achieve longer native liver survival. Histopathologic features of BA can differ based on age and specific surgical interventions. This review describes histopathologic features of BA at various stages and focuses on a variety of common and uncommon diseases mimicking BA. With the increasing use of molecular testing and comprehensive genetic cholestasis panels, several patients who would have otherwise been diagnosed as BA, are now classified with specific genetic conditions leading to cholestasis. atresia Elsevier hypoplasia Elsevier venopathy Elsevier biliary Elsevier extrahepatic Elsevier obliterative Elsevier non-cholestatic Elsevier Enthalten in Elsevier Haoula, Zeina J. ELSEVIER Levonorgestrel intra-uterine system as a treatment option for complex endometrial hyperplasia 2011 the continuously updated review of diagnostic histopathology Amsterdam [u.a.] (DE-627)ELV007989881 volume:29 year:2023 number:1 pages:52-66 extent:15 https://doi.org/10.1016/j.mpdhp.2022.11.001 Volltext GBV_USEFLAG_U GBV_ELV SYSFLAG_U SSG-OLC-PHA 44.92 Gynäkologie VZ AR 29 2023 1 52-66 15 |
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10.1016/j.mpdhp.2022.11.001 doi /cbs_pica/cbs_olc/import_discovery/elsevier/einzuspielen/GBV00000000001997.pica (DE-627)ELV059879564 (ELSEVIER)S1756-2317(22)00163-3 DE-627 ger DE-627 rakwb eng 610 VZ 44.92 bkl Patel, Kalyani R. verfasserin aut Biliary atresia and its mimics 2023transfer abstract 15 nicht spezifiziert zzz rdacontent nicht spezifiziert z rdamedia nicht spezifiziert zu rdacarrier Biliary atresia (BA) is an idiopathic, progressive, fibroinflammatory, and obliterative disease of the biliary tract that manifests in the neonatal period with scleral icterus, acholic stools, conjugated hyperbilirubinemia, and elevated serum-gamma glutamyl transferase. Definitive diagnosis is established by a multi-disciplinary team comprising of pediatricians, hepatologists, radiologists, surgeons, and pathologists. It is currently the most common cause of pediatric liver transplantation in the USA and worldwide. More than 100 diseases can present with neonatal cholestasis mimicking BA. Early diagnosis (<60 days of age) with a timely Kasai portoenterostomy (KP) is crucial to relieve biliary obstruction and achieve longer native liver survival. Histopathologic features of BA can differ based on age and specific surgical interventions. This review describes histopathologic features of BA at various stages and focuses on a variety of common and uncommon diseases mimicking BA. With the increasing use of molecular testing and comprehensive genetic cholestasis panels, several patients who would have otherwise been diagnosed as BA, are now classified with specific genetic conditions leading to cholestasis. Biliary atresia (BA) is an idiopathic, progressive, fibroinflammatory, and obliterative disease of the biliary tract that manifests in the neonatal period with scleral icterus, acholic stools, conjugated hyperbilirubinemia, and elevated serum-gamma glutamyl transferase. Definitive diagnosis is established by a multi-disciplinary team comprising of pediatricians, hepatologists, radiologists, surgeons, and pathologists. It is currently the most common cause of pediatric liver transplantation in the USA and worldwide. More than 100 diseases can present with neonatal cholestasis mimicking BA. Early diagnosis (<60 days of age) with a timely Kasai portoenterostomy (KP) is crucial to relieve biliary obstruction and achieve longer native liver survival. Histopathologic features of BA can differ based on age and specific surgical interventions. This review describes histopathologic features of BA at various stages and focuses on a variety of common and uncommon diseases mimicking BA. With the increasing use of molecular testing and comprehensive genetic cholestasis panels, several patients who would have otherwise been diagnosed as BA, are now classified with specific genetic conditions leading to cholestasis. atresia Elsevier hypoplasia Elsevier venopathy Elsevier biliary Elsevier extrahepatic Elsevier obliterative Elsevier non-cholestatic Elsevier Enthalten in Elsevier Haoula, Zeina J. ELSEVIER Levonorgestrel intra-uterine system as a treatment option for complex endometrial hyperplasia 2011 the continuously updated review of diagnostic histopathology Amsterdam [u.a.] (DE-627)ELV007989881 volume:29 year:2023 number:1 pages:52-66 extent:15 https://doi.org/10.1016/j.mpdhp.2022.11.001 Volltext GBV_USEFLAG_U GBV_ELV SYSFLAG_U SSG-OLC-PHA 44.92 Gynäkologie VZ AR 29 2023 1 52-66 15 |
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10.1016/j.mpdhp.2022.11.001 doi /cbs_pica/cbs_olc/import_discovery/elsevier/einzuspielen/GBV00000000001997.pica (DE-627)ELV059879564 (ELSEVIER)S1756-2317(22)00163-3 DE-627 ger DE-627 rakwb eng 610 VZ 44.92 bkl Patel, Kalyani R. verfasserin aut Biliary atresia and its mimics 2023transfer abstract 15 nicht spezifiziert zzz rdacontent nicht spezifiziert z rdamedia nicht spezifiziert zu rdacarrier Biliary atresia (BA) is an idiopathic, progressive, fibroinflammatory, and obliterative disease of the biliary tract that manifests in the neonatal period with scleral icterus, acholic stools, conjugated hyperbilirubinemia, and elevated serum-gamma glutamyl transferase. Definitive diagnosis is established by a multi-disciplinary team comprising of pediatricians, hepatologists, radiologists, surgeons, and pathologists. It is currently the most common cause of pediatric liver transplantation in the USA and worldwide. More than 100 diseases can present with neonatal cholestasis mimicking BA. Early diagnosis (<60 days of age) with a timely Kasai portoenterostomy (KP) is crucial to relieve biliary obstruction and achieve longer native liver survival. Histopathologic features of BA can differ based on age and specific surgical interventions. This review describes histopathologic features of BA at various stages and focuses on a variety of common and uncommon diseases mimicking BA. With the increasing use of molecular testing and comprehensive genetic cholestasis panels, several patients who would have otherwise been diagnosed as BA, are now classified with specific genetic conditions leading to cholestasis. Biliary atresia (BA) is an idiopathic, progressive, fibroinflammatory, and obliterative disease of the biliary tract that manifests in the neonatal period with scleral icterus, acholic stools, conjugated hyperbilirubinemia, and elevated serum-gamma glutamyl transferase. Definitive diagnosis is established by a multi-disciplinary team comprising of pediatricians, hepatologists, radiologists, surgeons, and pathologists. It is currently the most common cause of pediatric liver transplantation in the USA and worldwide. More than 100 diseases can present with neonatal cholestasis mimicking BA. Early diagnosis (<60 days of age) with a timely Kasai portoenterostomy (KP) is crucial to relieve biliary obstruction and achieve longer native liver survival. Histopathologic features of BA can differ based on age and specific surgical interventions. This review describes histopathologic features of BA at various stages and focuses on a variety of common and uncommon diseases mimicking BA. With the increasing use of molecular testing and comprehensive genetic cholestasis panels, several patients who would have otherwise been diagnosed as BA, are now classified with specific genetic conditions leading to cholestasis. atresia Elsevier hypoplasia Elsevier venopathy Elsevier biliary Elsevier extrahepatic Elsevier obliterative Elsevier non-cholestatic Elsevier Enthalten in Elsevier Haoula, Zeina J. ELSEVIER Levonorgestrel intra-uterine system as a treatment option for complex endometrial hyperplasia 2011 the continuously updated review of diagnostic histopathology Amsterdam [u.a.] (DE-627)ELV007989881 volume:29 year:2023 number:1 pages:52-66 extent:15 https://doi.org/10.1016/j.mpdhp.2022.11.001 Volltext GBV_USEFLAG_U GBV_ELV SYSFLAG_U SSG-OLC-PHA 44.92 Gynäkologie VZ AR 29 2023 1 52-66 15 |
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10.1016/j.mpdhp.2022.11.001 doi /cbs_pica/cbs_olc/import_discovery/elsevier/einzuspielen/GBV00000000001997.pica (DE-627)ELV059879564 (ELSEVIER)S1756-2317(22)00163-3 DE-627 ger DE-627 rakwb eng 610 VZ 44.92 bkl Patel, Kalyani R. verfasserin aut Biliary atresia and its mimics 2023transfer abstract 15 nicht spezifiziert zzz rdacontent nicht spezifiziert z rdamedia nicht spezifiziert zu rdacarrier Biliary atresia (BA) is an idiopathic, progressive, fibroinflammatory, and obliterative disease of the biliary tract that manifests in the neonatal period with scleral icterus, acholic stools, conjugated hyperbilirubinemia, and elevated serum-gamma glutamyl transferase. Definitive diagnosis is established by a multi-disciplinary team comprising of pediatricians, hepatologists, radiologists, surgeons, and pathologists. It is currently the most common cause of pediatric liver transplantation in the USA and worldwide. More than 100 diseases can present with neonatal cholestasis mimicking BA. Early diagnosis (<60 days of age) with a timely Kasai portoenterostomy (KP) is crucial to relieve biliary obstruction and achieve longer native liver survival. Histopathologic features of BA can differ based on age and specific surgical interventions. This review describes histopathologic features of BA at various stages and focuses on a variety of common and uncommon diseases mimicking BA. With the increasing use of molecular testing and comprehensive genetic cholestasis panels, several patients who would have otherwise been diagnosed as BA, are now classified with specific genetic conditions leading to cholestasis. Biliary atresia (BA) is an idiopathic, progressive, fibroinflammatory, and obliterative disease of the biliary tract that manifests in the neonatal period with scleral icterus, acholic stools, conjugated hyperbilirubinemia, and elevated serum-gamma glutamyl transferase. Definitive diagnosis is established by a multi-disciplinary team comprising of pediatricians, hepatologists, radiologists, surgeons, and pathologists. It is currently the most common cause of pediatric liver transplantation in the USA and worldwide. More than 100 diseases can present with neonatal cholestasis mimicking BA. Early diagnosis (<60 days of age) with a timely Kasai portoenterostomy (KP) is crucial to relieve biliary obstruction and achieve longer native liver survival. Histopathologic features of BA can differ based on age and specific surgical interventions. This review describes histopathologic features of BA at various stages and focuses on a variety of common and uncommon diseases mimicking BA. With the increasing use of molecular testing and comprehensive genetic cholestasis panels, several patients who would have otherwise been diagnosed as BA, are now classified with specific genetic conditions leading to cholestasis. atresia Elsevier hypoplasia Elsevier venopathy Elsevier biliary Elsevier extrahepatic Elsevier obliterative Elsevier non-cholestatic Elsevier Enthalten in Elsevier Haoula, Zeina J. ELSEVIER Levonorgestrel intra-uterine system as a treatment option for complex endometrial hyperplasia 2011 the continuously updated review of diagnostic histopathology Amsterdam [u.a.] (DE-627)ELV007989881 volume:29 year:2023 number:1 pages:52-66 extent:15 https://doi.org/10.1016/j.mpdhp.2022.11.001 Volltext GBV_USEFLAG_U GBV_ELV SYSFLAG_U SSG-OLC-PHA 44.92 Gynäkologie VZ AR 29 2023 1 52-66 15 |
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Enthalten in Levonorgestrel intra-uterine system as a treatment option for complex endometrial hyperplasia Amsterdam [u.a.] volume:29 year:2023 number:1 pages:52-66 extent:15 |
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Enthalten in Levonorgestrel intra-uterine system as a treatment option for complex endometrial hyperplasia Amsterdam [u.a.] volume:29 year:2023 number:1 pages:52-66 extent:15 |
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Biliary atresia (BA) is an idiopathic, progressive, fibroinflammatory, and obliterative disease of the biliary tract that manifests in the neonatal period with scleral icterus, acholic stools, conjugated hyperbilirubinemia, and elevated serum-gamma glutamyl transferase. Definitive diagnosis is established by a multi-disciplinary team comprising of pediatricians, hepatologists, radiologists, surgeons, and pathologists. It is currently the most common cause of pediatric liver transplantation in the USA and worldwide. More than 100 diseases can present with neonatal cholestasis mimicking BA. Early diagnosis (<60 days of age) with a timely Kasai portoenterostomy (KP) is crucial to relieve biliary obstruction and achieve longer native liver survival. Histopathologic features of BA can differ based on age and specific surgical interventions. This review describes histopathologic features of BA at various stages and focuses on a variety of common and uncommon diseases mimicking BA. With the increasing use of molecular testing and comprehensive genetic cholestasis panels, several patients who would have otherwise been diagnosed as BA, are now classified with specific genetic conditions leading to cholestasis. |
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Biliary atresia (BA) is an idiopathic, progressive, fibroinflammatory, and obliterative disease of the biliary tract that manifests in the neonatal period with scleral icterus, acholic stools, conjugated hyperbilirubinemia, and elevated serum-gamma glutamyl transferase. Definitive diagnosis is established by a multi-disciplinary team comprising of pediatricians, hepatologists, radiologists, surgeons, and pathologists. It is currently the most common cause of pediatric liver transplantation in the USA and worldwide. More than 100 diseases can present with neonatal cholestasis mimicking BA. Early diagnosis (<60 days of age) with a timely Kasai portoenterostomy (KP) is crucial to relieve biliary obstruction and achieve longer native liver survival. Histopathologic features of BA can differ based on age and specific surgical interventions. This review describes histopathologic features of BA at various stages and focuses on a variety of common and uncommon diseases mimicking BA. With the increasing use of molecular testing and comprehensive genetic cholestasis panels, several patients who would have otherwise been diagnosed as BA, are now classified with specific genetic conditions leading to cholestasis. |
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Biliary atresia (BA) is an idiopathic, progressive, fibroinflammatory, and obliterative disease of the biliary tract that manifests in the neonatal period with scleral icterus, acholic stools, conjugated hyperbilirubinemia, and elevated serum-gamma glutamyl transferase. Definitive diagnosis is established by a multi-disciplinary team comprising of pediatricians, hepatologists, radiologists, surgeons, and pathologists. It is currently the most common cause of pediatric liver transplantation in the USA and worldwide. More than 100 diseases can present with neonatal cholestasis mimicking BA. Early diagnosis (<60 days of age) with a timely Kasai portoenterostomy (KP) is crucial to relieve biliary obstruction and achieve longer native liver survival. Histopathologic features of BA can differ based on age and specific surgical interventions. This review describes histopathologic features of BA at various stages and focuses on a variety of common and uncommon diseases mimicking BA. With the increasing use of molecular testing and comprehensive genetic cholestasis panels, several patients who would have otherwise been diagnosed as BA, are now classified with specific genetic conditions leading to cholestasis. |
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