Intrahepatic cholangiocarcinoma in a patient with Wilson’s disease: a case report
Abstract The incidence of hepatobiliary malignancies, and especially intrahepatic cholangiocarcinoma (ICC), for patients with Wilson’s disease (WD), is very low, even for cirrhotic patients. A 44-year-old male was admitted to our department for treatment of a liver tumor. He was diagnosed with WD at...
Ausführliche Beschreibung
Autor*in: |
Mukai, Yosuke [verfasserIn] |
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Format: |
E-Artikel |
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Sprache: |
Englisch |
Erschienen: |
2016 |
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Schlagwörter: |
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Anmerkung: |
© Mukai et al. 2016 |
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Übergeordnetes Werk: |
Enthalten in: Surgical case reports - Berlin : SpringerOpen, 2015, 2(2016), 1 vom: 23. März |
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Übergeordnetes Werk: |
volume:2 ; year:2016 ; number:1 ; day:23 ; month:03 |
Links: |
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DOI / URN: |
10.1186/s40792-016-0156-3 |
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Katalog-ID: |
SPR037751816 |
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520 | |a Abstract The incidence of hepatobiliary malignancies, and especially intrahepatic cholangiocarcinoma (ICC), for patients with Wilson’s disease (WD), is very low, even for cirrhotic patients. A 44-year-old male was admitted to our department for treatment of a liver tumor. He was diagnosed with WD at the age of 15. According to radiological findings, his liver tumor was a suspected hepatocellular carcinoma (HCC) or a combined hepatocellular and cholangiocellular carcinoma. A partial resection of liver segments 8 (S8) and 5 (S5) was subsequently performed due to the intraoperative suspicion of intrahepatic metastasis at the surface of S5. Postoperative histology revealed that the resected portion of S8 contained an ICC; the removed S5 portion comprised a regenerative nodule with hemosiderosis. To date, the patient has survived without tumor recurrence for more than 44 months following surgery. A survey of the literature, inclusive of case reports, would suggest that surgical resection is the primary course of action for a WD patient with ICC, if liver function can be preserved and curative resection performed. | ||
650 | 4 | |a Wilson’s disease |7 (dpeaa)DE-He213 | |
650 | 4 | |a Intrahepatic cholangiocarcinoma |7 (dpeaa)DE-He213 | |
650 | 4 | |a Liver tumor |7 (dpeaa)DE-He213 | |
650 | 4 | |a Hepatobiliary malignancies |7 (dpeaa)DE-He213 | |
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700 | 1 | |a Eguchi, Hidetoshi |4 aut | |
700 | 1 | |a Yamada, Daisaku |4 aut | |
700 | 1 | |a Asaoka, Tadafumi |4 aut | |
700 | 1 | |a Noda, Takehiro |4 aut | |
700 | 1 | |a Kawamoto, Koichi |4 aut | |
700 | 1 | |a Gotoh, Kunihito |4 aut | |
700 | 1 | |a Takeda, Yutaka |4 aut | |
700 | 1 | |a Tanemura, Masahiro |4 aut | |
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700 | 1 | |a Mori, Masaki |4 aut | |
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10.1186/s40792-016-0156-3 doi (DE-627)SPR037751816 (SPR)s40792-016-0156-3-e DE-627 ger DE-627 rakwb eng Mukai, Yosuke verfasserin aut Intrahepatic cholangiocarcinoma in a patient with Wilson’s disease: a case report 2016 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier © Mukai et al. 2016 Abstract The incidence of hepatobiliary malignancies, and especially intrahepatic cholangiocarcinoma (ICC), for patients with Wilson’s disease (WD), is very low, even for cirrhotic patients. A 44-year-old male was admitted to our department for treatment of a liver tumor. He was diagnosed with WD at the age of 15. According to radiological findings, his liver tumor was a suspected hepatocellular carcinoma (HCC) or a combined hepatocellular and cholangiocellular carcinoma. A partial resection of liver segments 8 (S8) and 5 (S5) was subsequently performed due to the intraoperative suspicion of intrahepatic metastasis at the surface of S5. Postoperative histology revealed that the resected portion of S8 contained an ICC; the removed S5 portion comprised a regenerative nodule with hemosiderosis. To date, the patient has survived without tumor recurrence for more than 44 months following surgery. A survey of the literature, inclusive of case reports, would suggest that surgical resection is the primary course of action for a WD patient with ICC, if liver function can be preserved and curative resection performed. Wilson’s disease (dpeaa)DE-He213 Intrahepatic cholangiocarcinoma (dpeaa)DE-He213 Liver tumor (dpeaa)DE-He213 Hepatobiliary malignancies (dpeaa)DE-He213 Wada, Hiroshi aut Eguchi, Hidetoshi aut Yamada, Daisaku aut Asaoka, Tadafumi aut Noda, Takehiro aut Kawamoto, Koichi aut Gotoh, Kunihito aut Takeda, Yutaka aut Tanemura, Masahiro aut Umeshita, Koji aut Hori, Yumiko aut Morii, Eiichi aut Doki, Yuichiro aut Mori, Masaki aut Enthalten in Surgical case reports Berlin : SpringerOpen, 2015 2(2016), 1 vom: 23. März (DE-627)818040475 (DE-600)2809613-7 2198-7793 nnns volume:2 year:2016 number:1 day:23 month:03 https://dx.doi.org/10.1186/s40792-016-0156-3 kostenfrei Volltext GBV_USEFLAG_A SYSFLAG_A GBV_SPRINGER SSG-OLC-PHA GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_31 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2014 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 2 2016 1 23 03 |
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10.1186/s40792-016-0156-3 doi (DE-627)SPR037751816 (SPR)s40792-016-0156-3-e DE-627 ger DE-627 rakwb eng Mukai, Yosuke verfasserin aut Intrahepatic cholangiocarcinoma in a patient with Wilson’s disease: a case report 2016 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier © Mukai et al. 2016 Abstract The incidence of hepatobiliary malignancies, and especially intrahepatic cholangiocarcinoma (ICC), for patients with Wilson’s disease (WD), is very low, even for cirrhotic patients. A 44-year-old male was admitted to our department for treatment of a liver tumor. He was diagnosed with WD at the age of 15. According to radiological findings, his liver tumor was a suspected hepatocellular carcinoma (HCC) or a combined hepatocellular and cholangiocellular carcinoma. A partial resection of liver segments 8 (S8) and 5 (S5) was subsequently performed due to the intraoperative suspicion of intrahepatic metastasis at the surface of S5. Postoperative histology revealed that the resected portion of S8 contained an ICC; the removed S5 portion comprised a regenerative nodule with hemosiderosis. To date, the patient has survived without tumor recurrence for more than 44 months following surgery. A survey of the literature, inclusive of case reports, would suggest that surgical resection is the primary course of action for a WD patient with ICC, if liver function can be preserved and curative resection performed. Wilson’s disease (dpeaa)DE-He213 Intrahepatic cholangiocarcinoma (dpeaa)DE-He213 Liver tumor (dpeaa)DE-He213 Hepatobiliary malignancies (dpeaa)DE-He213 Wada, Hiroshi aut Eguchi, Hidetoshi aut Yamada, Daisaku aut Asaoka, Tadafumi aut Noda, Takehiro aut Kawamoto, Koichi aut Gotoh, Kunihito aut Takeda, Yutaka aut Tanemura, Masahiro aut Umeshita, Koji aut Hori, Yumiko aut Morii, Eiichi aut Doki, Yuichiro aut Mori, Masaki aut Enthalten in Surgical case reports Berlin : SpringerOpen, 2015 2(2016), 1 vom: 23. März (DE-627)818040475 (DE-600)2809613-7 2198-7793 nnns volume:2 year:2016 number:1 day:23 month:03 https://dx.doi.org/10.1186/s40792-016-0156-3 kostenfrei Volltext GBV_USEFLAG_A SYSFLAG_A GBV_SPRINGER SSG-OLC-PHA GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_31 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2014 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 2 2016 1 23 03 |
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10.1186/s40792-016-0156-3 doi (DE-627)SPR037751816 (SPR)s40792-016-0156-3-e DE-627 ger DE-627 rakwb eng Mukai, Yosuke verfasserin aut Intrahepatic cholangiocarcinoma in a patient with Wilson’s disease: a case report 2016 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier © Mukai et al. 2016 Abstract The incidence of hepatobiliary malignancies, and especially intrahepatic cholangiocarcinoma (ICC), for patients with Wilson’s disease (WD), is very low, even for cirrhotic patients. A 44-year-old male was admitted to our department for treatment of a liver tumor. He was diagnosed with WD at the age of 15. According to radiological findings, his liver tumor was a suspected hepatocellular carcinoma (HCC) or a combined hepatocellular and cholangiocellular carcinoma. A partial resection of liver segments 8 (S8) and 5 (S5) was subsequently performed due to the intraoperative suspicion of intrahepatic metastasis at the surface of S5. Postoperative histology revealed that the resected portion of S8 contained an ICC; the removed S5 portion comprised a regenerative nodule with hemosiderosis. To date, the patient has survived without tumor recurrence for more than 44 months following surgery. A survey of the literature, inclusive of case reports, would suggest that surgical resection is the primary course of action for a WD patient with ICC, if liver function can be preserved and curative resection performed. Wilson’s disease (dpeaa)DE-He213 Intrahepatic cholangiocarcinoma (dpeaa)DE-He213 Liver tumor (dpeaa)DE-He213 Hepatobiliary malignancies (dpeaa)DE-He213 Wada, Hiroshi aut Eguchi, Hidetoshi aut Yamada, Daisaku aut Asaoka, Tadafumi aut Noda, Takehiro aut Kawamoto, Koichi aut Gotoh, Kunihito aut Takeda, Yutaka aut Tanemura, Masahiro aut Umeshita, Koji aut Hori, Yumiko aut Morii, Eiichi aut Doki, Yuichiro aut Mori, Masaki aut Enthalten in Surgical case reports Berlin : SpringerOpen, 2015 2(2016), 1 vom: 23. März (DE-627)818040475 (DE-600)2809613-7 2198-7793 nnns volume:2 year:2016 number:1 day:23 month:03 https://dx.doi.org/10.1186/s40792-016-0156-3 kostenfrei Volltext GBV_USEFLAG_A SYSFLAG_A GBV_SPRINGER SSG-OLC-PHA GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_31 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2014 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 2 2016 1 23 03 |
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10.1186/s40792-016-0156-3 doi (DE-627)SPR037751816 (SPR)s40792-016-0156-3-e DE-627 ger DE-627 rakwb eng Mukai, Yosuke verfasserin aut Intrahepatic cholangiocarcinoma in a patient with Wilson’s disease: a case report 2016 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier © Mukai et al. 2016 Abstract The incidence of hepatobiliary malignancies, and especially intrahepatic cholangiocarcinoma (ICC), for patients with Wilson’s disease (WD), is very low, even for cirrhotic patients. A 44-year-old male was admitted to our department for treatment of a liver tumor. He was diagnosed with WD at the age of 15. According to radiological findings, his liver tumor was a suspected hepatocellular carcinoma (HCC) or a combined hepatocellular and cholangiocellular carcinoma. A partial resection of liver segments 8 (S8) and 5 (S5) was subsequently performed due to the intraoperative suspicion of intrahepatic metastasis at the surface of S5. Postoperative histology revealed that the resected portion of S8 contained an ICC; the removed S5 portion comprised a regenerative nodule with hemosiderosis. To date, the patient has survived without tumor recurrence for more than 44 months following surgery. A survey of the literature, inclusive of case reports, would suggest that surgical resection is the primary course of action for a WD patient with ICC, if liver function can be preserved and curative resection performed. Wilson’s disease (dpeaa)DE-He213 Intrahepatic cholangiocarcinoma (dpeaa)DE-He213 Liver tumor (dpeaa)DE-He213 Hepatobiliary malignancies (dpeaa)DE-He213 Wada, Hiroshi aut Eguchi, Hidetoshi aut Yamada, Daisaku aut Asaoka, Tadafumi aut Noda, Takehiro aut Kawamoto, Koichi aut Gotoh, Kunihito aut Takeda, Yutaka aut Tanemura, Masahiro aut Umeshita, Koji aut Hori, Yumiko aut Morii, Eiichi aut Doki, Yuichiro aut Mori, Masaki aut Enthalten in Surgical case reports Berlin : SpringerOpen, 2015 2(2016), 1 vom: 23. März (DE-627)818040475 (DE-600)2809613-7 2198-7793 nnns volume:2 year:2016 number:1 day:23 month:03 https://dx.doi.org/10.1186/s40792-016-0156-3 kostenfrei Volltext GBV_USEFLAG_A SYSFLAG_A GBV_SPRINGER SSG-OLC-PHA GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_31 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2014 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 2 2016 1 23 03 |
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10.1186/s40792-016-0156-3 doi (DE-627)SPR037751816 (SPR)s40792-016-0156-3-e DE-627 ger DE-627 rakwb eng Mukai, Yosuke verfasserin aut Intrahepatic cholangiocarcinoma in a patient with Wilson’s disease: a case report 2016 Text txt rdacontent Computermedien c rdamedia Online-Ressource cr rdacarrier © Mukai et al. 2016 Abstract The incidence of hepatobiliary malignancies, and especially intrahepatic cholangiocarcinoma (ICC), for patients with Wilson’s disease (WD), is very low, even for cirrhotic patients. A 44-year-old male was admitted to our department for treatment of a liver tumor. He was diagnosed with WD at the age of 15. According to radiological findings, his liver tumor was a suspected hepatocellular carcinoma (HCC) or a combined hepatocellular and cholangiocellular carcinoma. A partial resection of liver segments 8 (S8) and 5 (S5) was subsequently performed due to the intraoperative suspicion of intrahepatic metastasis at the surface of S5. Postoperative histology revealed that the resected portion of S8 contained an ICC; the removed S5 portion comprised a regenerative nodule with hemosiderosis. To date, the patient has survived without tumor recurrence for more than 44 months following surgery. A survey of the literature, inclusive of case reports, would suggest that surgical resection is the primary course of action for a WD patient with ICC, if liver function can be preserved and curative resection performed. Wilson’s disease (dpeaa)DE-He213 Intrahepatic cholangiocarcinoma (dpeaa)DE-He213 Liver tumor (dpeaa)DE-He213 Hepatobiliary malignancies (dpeaa)DE-He213 Wada, Hiroshi aut Eguchi, Hidetoshi aut Yamada, Daisaku aut Asaoka, Tadafumi aut Noda, Takehiro aut Kawamoto, Koichi aut Gotoh, Kunihito aut Takeda, Yutaka aut Tanemura, Masahiro aut Umeshita, Koji aut Hori, Yumiko aut Morii, Eiichi aut Doki, Yuichiro aut Mori, Masaki aut Enthalten in Surgical case reports Berlin : SpringerOpen, 2015 2(2016), 1 vom: 23. März (DE-627)818040475 (DE-600)2809613-7 2198-7793 nnns volume:2 year:2016 number:1 day:23 month:03 https://dx.doi.org/10.1186/s40792-016-0156-3 kostenfrei Volltext GBV_USEFLAG_A SYSFLAG_A GBV_SPRINGER SSG-OLC-PHA GBV_ILN_20 GBV_ILN_22 GBV_ILN_23 GBV_ILN_24 GBV_ILN_31 GBV_ILN_39 GBV_ILN_40 GBV_ILN_60 GBV_ILN_62 GBV_ILN_63 GBV_ILN_65 GBV_ILN_69 GBV_ILN_73 GBV_ILN_74 GBV_ILN_95 GBV_ILN_105 GBV_ILN_110 GBV_ILN_151 GBV_ILN_161 GBV_ILN_170 GBV_ILN_206 GBV_ILN_213 GBV_ILN_230 GBV_ILN_285 GBV_ILN_293 GBV_ILN_602 GBV_ILN_2014 GBV_ILN_4012 GBV_ILN_4037 GBV_ILN_4112 GBV_ILN_4125 GBV_ILN_4126 GBV_ILN_4249 GBV_ILN_4305 GBV_ILN_4306 GBV_ILN_4307 GBV_ILN_4313 GBV_ILN_4322 GBV_ILN_4323 GBV_ILN_4324 GBV_ILN_4325 GBV_ILN_4338 GBV_ILN_4367 GBV_ILN_4700 AR 2 2016 1 23 03 |
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Mukai, Yosuke @@aut@@ Wada, Hiroshi @@aut@@ Eguchi, Hidetoshi @@aut@@ Yamada, Daisaku @@aut@@ Asaoka, Tadafumi @@aut@@ Noda, Takehiro @@aut@@ Kawamoto, Koichi @@aut@@ Gotoh, Kunihito @@aut@@ Takeda, Yutaka @@aut@@ Tanemura, Masahiro @@aut@@ Umeshita, Koji @@aut@@ Hori, Yumiko @@aut@@ Morii, Eiichi @@aut@@ Doki, Yuichiro @@aut@@ Mori, Masaki @@aut@@ |
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Mukai, Yosuke Wada, Hiroshi Eguchi, Hidetoshi Yamada, Daisaku Asaoka, Tadafumi Noda, Takehiro Kawamoto, Koichi Gotoh, Kunihito Takeda, Yutaka Tanemura, Masahiro Umeshita, Koji Hori, Yumiko Morii, Eiichi Doki, Yuichiro Mori, Masaki |
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Intrahepatic cholangiocarcinoma in a patient with Wilson’s disease: a case report |
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Abstract The incidence of hepatobiliary malignancies, and especially intrahepatic cholangiocarcinoma (ICC), for patients with Wilson’s disease (WD), is very low, even for cirrhotic patients. A 44-year-old male was admitted to our department for treatment of a liver tumor. He was diagnosed with WD at the age of 15. According to radiological findings, his liver tumor was a suspected hepatocellular carcinoma (HCC) or a combined hepatocellular and cholangiocellular carcinoma. A partial resection of liver segments 8 (S8) and 5 (S5) was subsequently performed due to the intraoperative suspicion of intrahepatic metastasis at the surface of S5. Postoperative histology revealed that the resected portion of S8 contained an ICC; the removed S5 portion comprised a regenerative nodule with hemosiderosis. To date, the patient has survived without tumor recurrence for more than 44 months following surgery. A survey of the literature, inclusive of case reports, would suggest that surgical resection is the primary course of action for a WD patient with ICC, if liver function can be preserved and curative resection performed. © Mukai et al. 2016 |
abstractGer |
Abstract The incidence of hepatobiliary malignancies, and especially intrahepatic cholangiocarcinoma (ICC), for patients with Wilson’s disease (WD), is very low, even for cirrhotic patients. A 44-year-old male was admitted to our department for treatment of a liver tumor. He was diagnosed with WD at the age of 15. According to radiological findings, his liver tumor was a suspected hepatocellular carcinoma (HCC) or a combined hepatocellular and cholangiocellular carcinoma. A partial resection of liver segments 8 (S8) and 5 (S5) was subsequently performed due to the intraoperative suspicion of intrahepatic metastasis at the surface of S5. Postoperative histology revealed that the resected portion of S8 contained an ICC; the removed S5 portion comprised a regenerative nodule with hemosiderosis. To date, the patient has survived without tumor recurrence for more than 44 months following surgery. A survey of the literature, inclusive of case reports, would suggest that surgical resection is the primary course of action for a WD patient with ICC, if liver function can be preserved and curative resection performed. © Mukai et al. 2016 |
abstract_unstemmed |
Abstract The incidence of hepatobiliary malignancies, and especially intrahepatic cholangiocarcinoma (ICC), for patients with Wilson’s disease (WD), is very low, even for cirrhotic patients. A 44-year-old male was admitted to our department for treatment of a liver tumor. He was diagnosed with WD at the age of 15. According to radiological findings, his liver tumor was a suspected hepatocellular carcinoma (HCC) or a combined hepatocellular and cholangiocellular carcinoma. A partial resection of liver segments 8 (S8) and 5 (S5) was subsequently performed due to the intraoperative suspicion of intrahepatic metastasis at the surface of S5. Postoperative histology revealed that the resected portion of S8 contained an ICC; the removed S5 portion comprised a regenerative nodule with hemosiderosis. To date, the patient has survived without tumor recurrence for more than 44 months following surgery. A survey of the literature, inclusive of case reports, would suggest that surgical resection is the primary course of action for a WD patient with ICC, if liver function can be preserved and curative resection performed. © Mukai et al. 2016 |
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<?xml version="1.0" encoding="UTF-8"?><collection xmlns="http://www.loc.gov/MARC21/slim"><record><leader>01000caa a22002652 4500</leader><controlfield tag="001">SPR037751816</controlfield><controlfield tag="003">DE-627</controlfield><controlfield tag="005">20230519083424.0</controlfield><controlfield tag="007">cr uuu---uuuuu</controlfield><controlfield tag="008">201007s2016 xx |||||o 00| ||eng c</controlfield><datafield tag="024" ind1="7" ind2=" "><subfield code="a">10.1186/s40792-016-0156-3</subfield><subfield code="2">doi</subfield></datafield><datafield tag="035" ind1=" " ind2=" "><subfield code="a">(DE-627)SPR037751816</subfield></datafield><datafield tag="035" ind1=" " ind2=" "><subfield code="a">(SPR)s40792-016-0156-3-e</subfield></datafield><datafield tag="040" ind1=" " ind2=" "><subfield code="a">DE-627</subfield><subfield code="b">ger</subfield><subfield code="c">DE-627</subfield><subfield code="e">rakwb</subfield></datafield><datafield tag="041" ind1=" " ind2=" "><subfield code="a">eng</subfield></datafield><datafield tag="100" ind1="1" ind2=" "><subfield code="a">Mukai, Yosuke</subfield><subfield code="e">verfasserin</subfield><subfield code="4">aut</subfield></datafield><datafield tag="245" ind1="1" ind2="0"><subfield code="a">Intrahepatic cholangiocarcinoma in a patient with Wilson’s disease: a case report</subfield></datafield><datafield tag="264" ind1=" " ind2="1"><subfield code="c">2016</subfield></datafield><datafield tag="336" ind1=" " ind2=" "><subfield code="a">Text</subfield><subfield code="b">txt</subfield><subfield code="2">rdacontent</subfield></datafield><datafield tag="337" ind1=" " ind2=" "><subfield code="a">Computermedien</subfield><subfield code="b">c</subfield><subfield code="2">rdamedia</subfield></datafield><datafield tag="338" ind1=" " ind2=" "><subfield code="a">Online-Ressource</subfield><subfield code="b">cr</subfield><subfield code="2">rdacarrier</subfield></datafield><datafield tag="500" ind1=" " ind2=" "><subfield code="a">© Mukai et al. 2016</subfield></datafield><datafield tag="520" ind1=" " ind2=" "><subfield code="a">Abstract The incidence of hepatobiliary malignancies, and especially intrahepatic cholangiocarcinoma (ICC), for patients with Wilson’s disease (WD), is very low, even for cirrhotic patients. A 44-year-old male was admitted to our department for treatment of a liver tumor. He was diagnosed with WD at the age of 15. According to radiological findings, his liver tumor was a suspected hepatocellular carcinoma (HCC) or a combined hepatocellular and cholangiocellular carcinoma. A partial resection of liver segments 8 (S8) and 5 (S5) was subsequently performed due to the intraoperative suspicion of intrahepatic metastasis at the surface of S5. Postoperative histology revealed that the resected portion of S8 contained an ICC; the removed S5 portion comprised a regenerative nodule with hemosiderosis. To date, the patient has survived without tumor recurrence for more than 44 months following surgery. 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